2020 ICD-10-CM Diagnosis Code K00.5

Hereditary disturbances in tooth structure, not elsewhere classified

    2016 2017 2018 2019 2020 Billable/Specific Code
  • K00.5 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • Short description: Hereditary disturbances in tooth structure, NEC
  • The 2020 edition of ICD-10-CM K00.5 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of K00.5 - other international versions of ICD-10 K00.5 may differ.
Applicable To
  • Amelogenesis imperfecta
  • Dentinogenesis imperfecta
  • Odontogenesis imperfecta
  • Dentinal dysplasia
  • Shell teeth
The following code(s) above K00.5 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to K00.5:
  • K00-K95
    2020 ICD-10-CM Range K00-K95

    Diseases of the digestive system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the digestive system
  • K00
    ICD-10-CM Diagnosis Code K00

    Disorders of tooth development and eruption

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • embedded and impacted teeth (K01.-)
    Disorders of tooth development and eruption
Approximate Synonyms
  • Hereditary disturbances in tooth structure
Clinical Information
  • A clinically and genetically heterogeneous group of hereditary conditions characterized by malformed dental enamel, usually involving dental enamel hypoplasia and/or tooth hypomineralization.
  • A congenital tooth development disorder caused by mutations in the dspp gene. The teeth are weak, discolored, and translucent.
  • An apparently hereditary disorder of dentin formation, marked by a normal appearance of coronal dentin associated with pulpal obliteration, faulty root formation, and a tendency for peripheral lesions without obvious cause. (from Dorland, 27th ed)
  • An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.
ICD-10-CM K00.5 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 011 Tracheostomy for face, mouth & neck diagnoses or laryngectomy with mcc
  • 012 Tracheostomy for face, mouth & neck diagnoses or laryngectomy with cc
  • 013 Tracheostomy for face, mouth & neck diagnoses or laryngectomy without cc/mcc
  • 157 Dental and oral diseases with mcc
  • 158 Dental and oral diseases with cc
  • 159 Dental and oral diseases without cc/mcc

Convert K00.5 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to K00.5:
  • Amelogenesis imperfecta K00.5
  • Brown enamel of teeth K00.5 (hereditary)
  • Defect, defective Q89.9
    ICD-10-CM Diagnosis Code Q89.9

    Congenital malformation, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital anomaly NOS
    • Congenital deformity NOS
    • dentin K00.5 (hereditary)
  • Dentin
    • opalescent K00.5
  • Dentinogenesis imperfecta K00.5
  • Disturbance(s) - see also Disease
    • tooth
      • structure, hereditary NEC K00.5
  • Dysplasia - see also Anomaly
    • dentinal K00.5
  • Odontogenesis imperfecta K00.5
  • Opalescent dentin K00.5 (hereditary)
  • Shell teeth K00.5

ICD-10-CM Codes Adjacent To K00.5
J98.6 Disorders of diaphragm
J98.8 Other specified respiratory disorders
J98.9 Respiratory disorder, unspecified
J99 Respiratory disorders in diseases classified elsewhere
K00 Disorders of tooth development and eruption
K00.0 Anodontia
K00.1 Supernumerary teeth
K00.2 Abnormalities of size and form of teeth
K00.3 Mottled teeth
K00.4 Disturbances in tooth formation
K00.5 Hereditary disturbances in tooth structure, not elsewhere classified
K00.6 Disturbances in tooth eruption
K00.7 Teething syndrome
K00.8 Other disorders of tooth development
K00.9 Disorder of tooth development, unspecified
K01 Embedded and impacted teeth
K01.0 Embedded teeth
K01.1 Impacted teeth
K02 Dental caries
K02.3 Arrested dental caries
K02.5 Dental caries on pit and fissure surface

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.