2020 ICD-10-CM Diagnosis Code M04.1

Periodic fever syndromes

    2017 - New Code 2018 2019 2020 Billable/Specific Code
  • M04.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM M04.1 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of M04.1 - other international versions of ICD-10 M04.1 may differ.
Applicable To
  • Familial Mediterranean fever
  • Hyperimmunoglobin D syndrome
  • Mevalonate kinase deficiency
  • Tumor necrosis factor receptor associated periodic syndrome [TRAPS]
The following code(s) above M04.1 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to M04.1:
  • M00-M99
    2020 ICD-10-CM Range M00-M99

    Diseases of the musculoskeletal system and connective tissue

    Note
    • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
    Type 2 Excludes
    • arthropathic psoriasis (L40.5-)
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • compartment syndrome (traumatic) (T79.A-)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the musculoskeletal system and connective tissue
  • M04
    ICD-10-CM Diagnosis Code M04

    Autoinflammatory syndromes

      2017 - New Code 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 2 Excludes
    Autoinflammatory syndromes
ICD-10-CM M04.1 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 545 Connective tissue disorders with mcc
  • 546 Connective tissue disorders with cc
  • 547 Connective tissue disorders without cc/mcc

Convert M04.1 to ICD-9-CM

Code History
  • 2017 (effective 10/1/2016): New code
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to M04.1:
  • Arthritis, arthritic (acute) (chronic) (nonpyogenic) (subacute) M19.90
    ICD-10-CM Diagnosis Code M19.90

    Unspecified osteoarthritis, unspecified site

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Arthrosis NOS
    • Arthritis NOS
    • Osteoarthritis NOS
    • in (due to)
      • Mediterranean fever, familial M04.1 - see also subcategory M14.8-
  • Deficiency, deficient
    • mevalonate kinase M04.1
  • Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor) R50.9
    ICD-10-CM Diagnosis Code R50.9

    Fever, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Fever NOS
    • Fever of unknown origin [FUO]
    • Fever with chills
    • Fever with rigors
    • Hyperpyrexia NOS
    • Persistent fever
    • Pyrexia NOS
    • Mediterranean A23.9
      - see also Brucellosis
      ICD-10-CM Diagnosis Code A23.9

      Brucellosis, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
      • familial M04.1
    • periodic M04.1 (Mediterranean)
  • Mediterranean
  • Syndrome - see also Disease
    • hyperimmunoglobulin D M04.1
    • periodic fever M04.1
    • tumor necrosis factor receptor associated periodic M04.1 (TRAPS)
  • TRAPS M04.1 (tumor necrosis factor receptor associated periodic syndrome)

ICD-10-CM Codes Adjacent To M04.1
M02.862 Other reactive arthropathies, left knee
M02.869 Other reactive arthropathies, unspecified knee
M02.87 Other reactive arthropathies, ankle and foot
M02.871 Other reactive arthropathies, right ankle and foot
M02.872 Other reactive arthropathies, left ankle and foot
M02.879 Other reactive arthropathies, unspecified ankle and foot
M02.88 …… vertebrae
M02.89 …… multiple sites
M02.9 Reactive arthropathy, unspecified
M04 Autoinflammatory syndromes
M04.1 Periodic fever syndromes
M04.2 Cryopyrin-associated periodic syndromes
M04.8 Other autoinflammatory syndromes
M04.9 Autoinflammatory syndrome, unspecified
M05 Rheumatoid arthritis with rheumatoid factor
M05.0 Felty's syndrome
M05.00 …… unspecified site
M05.01 Felty's syndrome, shoulder
M05.011 Felty's syndrome, right shoulder
M05.012 Felty's syndrome, left shoulder
M05.019 Felty's syndrome, unspecified shoulder

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.