2020 ICD-10-CM Diagnosis Code M34

Systemic sclerosis [scleroderma]

    2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
  • M34 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2020 edition of ICD-10-CM M34 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of M34 - other international versions of ICD-10 M34 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as M34. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • circumscribed scleroderma (
    ICD-10-CM Diagnosis Code L94.0

    Localized scleroderma [morphea]

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Circumscribed scleroderma
    L94.0
    )
  • neonatal scleroderma (
    ICD-10-CM Diagnosis Code P83.88

    Other specified conditions of integument specific to newborn

      2018 - New Code 2019 2020 Billable/Specific Code Code on Newborn Record POA Exempt
    Applicable To
    • Bronze baby syndrome
    • Neonatal scleroderma
    • Urticaria neonatorum
    P83.88
    )
The following code(s) above M34 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to M34:
  • M00-M99
    2020 ICD-10-CM Range M00-M99

    Diseases of the musculoskeletal system and connective tissue

    Note
    • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
    Type 2 Excludes
    • arthropathic psoriasis (L40.5-)
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • compartment syndrome (traumatic) (T79.A-)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the musculoskeletal system and connective tissue
  • M30-M36
    2020 ICD-10-CM Range M30-M36

    Systemic connective tissue disorders

    Includes
    • autoimmune disease NOS
    • collagen (vascular) disease NOS
    • systemic autoimmune disease
    • systemic collagen (vascular) disease
    Type 1 Excludes
    • autoimmune disease, single organ or single cell-type -code to relevant condition category
    Systemic connective tissue disorders
Clinical Information
  • A chronic disorder, possibly autoimmune, marked by excessive production of collagen which results in hardening and thickening of body tissues. The two types of systemic scleroderma, limited cutaneous and diffuse cutaneous are classified with focus on the extent of affected skin. A relationship exists between the extent of skin area affected and degree of internal organ/system involvement. Systemic scleroderma can manifest itself in pulmonary fibrosis, raynaud's syndrome, digestive system telangiectasias, renal hypertension and/or pulmonary hypertension.
  • A chronic multi-system disorder of connective tissue. It is characterized by sclerosis in the skin, the lungs, the heart, the gastrointestinal tract, the kidneys, and the musculoskeletal system. Other important features include diseased small blood vessels and autoantibodies. The disorder is named for its most prominent feature (hard skin), and classified into subsets by the extent of skin thickening: limited scleroderma and diffuse scleroderma.
  • A disease that is marked by hardening and thickening of skin, connective tissue that surrounds other tissues and organs, and blood vessels.
  • A rare, chronic disease characterized by excessive deposits of collagen in the skin or other organs
  • Systemic disorder of the connective tissue; manifested by hardening and thickening of the skin, by abnormalities involving the microvasculature and larger vessels, and by fibrotic degenerative changes in various body organs including the heart, lungs, kidneys, and gastrointestinal tract.
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to M34:
  • Code Also: I27.21
    ICD-10-CM Diagnosis Code I27.21

    Secondary pulmonary arterial hypertension

      2018 - New Code 2019 2020 Billable/Specific Code
    Applicable To
    • (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
    • (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
    Code Also
    • associated conditions if applicable, or adverse effects of drugs or toxins, such as:
    • adverse effect of appetite depressants (T50.5X5)
    • congenital heart disease (Q20-Q28)
    • human immunodeficiency virus [HIV] disease (B20)
    • polymyositis (M33.2-)
    • portal hypertension (K76.6)
    • rheumatoid arthritis (M05.-)
    • schistosomiasis (B65.-)
    • Sjögren syndrome (M35.0-)
    • systemic sclerosis (M34.-)
  • Code First: K31.84
    ICD-10-CM Diagnosis Code K31.84

    Gastroparesis

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Gastroparalysis
    Code First
  • Type 1 Excludes: L93
    ICD-10-CM Diagnosis Code L93

    Lupus erythematosus

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Use Additional
    • code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
ICD-10-CM Codes Adjacent To M34
M33.20 …… organ involvement unspecified
M33.21 …… with respiratory involvement
M33.22 …… with myopathy
M33.29 …… with other organ involvement
M33.9 Dermatopolymyositis, unspecified
M33.90 …… organ involvement unspecified
M33.91 …… with respiratory involvement
M33.92 …… with myopathy
M33.93 …… without myopathy
M33.99 …… with other organ involvement
M34 Systemic sclerosis [scleroderma]
M34.0 Progressive systemic sclerosis
M34.1 CR(E)ST syndrome
M34.2 Systemic sclerosis induced by drug and chemical
M34.8 Other forms of systemic sclerosis
M34.81 Systemic sclerosis with lung involvement
M34.82 Systemic sclerosis with myopathy
M34.83 Systemic sclerosis with polyneuropathy
M34.89 Other systemic sclerosis
M34.9 Systemic sclerosis, unspecified
M35 Other systemic involvement of connective tissue

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.