2020 ICD-10-CM Diagnosis Code L81.3

Café au lait spots

    2016 2017 2018 2019 2020 Billable/Specific Code
  • L81.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • Short description: Cafe au lait spots
  • The 2020 edition of ICD-10-CM L81.3 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of L81.3 - other international versions of ICD-10 L81.3 may differ.
The following code(s) above L81.3 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to L81.3:
  • L00-L99
    2020 ICD-10-CM Range L00-L99

    Diseases of the skin and subcutaneous tissue

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • lipomelanotic reticulosis (I89.8)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    • systemic connective tissue disorders (M30-M36)
    • viral warts (B07.-)
    Diseases of the skin and subcutaneous tissue
  • L81
    ICD-10-CM Diagnosis Code L81

    Other disorders of pigmentation

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • birthmark NOS (Q82.5)
    • Peutz-Jeghers syndrome (Q85.8)
    Type 2 Excludes
    • nevus - see Alphabetical Index
    Other disorders of pigmentation
Approximate Synonyms
  • Cafe au lait spots
  • Cafè au lait spots
Clinical Information
  • A light brown, sharply demarcated skin patch. It is a manifestation of neurofibromatosis type 1 and mccune-albright syndrome.
  • Light brown pigmented macules associated with neurofibromatosis and albright's syndrome (see fibrous dysplasia, polyostotic).
ICD-10-CM L81.3 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 606 Minor skin disorders with mcc
  • 607 Minor skin disorders without mcc
  • 795 Normal newborn

Convert L81.3 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to L81.3:
  • Type 2 Excludes: Q82.5
    ICD-10-CM Diagnosis Code Q82.5

    Congenital non-neoplastic nevus

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Birthmark NOS
    • Flammeus Nevus
    • Portwine Nevus
    • Sanguineous Nevus
    • Strawberry Nevus
    • Vascular Nevus NOS
    • Verrucous Nevus
    Type 2 Excludes

Diagnosis Index entries containing back-references to L81.3:
  • Café, au lait spots L81.3
  • Spots, spotting (in) (of)
    • café, au lait L81.3

ICD-10-CM Codes Adjacent To L81.3
L76.33 Postprocedural seroma of skin and subcutaneous tissue following a dermatologic procedure
L76.34 Postprocedural seroma of skin and subcutaneous tissue following other procedure
L76.8 Other intraoperative and postprocedural complications of skin and subcutaneous tissue
L76.81 Other intraoperative complications of skin and subcutaneous tissue
L76.82 Other postprocedural complications of skin and subcutaneous tissue
L80 Vitiligo
L81 Other disorders of pigmentation
L81.0 Postinflammatory hyperpigmentation
L81.1 Chloasma
L81.2 Freckles
L81.3 Café au lait spots
L81.4 Other melanin hyperpigmentation
L81.5 Leukoderma, not elsewhere classified
L81.6 Other disorders of diminished melanin formation
L81.7 Pigmented purpuric dermatosis
L81.8 Other specified disorders of pigmentation
L81.9 Disorder of pigmentation, unspecified
L82 Seborrheic keratosis
L82.0 Inflamed seborrheic keratosis
L82.1 Other seborrheic keratosis
L83 Acanthosis nigricans

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.