2023 ICD-10-CM Diagnosis Code Q00

Anencephaly and similar malformations

    2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
  • Q00 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2023 edition of ICD-10-CM Q00 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of Q00 - other international versions of ICD-10 Q00 may differ.
The following code(s) above Q00 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q00:
  • Q00-Q99
    2023 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change
ICD-10-CM Codes Adjacent To Q00
P96.1 Neonatal withdrawal symptoms from maternal use of drugs of addiction
P96.2 Withdrawal symptoms from therapeutic use of drugs in newborn
P96.3 Wide cranial sutures of newborn
P96.5 Complication to newborn due to (fetal) intrauterine procedure
P96.8 Other specified conditions originating in the perinatal period
P96.81 Exposure to (parental) (environmental) tobacco smoke in the perinatal period
P96.82 Delayed separation of umbilical cord
P96.83 Meconium staining
P96.89 Other specified conditions originating in the perinatal period
P96.9 Condition originating in the perinatal period, unspecified
Q00 Anencephaly and similar malformations
Q00.0 Anencephaly
Q00.1 Craniorachischisis
Q00.2 Iniencephaly
Q01 Encephalocele
Q01.0 Frontal encephalocele
Q01.1 Nasofrontal encephalocele
Q01.2 Occipital encephalocele
Q01.8 Encephalocele of other sites
Q01.9 Encephalocele, unspecified
Q02 Microcephaly

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.