1. ICD-10-CM Codes
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2. M00-M99 Diseases of the musculoskeletal system and connective tissue
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3. M30-M36 Systemic connective tissue disorders
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4. M35- Other systemic involvement of connective tissue
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5. 2022 ICD-10-CM Diagnosis Code M35.0

2022 ICD-10-CM Diagnosis Code M35.0

Sjögren syndrome

2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code

• M35.0 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
• Short description: Sjogren syndrome
• The 2022 edition of ICD-10-CM M35.0 became effective on October 1, 2021.
• This is the American ICD-10-CM version of M35.0 - other international versions of ICD-10 M35.0 may differ.

• A chronic inflammation of the tear and salivary glands, often accompanied by rheumatoid arthritis and the presence of autoantibodies in the blood
• An autoimmune disease that affects the tear glands and salivary glands, and may affect glands in the stomach, pancreas, and intestines. The disease causes dry eyes and mouth, and may cause dryness in the nose, throat, air passages, skin, and vagina. It may also cause inflammation in the joints, muscles, and skin; pneumonia; tingling in the fingers and toes; and fatigue. It often occurs with rheumatoid arthritis or other connective tissue diseases.
• An autoimmune disorder affecting the salivary and lacrimal glands. Morphologically, it is characterized by the presence of lymphocytic and plasmacytic infiltrates which cause destruction of these glands. It results in dry mouth and dry eyes. It may be associated with the presence of other autoimmune disorders, including rheumatoid arthritis and lupus erythematosus.
• Chronic inflammatory and autoimmune disease in which the salivary and lacrimal glands undergo progressive destruction by lymphocytes and plasma cells resulting in decreased production of saliva and tears. The primary form, often called sicca syndrome, involves both keratoconjunctivitis sicca and xerostomia. The secondary form includes, in addition, the presence of a connective tissue disease, usually rheumatoid arthritis.
• Sjogren's syndrome is a disease that causes dryness in your mouth and eyes. It can also lead to dryness in other places that need moisture, such as your nose, throat and skin. Most people who get sjogren's syndrome are older than 40. Nine of 10 are women. Sjogren's syndrome is sometimes linked to rheumatic problems such as rheumatoid arthritis.sjogren's syndrome is an autoimmune disease. If you have an autoimmune disease, your immune system, which is supposed to fight disease, mistakenly attacks parts of your own body. In sjogren's syndrome, your immune system attacks the glands that make tears and saliva. It may also affect your joints, lungs, kidneys, blood vessels, digestive organs and nerves. The main symptoms are:
  • dry eyes
  • dry mouth
  treatment focuses on relieving symptoms. nih: national institute of arthritis and musculoskeletal and skin diseases
• Symptom complex of unknown etiology, usually occurring in middle-aged or older women, marked by the triad of keratoconjunctivitis sicca with or without lacrimal gland enlargement, xerostomia with or without salivary gland enlargement, and the presence of a connective tissue disease, usually rheumatoid arthritis but sometimes systemic lupus erythematosus, scleroderma, or polymyositis; an abnormal immune response has been implicated.

• 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
• 2017 (effective 10/1/2016): No change
• 2018 (effective 10/1/2017): No change
• 2019 (effective 10/1/2018): No change
• 2020 (effective 10/1/2019): No change
• 2021 (effective 10/1/2020): No change
• 2022 (effective 10/1/2021): No change

• Code Also: I27.21
  ICD-10-CM Diagnosis Code I27.21

  Secondary pulmonary arterial hypertension

  2018 - New Code 2019 2020 2021 2022 Billable/Specific Code

  Applicable To

  • (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
  • (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension

  Code Also

  • associated conditions if applicable, or adverse effects of drugs or toxins, such as:
  • adverse effect of appetite depressants (T50.5X5)
  • congenital heart disease (Q20-Q28)
  • human immunodeficiency virus [HIV] disease (B20)
  • polymyositis (M33.2-)
  • portal hypertension (K76.6)
  • rheumatoid arthritis (M05.-)
  • schistosomiasis (B65.-)
  • Sjögren syndrome (M35.0-)
  • systemic sclerosis (M34.-)
• Type 1 Excludes: K11.8
  , R68.2
  ICD-10-CM Diagnosis Code K11.8

  Other diseases of salivary glands

  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code

  Applicable To

  • Benign lymphoepithelial lesion of salivary gland
  • Mikulicz' disease
  • Necrotizing sialometaplasia
  • Sialectasia
  • Stenosis of salivary duct
  • Stricture of salivary duct

  Type 1 Excludes

  • Sjögren syndrome (M35.0-)
  ICD-10-CM Diagnosis Code R68.2

  Dry mouth, unspecified

  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code

  Type 1 Excludes

  • dry mouth due to dehydration (E86.0)
  • dry mouth due to Sjögren syndrome (M35.0-)
  • salivary gland hyposecretion (K11.7)

• Keratoconjunctivitis H16.20-
  ICD-10-CM Diagnosis Code H16.20-

  Unspecified keratoconjunctivitis

  2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code

  Applicable To

  • Superficial keratitis with conjunctivitis NOS
  • sicca (Sjögren's) M35.0-

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.