2020 ICD-10-CM Diagnosis Code M34.1

CR(E)ST syndrome

    2016 2017 2018 2019 2020 Billable/Specific Code
  • M34.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM M34.1 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of M34.1 - other international versions of ICD-10 M34.1 may differ.
Applicable To
  • Combination of calcinosis, Raynaud's phenomenon, esophageal dysfunction, sclerodactyly, telangiectasia
The following code(s) above M34.1 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to M34.1:
  • M00-M99
    2020 ICD-10-CM Range M00-M99

    Diseases of the musculoskeletal system and connective tissue

    Note
    • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
    Type 2 Excludes
    • arthropathic psoriasis (L40.5-)
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • compartment syndrome (traumatic) (T79.A-)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the musculoskeletal system and connective tissue
  • M30-M36
    2020 ICD-10-CM Range M30-M36

    Systemic connective tissue disorders

    Includes
    • autoimmune disease NOS
    • collagen (vascular) disease NOS
    • systemic autoimmune disease
    • systemic collagen (vascular) disease
    Type 1 Excludes
    • autoimmune disease, single organ or single cell-type -code to relevant condition category
    Systemic connective tissue disorders
  • M34
    ICD-10-CM Diagnosis Code M34

    Systemic sclerosis [scleroderma]

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • circumscribed scleroderma (L94.0)
    • neonatal scleroderma (P83.88)
    Systemic sclerosis [scleroderma]
Approximate Synonyms
  • Crest syndrome
Clinical Information
  • A mild form of limited scleroderma, a multi-system disorder. Its features include symptoms of calcinosis; raynaud disease; esophageal motility disorders; sclerodactyly, and telangiectasis. When the defect in esophageal function is not prominent, it is known as crst syndrome.
  • A variant of systemic sclerosis characterized by calcinosis, raynaud phenomenon, esophageal motility disorders, sclerodactyly, and telangiectasia.
ICD-10-CM M34.1 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 545 Connective tissue disorders with mcc
  • 546 Connective tissue disorders with cc
  • 547 Connective tissue disorders without cc/mcc

Convert M34.1 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to M34.1:
  • Calcinosis (interstitial) (tumoral) (universalis) E83.59
    ICD-10-CM Diagnosis Code E83.59

    Other disorders of calcium metabolism

      2016 2017 2018 2019 2020 Billable/Specific Code
    • with Raynaud's phenomenon, esophageal dysfunction, sclerodactyly, telangiectasia M34.1 (CREST syndrome)
  • CREST syndrome M34.1
  • CRST syndrome M34.1

ICD-10-CM Codes Adjacent To M34.1
M33.22 …… with myopathy
M33.29 …… with other organ involvement
M33.9 Dermatopolymyositis, unspecified
M33.90 …… organ involvement unspecified
M33.91 …… with respiratory involvement
M33.92 …… with myopathy
M33.93 …… without myopathy
M33.99 …… with other organ involvement
M34 Systemic sclerosis [scleroderma]
M34.0 Progressive systemic sclerosis
M34.1 CR(E)ST syndrome
M34.2 Systemic sclerosis induced by drug and chemical
M34.8 Other forms of systemic sclerosis
M34.81 Systemic sclerosis with lung involvement
M34.82 Systemic sclerosis with myopathy
M34.83 Systemic sclerosis with polyneuropathy
M34.89 Other systemic sclerosis
M34.9 Systemic sclerosis, unspecified
M35 Other systemic involvement of connective tissue
M35.0 Sicca syndrome [Sjögren]
M35.00 Sicca syndrome, unspecified

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.