2020 ICD-10-CM Diagnosis Code M31.3

Wegener's granulomatosis

    2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
  • M31.3 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2020 edition of ICD-10-CM M31.3 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of M31.3 - other international versions of ICD-10 M31.3 may differ.
Applicable To
  • Necrotizing respiratory granulomatosis
The following code(s) above M31.3 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to M31.3:
  • M00-M99
    2020 ICD-10-CM Range M00-M99

    Diseases of the musculoskeletal system and connective tissue

    Note
    • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
    Type 2 Excludes
    • arthropathic psoriasis (L40.5-)
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • compartment syndrome (traumatic) (T79.A-)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the musculoskeletal system and connective tissue
  • M30-M36
    2020 ICD-10-CM Range M30-M36

    Systemic connective tissue disorders

    Includes
    • autoimmune disease NOS
    • collagen (vascular) disease NOS
    • systemic autoimmune disease
    • systemic collagen (vascular) disease
    Type 1 Excludes
    • autoimmune disease, single organ or single cell-type -code to relevant condition category
    Systemic connective tissue disorders
Clinical Information
  • A multisystemic disease of a complex genetic background. It is characterized by inflammation of the blood vessels (vasculitis) leading to damage in any number of organs. The common features include granulomatous inflammation of the respiratory tract and kidneys. Most patients have measurable autoantibodies (antineutrophil cytoplasmic antibodies) against neutrophil proteinase-3 (wegener autoantigen).
  • A rare, autoimmune, systemic medium and small size vasculitis. It is characterized by the formation of necrotizing granulomas in the respiratory tract, necrotizing angiitis, and glomerulonephritis.
  • Multisystem disease chiefly affecting males, characterized by necrotizing granulomatous vasculitis involving the upper and lower respiratory tracts, glomerulonephritis, and variable degrees of systemic small vessel vasculitis; considered an aberrant hypersensitivity reaction to an unknown antigen.
  • Wegener's granulomatosis is a rare disease. It is a type of vasculitis, or inflammation of the blood vessels. The inflammation limits the flow of blood to important organs, causing damage. It can affect any organ, but it mainly affects the sinuses, nose, trachea (windpipe), lungs, and kidneys. The cause of wegener's granulomatosis is unknown. It can affect people at any age. Men and women are equally affected. It is more common in whites. Symptoms may include joint pain, weakness, tiredness, and cold symptoms such as a runny nose that doesn't get better. Doctors use blood tests, chest x-rays, and biopsies to diagnose the disease and rule out other causes of the symptoms.early treatment is important. Most people improve with medicines to slow or stop the inflammation.
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to M31.3:
  • Type 1 Excludes: L95
    ICD-10-CM Diagnosis Code L95

    Vasculitis limited to skin, not elsewhere classified

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • angioma serpiginosum (L81.7)
    • Henoch(-Schönlein) purpura (D69.0)
    • hypersensitivity angiitis (M31.0)
    • lupus panniculitis (L93.2)
    • panniculitis NOS (M79.3)
    • panniculitis of neck and back (M54.0-)
    • polyarteritis nodosa (M30.0)
    • relapsing panniculitis (M35.6)
    • rheumatoid vasculitis (M05.2)
    • serum sickness (T80.6-)
    • urticaria (L50.-)
    • Wegener's granulomatosis (M31.3-)
ICD-10-CM Codes Adjacent To M31.3
M30 Polyarteritis nodosa and related conditions
M30.0 Polyarteritis nodosa
M30.1 Polyarteritis with lung involvement [Churg-Strauss]
M30.2 Juvenile polyarteritis
M30.3 Mucocutaneous lymph node syndrome [Kawasaki]
M30.8 Other conditions related to polyarteritis nodosa
M31 Other necrotizing vasculopathies
M31.0 Hypersensitivity angiitis
M31.1 Thrombotic microangiopathy
M31.2 Lethal midline granuloma
M31.3 Wegener's granulomatosis
M31.30 …… without renal involvement
M31.31 …… with renal involvement
M31.4 Aortic arch syndrome [Takayasu]
M31.5 Giant cell arteritis with polymyalgia rheumatica
M31.6 Other giant cell arteritis
M31.7 Microscopic polyangiitis
M31.8 Other specified necrotizing vasculopathies
M31.9 Necrotizing vasculopathy, unspecified
M32 Systemic lupus erythematosus (SLE)
M32.0 Drug-induced systemic lupus erythematosus

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.