2020 ICD-10-CM Diagnosis Code N04

Nephrotic syndrome

    2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
  • N04 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2020 edition of ICD-10-CM N04 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of N04 - other international versions of ICD-10 N04 may differ.
Includes
Includes Help
"Includes" further defines, or give examples of, the content of the code or category.
  • congenital nephrotic syndrome
  • lipoid nephrosis
The following code(s) above N04 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to N04:
  • N00-N99
    2020 ICD-10-CM Range N00-N99

    Diseases of the genitourinary system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the genitourinary system
  • N00-N08
    2020 ICD-10-CM Range N00-N08

    Glomerular diseases

    Code Also
    • any associated kidney failure (N17-N19).
    Type 1 Excludes
    • hypertensive chronic kidney disease (I12.-)
    Glomerular diseases
Clinical Information
  • A collection of symptoms that include severe edema, proteinuria, and hypoalbuminemia; it is indicative of renal dysfunction.
  • A condition characterized by severe proteinuria, greater than 3.5 g/day in an average adult. The substantial loss of protein in the urine results in complications such as hypoproteinemia; generalized edema; hypertension; and hyperlipidemias. Diseases associated with nephrotic syndrome generally cause chronic kidney dysfunction.
  • A kidney disease characterized by a high protein level in urine
  • A kidney disease with no or minimal histological glomerular changes on light microscopy and with no immune deposits. It is characterized by lipid accumulation in the epithelial cells of kidney tubules and in the urine. Patients usually show nephrotic syndrome indicating the presence of proteinuria with accompanying edema.
  • A rare autosomal recessive inherited nephrotic syndrome that is present in the first week of life. It manifests with edema and proteinuria and usually has a poor prognosis.
  • Diseases involving defective kidney glomeruli, characterized by massive proteinuria and lipiduria with varying degrees of edema, hypoalbuminemia, and hyperlipidemia.
  • Nephrotic syndrome: twenty-four hour urine protein > three grams. May be associated with hypoalbuminemia and hypercholesterolemia.
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to N04:
  • Type 1 Excludes: Q63
    ICD-10-CM Diagnosis Code Q63

    Other congenital malformations of kidney

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • congenital nephrotic syndrome (N04.-)
ICD-10-CM Codes Adjacent To N04
N03.0 Chronic nephritic syndrome with minor glomerular abnormality
N03.1 Chronic nephritic syndrome with focal and segmental glomerular lesions
N03.2 Chronic nephritic syndrome with diffuse membranous glomerulonephritis
N03.3 Chronic nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N03.4 Chronic nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N03.5 Chronic nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
N03.6 Chronic nephritic syndrome with dense deposit disease
N03.7 Chronic nephritic syndrome with diffuse crescentic glomerulonephritis
N03.8 Chronic nephritic syndrome with other morphologic changes
N03.9 Chronic nephritic syndrome with unspecified morphologic changes
N04 Nephrotic syndrome
N04.0 Nephrotic syndrome with minor glomerular abnormality
N04.1 Nephrotic syndrome with focal and segmental glomerular lesions
N04.2 Nephrotic syndrome with diffuse membranous glomerulonephritis
N04.3 Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
N04.4 Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
N04.5 Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
N04.6 Nephrotic syndrome with dense deposit disease
N04.7 Nephrotic syndrome with diffuse crescentic glomerulonephritis
N04.8 Nephrotic syndrome with other morphologic changes
N04.9 Nephrotic syndrome with unspecified morphologic changes

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.