2020 ICD-10-CM Diagnosis Code M04

Autoinflammatory syndromes

    2017 - New Code 2018 2019 2020 Non-Billable/Non-Specific Code
  • M04 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2020 edition of ICD-10-CM M04 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of M04 - other international versions of ICD-10 M04 may differ.
Type 2 Excludes
Type 2 Excludes Help
A type 2 excludes note represents "not included here". A type 2 excludes note indicates that the condition excluded is not part of the condition it is excluded from but a patient may have both conditions at the same time. When a type 2 excludes note appears under a code it is acceptable to use both the code (M04) and the excluded code together.
  • Crohn's disease (
    ICD-10-CM Diagnosis Code K50
    • K50 Crohn's disease [regional enteritis]
      • K50.0 Crohn's disease of small intestine
        • K50.00 Crohn's disease of small intestine without co...
        • K50.01 Crohn's disease of small intestine with compl...
          • K50.011 Crohn's disease of small intestine with recta...
          • K50.012 Crohn's disease of small intestine with intes...
          • K50.013 Crohn's disease of small intestine with fistu...
          • K50.014 Crohn's disease of small intestine with absce...
          • K50.018 Crohn's disease of small intestine with other...
          • K50.019 Crohn's disease of small intestine with unspe...
      • K50.1 Crohn's disease of large intestine
        • K50.10 Crohn's disease of large intestine without co...
        • K50.11 Crohn's disease of large intestine with compl...
          • K50.111 Crohn's disease of large intestine with recta...
          • K50.112 Crohn's disease of large intestine with intes...
          • K50.113 Crohn's disease of large intestine with fistu...
          • K50.114 Crohn's disease of large intestine with absce...
          • K50.118 Crohn's disease of large intestine with other...
          • K50.119 Crohn's disease of large intestine with unspe...
      • K50.8 Crohn's disease of both small and large intes...
        • K50.80 Crohn's disease of both small and large intes...
        • K50.81 Crohn's disease of both small and large intes...
          • K50.811 Crohn's disease of both small and large intes...
          • K50.812 Crohn's disease of both small and large intes...
          • K50.813 Crohn's disease of both small and large intes...
          • K50.814 Crohn's disease of both small and large intes...
          • K50.818 Crohn's disease of both small and large intes...
          • K50.819 Crohn's disease of both small and large intes...
      • K50.9 Crohn's disease, unspecified
        • K50.90 Crohn's disease, unspecified, without complic...
        • K50.91 Crohn's disease, unspecified, with complicati...
          • K50.911 Crohn's disease, unspecified, with rectal ble...
          • K50.912 Crohn's disease, unspecified, with intestinal...
          • K50.913 Crohn's disease, unspecified, with fistula
          • K50.914 Crohn's disease, unspecified, with abscess
          • K50.918 Crohn's disease, unspecified, with other comp...
          • K50.919 Crohn's disease, unspecified, with unspecifie...
    K50.-
    )
The following code(s) above M04 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to M04:
  • M00-M99
    2020 ICD-10-CM Range M00-M99

    Diseases of the musculoskeletal system and connective tissue

    Note
    • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
    Type 2 Excludes
    • arthropathic psoriasis (L40.5-)
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • compartment syndrome (traumatic) (T79.A-)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the musculoskeletal system and connective tissue
Code History
  • 2017 (effective 10/1/2016): New code
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to M04:
  • Code Also: E85.0
    ICD-10-CM Diagnosis Code E85.0

    Non-neuropathic heredofamilial amyloidosis

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Hereditary amyloid nephropathy
    Code Also
    • associated disorders, such as:
    • autoinflammatory syndromes (M04.-)
    Type 2 Excludes
    • Transthyretin-related (ATTR) familial amyloid cardiomyopathy (E85.4)
ICD-10-CM Codes Adjacent To M04
M02.861 Other reactive arthropathies, right knee
M02.862 Other reactive arthropathies, left knee
M02.869 Other reactive arthropathies, unspecified knee
M02.87 Other reactive arthropathies, ankle and foot
M02.871 Other reactive arthropathies, right ankle and foot
M02.872 Other reactive arthropathies, left ankle and foot
M02.879 Other reactive arthropathies, unspecified ankle and foot
M02.88 …… vertebrae
M02.89 …… multiple sites
M02.9 Reactive arthropathy, unspecified
M04 Autoinflammatory syndromes
M04.1 Periodic fever syndromes
M04.2 Cryopyrin-associated periodic syndromes
M04.8 Other autoinflammatory syndromes
M04.9 Autoinflammatory syndrome, unspecified
M05 Rheumatoid arthritis with rheumatoid factor
M05.0 Felty's syndrome
M05.00 …… unspecified site
M05.01 Felty's syndrome, shoulder
M05.011 Felty's syndrome, right shoulder
M05.012 Felty's syndrome, left shoulder

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.