2020 ICD-10-CM Diagnosis Code M33.2

Polymyositis

    2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
  • M33.2 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2020 edition of ICD-10-CM M33.2 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of M33.2 - other international versions of ICD-10 M33.2 may differ.
The following code(s) above M33.2 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to M33.2:
  • M00-M99
    2020 ICD-10-CM Range M00-M99

    Diseases of the musculoskeletal system and connective tissue

    Note
    • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
    Type 2 Excludes
    • arthropathic psoriasis (L40.5-)
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • compartment syndrome (traumatic) (T79.A-)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the musculoskeletal system and connective tissue
  • M30-M36
    2020 ICD-10-CM Range M30-M36

    Systemic connective tissue disorders

    Includes
    • autoimmune disease NOS
    • collagen (vascular) disease NOS
    • systemic autoimmune disease
    • systemic collagen (vascular) disease
    Type 1 Excludes
    • autoimmune disease, single organ or single cell-type -code to relevant condition category
    Systemic connective tissue disorders
Clinical Information
  • An idiopathic inflammatory disorder affecting the muscles. It presents with symmetrical proximal muscle weakness and elevated skeletal muscle enzymes.
  • An inflammatory disease of the muscles closest to the center of the body. It causes weakness, inability to stand, climb stairs, lift, or reach. It may also cause muscle pain and difficulty swallowing, and may affect the lungs and heart. Having polymyositis increases the risk of certain types of cancer.
  • Diseases characterized by inflammation involving multiple muscles. This may occur as an acute or chronic condition associated with medication toxicity (drug toxicity); connective tissue diseases; infections; malignant neoplasms; and other disorders. The term polymyositis is frequently used to refer to a specific clinical entity characterized by subacute or slowly progressing symmetrical weakness primarily affecting the proximal limb and trunk muscles. The illness may occur at any age, but is most frequent in the fourth to sixth decade of life. Weakness of pharyngeal and laryngeal muscles, interstitial lung disease, and inflammation of the myocardium may also occur. Muscle biopsy reveals widespread destruction of segments of muscle fibers and an inflammatory cellular response. (Adams et al., Principles of Neurology, 6th ed, pp1404-9)
  • Inflammation of a number of voluntary muscles simultaneously.
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to M33.2:
  • Code Also: I27.21
    ICD-10-CM Diagnosis Code I27.21

    Secondary pulmonary arterial hypertension

      2018 - New Code 2019 2020 Billable/Specific Code
    Applicable To
    • (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
    • (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
    Code Also
    • associated conditions if applicable, or adverse effects of drugs or toxins, such as:
    • adverse effect of appetite depressants (T50.5X5)
    • congenital heart disease (Q20-Q28)
    • human immunodeficiency virus [HIV] disease (B20)
    • polymyositis (M33.2-)
    • portal hypertension (K76.6)
    • rheumatoid arthritis (M05.-)
    • schistosomiasis (B65.-)
    • Sjögren syndrome (M35.0-)
    • systemic sclerosis (M34.-)
  • Type 1 Excludes: G72
    ICD-10-CM Diagnosis Code G72

    Other and unspecified myopathies

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • arthrogryposis multiplex congenita (Q74.3)
    • dermatopolymyositis (M33.-)
    • ischemic infarction of muscle (M62.2-)
    • myositis (M60.-)
    • polymyositis (M33.2.-)
ICD-10-CM Codes Adjacent To M33.2
M33.01 …… with respiratory involvement
M33.02 …… with myopathy
M33.03 …… without myopathy
M33.09 …… with other organ involvement
M33.1 Other dermatomyositis
M33.10 …… organ involvement unspecified
M33.11 …… with respiratory involvement
M33.12 …… with myopathy
M33.13 …… without myopathy
M33.19 …… with other organ involvement
M33.2 Polymyositis
M33.20 …… organ involvement unspecified
M33.21 …… with respiratory involvement
M33.22 …… with myopathy
M33.29 …… with other organ involvement
M33.9 Dermatopolymyositis, unspecified
M33.90 …… organ involvement unspecified
M33.91 …… with respiratory involvement
M33.92 …… with myopathy
M33.93 …… without myopathy
M33.99 …… with other organ involvement

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.