Dermatopolymyositis M33- >

Clinical Information
  • A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (from Adams et al., Principles of Neurology, 6th ed, pp1405-6)
  • An inflammatory muscle disease accompanied by muscle weakness and skin rash
  • Progressive condition characterized by symmetric proximal muscular weakness with elevated serum levels of muscle enzymes and a skin rash, typically a purplish-red erythema on the face, and edema of the eyelids and periorbital tissue; affected muscle tissue shows degeneration of fibers with a chronic inflammatory reaction; occurs in children and adults, and in the latter may be associated with visceral cancer or other disorders of connective tissue.
Codes
  • M33 Dermatopolymyositis
    • M33.0 Juvenile dermatomyositis
      • M33.00 …… organ involvement unspecified
      • M33.01 …… with respiratory involvement
      • M33.02 …… with myopathy
      • M33.03 …… without myopathy
      • M33.09 …… with other organ involvement
    • M33.1 Other dermatomyositis
      • M33.10 …… organ involvement unspecified
      • M33.11 …… with respiratory involvement
      • M33.12 …… with myopathy
      • M33.13 …… without myopathy
      • M33.19 …… with other organ involvement
    • M33.2 Polymyositis
      • M33.20 …… organ involvement unspecified
      • M33.21 …… with respiratory involvement
      • M33.22 …… with myopathy
      • M33.29 …… with other organ involvement
    • M33.9 Dermatopolymyositis, unspecified
      • M33.90 …… organ involvement unspecified
      • M33.91 …… with respiratory involvement
      • M33.92 …… with myopathy
      • M33.93 …… without myopathy
      • M33.99 …… with other organ involvement