2020 ICD-10-CM Diagnosis Code M34.0

Progressive systemic sclerosis

    2016 2017 2018 2019 2020 Billable/Specific Code
  • M34.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM M34.0 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of M34.0 - other international versions of ICD-10 M34.0 may differ.
The following code(s) above M34.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to M34.0:
  • M00-M99
    2020 ICD-10-CM Range M00-M99

    Diseases of the musculoskeletal system and connective tissue

    Note
    • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
    Type 2 Excludes
    • arthropathic psoriasis (L40.5-)
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • compartment syndrome (traumatic) (T79.A-)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the musculoskeletal system and connective tissue
  • M30-M36
    2020 ICD-10-CM Range M30-M36

    Systemic connective tissue disorders

    Includes
    • autoimmune disease NOS
    • collagen (vascular) disease NOS
    • systemic autoimmune disease
    • systemic collagen (vascular) disease
    Type 1 Excludes
    • autoimmune disease, single organ or single cell-type -code to relevant condition category
    Systemic connective tissue disorders
  • M34
    ICD-10-CM Diagnosis Code M34

    Systemic sclerosis [scleroderma]

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • circumscribed scleroderma (L94.0)
    • neonatal scleroderma (P83.88)
    Systemic sclerosis [scleroderma]
Clinical Information
  • A chronic disorder, possibly autoimmune, marked by excessive production of collagen which results in hardening and thickening of body tissues. The two types of systemic scleroderma, limited cutaneous and diffuse cutaneous are classified with focus on the extent of affected skin. A relationship exists between the extent of skin area affected and degree of internal organ/system involvement. Systemic scleroderma can manifest itself in pulmonary fibrosis, raynaud's syndrome, digestive system telangiectasias, renal hypertension and/or pulmonary hypertension.
  • A chronic multi-system disorder of connective tissue. It is characterized by sclerosis in the skin, the lungs, the heart, the gastrointestinal tract, the kidneys, and the musculoskeletal system. Other important features include diseased small blood vessels and autoantibodies. The disorder is named for its most prominent feature (hard skin), and classified into subsets by the extent of skin thickening: limited scleroderma and diffuse scleroderma.
  • A disease that is marked by hardening and thickening of skin, connective tissue that surrounds other tissues and organs, and blood vessels.
  • A rare, chronic disease characterized by excessive deposits of collagen in the skin or other organs
  • Systemic disorder of the connective tissue; manifested by hardening and thickening of the skin, by abnormalities involving the microvasculature and larger vessels, and by fibrotic degenerative changes in various body organs including the heart, lungs, kidneys, and gastrointestinal tract.
ICD-10-CM M34.0 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 545 Connective tissue disorders with mcc
  • 546 Connective tissue disorders with cc
  • 547 Connective tissue disorders without cc/mcc

Convert M34.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to M34.0:
  • Code First: J84.17
    ICD-10-CM Diagnosis Code J84.17

    Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

      2016 2017 2018 2019 2020 Billable/Specific Code Manifestation Code
    Applicable To
    • Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
    • Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
    • Organizing pneumonia due to collagen vascular disease
    • Organizing pneumonia in diseases classified elsewhere
    Code First
    • underlying disease, such as:
    • progressive systemic sclerosis (M34.0)
    • rheumatoid arthritis (M05.00-M06.9)
    • systemic lupus erythematosis (M32.0-M32.9)

Diagnosis Index entries containing back-references to M34.0:
  • Sclerosis, sclerotic
    • systemic M34.9
      ICD-10-CM Diagnosis Code M34.9

      Systemic sclerosis, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
      • progressive M34.0
    • progressive, systemic M34.0

ICD-10-CM Codes Adjacent To M34.0
M33.21 …… with respiratory involvement
M33.22 …… with myopathy
M33.29 …… with other organ involvement
M33.9 Dermatopolymyositis, unspecified
M33.90 …… organ involvement unspecified
M33.91 …… with respiratory involvement
M33.92 …… with myopathy
M33.93 …… without myopathy
M33.99 …… with other organ involvement
M34 Systemic sclerosis [scleroderma]
M34.0 Progressive systemic sclerosis
M34.1 CR(E)ST syndrome
M34.2 Systemic sclerosis induced by drug and chemical
M34.8 Other forms of systemic sclerosis
M34.81 Systemic sclerosis with lung involvement
M34.82 Systemic sclerosis with myopathy
M34.83 Systemic sclerosis with polyneuropathy
M34.89 Other systemic sclerosis
M34.9 Systemic sclerosis, unspecified
M35 Other systemic involvement of connective tissue
M35.0 Sicca syndrome [Sjögren]

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.