2020 ICD-10-CM Diagnosis Code M33.01

Juvenile dermatomyositis with respiratory involvement

    2016 2017 2018 - Revised Code 2019 2020 Billable/Specific Code
  • M33.01 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM M33.01 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of M33.01 - other international versions of ICD-10 M33.01 may differ.
The following code(s) above M33.01 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to M33.01:
  • M00-M99
    2020 ICD-10-CM Range M00-M99

    Diseases of the musculoskeletal system and connective tissue

    Note
    • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
    Type 2 Excludes
    • arthropathic psoriasis (L40.5-)
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • compartment syndrome (traumatic) (T79.A-)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the musculoskeletal system and connective tissue
  • M30-M36
    2020 ICD-10-CM Range M30-M36

    Systemic connective tissue disorders

    Includes
    • autoimmune disease NOS
    • collagen (vascular) disease NOS
    • systemic autoimmune disease
    • systemic collagen (vascular) disease
    Type 1 Excludes
    • autoimmune disease, single organ or single cell-type -code to relevant condition category
    Systemic connective tissue disorders
Approximate Synonyms
  • Juvenile dermatomyositis co-occurrent with respiratory involvement
  • Juvenile dermatopolymyositis w respiratory involvement
  • Juvenile dermatopolymyositis with lung involvement
ICD-10-CM M33.01 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 545 Connective tissue disorders with mcc
  • 546 Connective tissue disorders with cc
  • 547 Connective tissue disorders without cc/mcc

Convert M33.01 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): Revised code
    • New description: Juvenile dermatomyositis with respiratory involvement
    • 2017 description: Juvenile dermatopolymyositis with respiratory involvement
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to M33.01:
  • Type 1 Excludes: J99
    ICD-10-CM Diagnosis Code J99

    Respiratory disorders in diseases classified elsewhere

      2016 2017 2018 2019 2020 Billable/Specific Code Manifestation Code
    Code First
    • underlying disease, such as:
    • amyloidosis (E85.-)
    • ankylosing spondylitis (M45)
    • congenital syphilis (A50.5)
    • cryoglobulinemia (D89.1)
    • early congenital syphilis (A50.0)
    • plasminogen deficiency (E88.02)
    • schistosomiasis (B65.0-B65.9)
    Type 1 Excludes

Diagnosis Index entries containing back-references to M33.01:
  • Dermatomyositis (acute) (chronic) - see also Dermatopolymyositis
    • juvenile M33.00
      ICD-10-CM Diagnosis Code M33.00

      Juvenile dermatomyositis, organ involvement unspecified

        2016 2017 2018 - Revised Code 2019 2020 Billable/Specific Code
      • with
        • respiratory involvement M33.01
  • Dermatopolymyositis M33.90
    ICD-10-CM Diagnosis Code M33.90

    Dermatopolymyositis, unspecified, organ involvement unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    • juvenile M33.00
      ICD-10-CM Diagnosis Code M33.00

      Juvenile dermatomyositis, organ involvement unspecified

        2016 2017 2018 - Revised Code 2019 2020 Billable/Specific Code
      • with
        • respiratory involvement M33.01

ICD-10-CM Codes Adjacent To M33.01
M32.12 Pericarditis in systemic lupus erythematosus
M32.13 Lung involvement in systemic lupus erythematosus
M32.14 Glomerular disease in systemic lupus erythematosus
M32.15 Tubulo-interstitial nephropathy in systemic lupus erythematosus
M32.19 Other organ or system involvement in systemic lupus erythematosus
M32.8 Other forms of systemic lupus erythematosus
M32.9 Systemic lupus erythematosus, unspecified
M33 Dermatopolymyositis
M33.0 Juvenile dermatomyositis
M33.00 …… organ involvement unspecified
M33.01 …… with respiratory involvement
M33.02 …… with myopathy
M33.03 …… without myopathy
M33.09 …… with other organ involvement
M33.1 Other dermatomyositis
M33.10 …… organ involvement unspecified
M33.11 …… with respiratory involvement
M33.12 …… with myopathy
M33.13 …… without myopathy
M33.19 …… with other organ involvement
M33.2 Polymyositis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.