2020 ICD-10-CM Diagnosis Code M30.3

Mucocutaneous lymph node syndrome [Kawasaki]

    2016 2017 2018 2019 2020 Billable/Specific Code
  • M30.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM M30.3 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of M30.3 - other international versions of ICD-10 M30.3 may differ.
The following code(s) above M30.3 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to M30.3:
  • M00-M99
    2020 ICD-10-CM Range M00-M99

    Diseases of the musculoskeletal system and connective tissue

    Note
    • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
    Type 2 Excludes
    • arthropathic psoriasis (L40.5-)
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • compartment syndrome (traumatic) (T79.A-)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the musculoskeletal system and connective tissue
  • M30-M36
    2020 ICD-10-CM Range M30-M36

    Systemic connective tissue disorders

    Includes
    • autoimmune disease NOS
    • collagen (vascular) disease NOS
    • systemic autoimmune disease
    • systemic collagen (vascular) disease
    Type 1 Excludes
    • autoimmune disease, single organ or single cell-type -code to relevant condition category
    Systemic connective tissue disorders
  • M30
    ICD-10-CM Diagnosis Code M30

    Polyarteritis nodosa and related conditions

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • microscopic polyarteritis (M31.7)
    Polyarteritis nodosa and related conditions
Approximate Synonyms
  • Acute febrile mucocutaneous lymph node syndrome
  • Aneurysm of coronary artery due to acute febrile mucocutaneous lymph node syndrome
  • Coronary aneurysm in kawasaki disease
Clinical Information
  • A vasculitis characterized by inflammation of the arteries, particularly the coronary arteries. The vasculitis may lead to aneurysm formation and possibly, heart attacks. It affects young children who usually present with persistent high fever, redness of the mucous membranes of the mouth, redness of the palms and soles, skin rashes, lymphadenitis, and joint pain and swelling.
  • An acute, febrile, mucocutaneous condition accompanied by swelling of cervical lymph nodes in infants and young children. The principal symptoms are fever, congestion of the ocular conjunctivae, reddening of the lips and oral cavity, protuberance of tongue papillae, and edema or erythema of the extremities.
  • Kawasaki disease is a rare childhood disease. It makes the walls of the blood vessels throughout the body become inflamed. It can affect any type of blood vessel, including the arteries, veins and capillaries.no one knows what causes kawasaki disease. Symptoms include
    • high fever
    • swollen lymph nodes in the neck
    • a rash on the mid-section and genital area
    • red, dry, cracked lips and a red, swollen tongue
    • red, swollen palms of the hands and soles of the feet
    • redness of the eyes
    kawasaki disease can't be passed from one child to another. It is mainly treated with medicines. Rarely, medical procedures and surgery also may be used for children whose coronary arteries are affected. Kawasaki disease can't be prevented. However, most children who develop the disease fully recover -- usually within weeks of getting signs and symptoms. Further problems are rare.
  • Systemic disease primarily of infants and young children, characterized by skin rash, swelling of hands and feet, enlarged cervical lymph nodes, "strawberry tongue", dry and cracked lips, high fevers, and coronary artery disease.
ICD-10-CM M30.3 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 545 Connective tissue disorders with mcc
  • 546 Connective tissue disorders with cc
  • 547 Connective tissue disorders without cc/mcc

Convert M30.3 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to M30.3:
  • Kawasaki's syndrome M30.3
  • Syndrome - see also Disease
    • mucocutaneous lymph node M30.3 (acute febrile) (MCLS)

ICD-10-CM Codes Adjacent To M30.3
M27.61 Osseointegration failure of dental implant
M27.62 Post-osseointegration biological failure of dental implant
M27.63 Post-osseointegration mechanical failure of dental implant
M27.69 Other endosseous dental implant failure
M27.8 Other specified diseases of jaws
M27.9 Disease of jaws, unspecified
M30 Polyarteritis nodosa and related conditions
M30.0 Polyarteritis nodosa
M30.1 Polyarteritis with lung involvement [Churg-Strauss]
M30.2 Juvenile polyarteritis
M30.3 Mucocutaneous lymph node syndrome [Kawasaki]
M30.8 Other conditions related to polyarteritis nodosa
M31 Other necrotizing vasculopathies
M31.0 Hypersensitivity angiitis
M31.1 Thrombotic microangiopathy
M31.2 Lethal midline granuloma
M31.3 Wegener's granulomatosis
M31.30 …… without renal involvement
M31.31 …… with renal involvement
M31.4 Aortic arch syndrome [Takayasu]
M31.5 Giant cell arteritis with polymyalgia rheumatica

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.