2020 ICD-10-CM Diagnosis Code N07

Hereditary nephropathy, not elsewhere classified

    2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
  • N07 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2020 edition of ICD-10-CM N07 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of N07 - other international versions of ICD-10 N07 may differ.
Type 2 Excludes
Type 2 Excludes Help
A type 2 excludes note represents "not included here". A type 2 excludes note indicates that the condition excluded is not part of the condition it is excluded from but a patient may have both conditions at the same time. When a type 2 excludes note appears under a code it is acceptable to use both the code (N07) and the excluded code together.
  • Alport's syndrome (
    ICD-10-CM Diagnosis Code Q87.81

    Alport syndrome

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Use Additional
    • code to identify stage of chronic kidney disease (N18.1-N18.6)
    Q87.81-
    )
  • hereditary amyloid nephropathy (
    ICD-10-CM Diagnosis Code E85
    • E85 Amyloidosis
      • E85.0 Non-neuropathic heredofamilial amyloidosis
      • E85.1 Neuropathic heredofamilial amyloidosis
      • E85.2 Heredofamilial amyloidosis, unspecified
      • E85.3 Secondary systemic amyloidosis
      • E85.4 Organ-limited amyloidosis
      • E85.8 Other amyloidosis
        • E85.81 Light chain (AL) amyloidosis
        • E85.82 Wild-type transthyretin-related (ATTR) amyloi...
        • E85.89 Other amyloidosis
      • E85.9 Amyloidosis, unspecified
    E85.-
    )
  • nail patella syndrome (
    ICD-10-CM Diagnosis Code Q87.2

    Congenital malformation syndromes predominantly involving limbs

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Holt-Oram syndrome
    • Klippel-Trenaunay-Weber syndrome
    • Nail patella syndrome
    • Rubinstein-Taybi syndrome
    • Sirenomelia syndrome
    • Thrombocytopenia with absent radius [TAR] syndrome
    • VATER syndrome
    Q87.2
    )
  • non-neuropathic heredofamilial amyloidosis (
    ICD-10-CM Diagnosis Code E85
    • E85 Amyloidosis
      • E85.0 Non-neuropathic heredofamilial amyloidosis
      • E85.1 Neuropathic heredofamilial amyloidosis
      • E85.2 Heredofamilial amyloidosis, unspecified
      • E85.3 Secondary systemic amyloidosis
      • E85.4 Organ-limited amyloidosis
      • E85.8 Other amyloidosis
        • E85.81 Light chain (AL) amyloidosis
        • E85.82 Wild-type transthyretin-related (ATTR) amyloi...
        • E85.89 Other amyloidosis
      • E85.9 Amyloidosis, unspecified
    E85.-
    )
The following code(s) above N07 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to N07:
  • N00-N99
    2020 ICD-10-CM Range N00-N99

    Diseases of the genitourinary system

    Type 2 Excludes
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the genitourinary system
  • N00-N08
    2020 ICD-10-CM Range N00-N08

    Glomerular diseases

    Code Also
    • any associated kidney failure (N17-N19).
    Type 1 Excludes
    • hypertensive chronic kidney disease (I12.-)
    Glomerular diseases
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
ICD-10-CM Codes Adjacent To N07
N06.0 Isolated proteinuria with minor glomerular abnormality
N06.1 Isolated proteinuria with focal and segmental glomerular lesions
N06.2 Isolated proteinuria with diffuse membranous glomerulonephritis
N06.3 Isolated proteinuria with diffuse mesangial proliferative glomerulonephritis
N06.4 Isolated proteinuria with diffuse endocapillary proliferative glomerulonephritis
N06.5 Isolated proteinuria with diffuse mesangiocapillary glomerulonephritis
N06.6 Isolated proteinuria with dense deposit disease
N06.7 Isolated proteinuria with diffuse crescentic glomerulonephritis
N06.8 Isolated proteinuria with other morphologic lesion
N06.9 Isolated proteinuria with unspecified morphologic lesion
N07 Hereditary nephropathy, not elsewhere classified
N07.0 Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality
N07.1 Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions
N07.2 Hereditary nephropathy, not elsewhere classified with diffuse membranous glomerulonephritis
N07.3 Hereditary nephropathy, not elsewhere classified with diffuse mesangial proliferative glomerulonephritis
N07.4 Hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis
N07.5 Hereditary nephropathy, not elsewhere classified with diffuse mesangiocapillary glomerulonephritis
N07.6 Hereditary nephropathy, not elsewhere classified with dense deposit disease
N07.7 Hereditary nephropathy, not elsewhere classified with diffuse crescentic glomerulonephritis
N07.8 Hereditary nephropathy, not elsewhere classified with other morphologic lesions
N07.9 Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.