2020 ICD-10-CM Diagnosis Code M31.4

Aortic arch syndrome [Takayasu]

    2016 2017 2018 2019 2020 Billable/Specific Code
  • M31.4 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM M31.4 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of M31.4 - other international versions of ICD-10 M31.4 may differ.
The following code(s) above M31.4 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to M31.4:
  • M00-M99
    2020 ICD-10-CM Range M00-M99

    Diseases of the musculoskeletal system and connective tissue

    Note
    • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
    Type 2 Excludes
    • arthropathic psoriasis (L40.5-)
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • compartment syndrome (traumatic) (T79.A-)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the musculoskeletal system and connective tissue
  • M30-M36
    2020 ICD-10-CM Range M30-M36

    Systemic connective tissue disorders

    Includes
    • autoimmune disease NOS
    • collagen (vascular) disease NOS
    • systemic autoimmune disease
    • systemic collagen (vascular) disease
    Type 1 Excludes
    • autoimmune disease, single organ or single cell-type -code to relevant condition category
    Systemic connective tissue disorders
Approximate Synonyms
  • Takayasu's disease
  • Takayasus disease
Clinical Information
  • A chronic inflammatory process that affects the aorta and its primary branches, such as the brachiocephalic artery (brachiocephalic trunk) and carotid arteries. It results in progressive arterial stenosis, occlusion, and aneurysm formation. The pulse in the arm is hard to detect. Patients with aortitis syndrome often exhibit retinopathy.
  • A large vessel vasculitis affecting the aorta and its branches. It usually affects young females. It causes vascular obstruction, resulting in asymmetric pulses.
ICD-10-CM M31.4 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 545 Connective tissue disorders with mcc
  • 546 Connective tissue disorders with cc
  • 547 Connective tissue disorders without cc/mcc

Convert M31.4 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to M31.4:
  • Type 1 Excludes: I77.6
    ICD-10-CM Diagnosis Code I77.6

    Arteritis, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Aortitis NOS
    • Endarteritis NOS
    Type 1 Excludes

Diagnosis Index entries containing back-references to M31.4:
  • Arteritis I77.6
    ICD-10-CM Diagnosis Code I77.6

    Arteritis, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Aortitis NOS
    • Endarteritis NOS
    Type 1 Excludes
    • aortic arch M31.4
    • brachiocephalic M31.4
    • young female aortic arch syndrome M31.4
  • Disease, diseased - see also Syndrome
    • pulseless M31.4
  • Syndrome - see also Disease
  • Takayasu's disease or syndrome M31.4

ICD-10-CM Codes Adjacent To M31.4
M30.2 Juvenile polyarteritis
M30.3 Mucocutaneous lymph node syndrome [Kawasaki]
M30.8 Other conditions related to polyarteritis nodosa
M31 Other necrotizing vasculopathies
M31.0 Hypersensitivity angiitis
M31.1 Thrombotic microangiopathy
M31.2 Lethal midline granuloma
M31.3 Wegener's granulomatosis
M31.30 …… without renal involvement
M31.31 …… with renal involvement
M31.4 Aortic arch syndrome [Takayasu]
M31.5 Giant cell arteritis with polymyalgia rheumatica
M31.6 Other giant cell arteritis
M31.7 Microscopic polyangiitis
M31.8 Other specified necrotizing vasculopathies
M31.9 Necrotizing vasculopathy, unspecified
M32 Systemic lupus erythematosus (SLE)
M32.0 Drug-induced systemic lupus erythematosus
M32.1 Systemic lupus erythematosus with organ or system involvement
M32.10 Systemic lupus erythematosus, organ or system involvement unspecified
M32.11 Endocarditis in systemic lupus erythematosus

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.