2022 ICD-10-CM Diagnosis Code N04.A

Nephrotic syndrome with C3 glomerulonephritis

    2021 - New Code 2022 Billable/Specific Code
  • N04.A is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2022 edition of ICD-10-CM N04.A became effective on October 1, 2021.
  • This is the American ICD-10-CM version of N04.A - other international versions of ICD-10 N04.A may differ.
Applicable To
  • Nephrotic syndrome with C3 glomerulopathy
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as N04.A. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Nephrotic syndrome (with C3 glomerulopathy) with dense deposit disease (
    ICD-10-CM Diagnosis Code N04.6

    Nephrotic syndrome with dense deposit disease

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
    Applicable To
    • Nephrotic syndrome with C3 glomerulopathy with dense deposit disease
    • Nephrotic syndrome with membranoproliferative glomerulonephritis, type 2
    N04.6
    )
The following code(s) above N04.A contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to N04.A:
  • N00-N99
    2022 ICD-10-CM Range N00-N99

    Diseases of the genitourinary system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the genitourinary system
  • N00-N08
    2022 ICD-10-CM Range N00-N08

    Glomerular diseases

    Code Also
    • any associated kidney failure (N17-N19).
    Type 1 Excludes
    • hypertensive chronic kidney disease (I12.-)
    Glomerular diseases
  • N04
    ICD-10-CM Diagnosis Code N04

    Nephrotic syndrome

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Includes
    • congenital nephrotic syndrome
    • lipoid nephrosis
    Nephrotic syndrome
ICD-10-CM N04.A is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):
  • 698 Other kidney and urinary tract diagnoses with mcc
  • 699 Other kidney and urinary tract diagnoses with cc
  • 700 Other kidney and urinary tract diagnoses without cc/mcc
Code History
  • 2021 (effective 10/1/2020): New code
  • 2022 (effective 10/1/2021): No change
Code annotations containing back-references to N04.A:
  • Type 1 Excludes: N04.5
    , N04.5
    ICD-10-CM Diagnosis Code N04.5

    Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
    Applicable To
    • Nephrotic syndrome with membranoproliferative glomerulonephritis, types 1 and 3, or NOS
    Type 1 Excludes
    • Nephrotic syndrome with C3 glomerulonephritis (N04.A)
    • Nephrotic syndrome with C3 glomerulopathy (N04.A)
    ICD-10-CM Diagnosis Code N04.5

    Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis

      2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
    Applicable To
    • Nephrotic syndrome with membranoproliferative glomerulonephritis, types 1 and 3, or NOS
    Type 1 Excludes
    • Nephrotic syndrome with C3 glomerulonephritis (N04.A)
    • Nephrotic syndrome with C3 glomerulopathy (N04.A)

Diagnosis Index entries containing back-references to N04.A:

ICD-10-CM Codes Adjacent To N04.A
N04.0 Nephrotic syndrome with minor glomerular abnormality
N04.1 Nephrotic syndrome with focal and segmental glomerular lesions
N04.2 Nephrotic syndrome with diffuse membranous glomerulonephritis
N04.3 Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
N04.4 Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
N04.5 Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
N04.6 Nephrotic syndrome with dense deposit disease
N04.7 Nephrotic syndrome with diffuse crescentic glomerulonephritis
N04.8 Nephrotic syndrome with other morphologic changes
N04.9 Nephrotic syndrome with unspecified morphologic changes
N04.A Nephrotic syndrome with C3 glomerulonephritis
N05 Unspecified nephritic syndrome
N05.0 Unspecified nephritic syndrome with minor glomerular abnormality
N05.1 Unspecified nephritic syndrome with focal and segmental glomerular lesions
N05.2 Unspecified nephritic syndrome with diffuse membranous glomerulonephritis
N05.3 Unspecified nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N05.4 Unspecified nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N05.5 Unspecified nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
N05.6 Unspecified nephritic syndrome with dense deposit disease
N05.7 Unspecified nephritic syndrome with diffuse crescentic glomerulonephritis
N05.8 Unspecified nephritic syndrome with other morphologic changes

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.