2023 ICD-10-CM Diagnosis Code Q01

Encephalocele

    2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
  • Q01 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2023 edition of ICD-10-CM Q01 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of Q01 - other international versions of ICD-10 Q01 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q01. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Meckel-Gruber syndrome (
    ICD-10-CM Diagnosis Code Q61.9

    Cystic kidney disease, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    • Meckel-Gruber syndrome
    Q61.9
    )
Includes
Includes Help
"Includes" further defines, or give examples of, the content of the code or category.
  • Arnold-Chiari syndrome, type III
  • encephalocystocele
  • encephalomyelocele
  • hydroencephalocele
  • hydromeningocele, cranial
  • meningocele, cerebral
  • meningoencephalocele
The following code(s) above Q01 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q01:
  • Q00-Q99
    2023 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
Clinical Information
  • A congenital neural tube closure defect resulting in the protrusion of the brain through a skull opening. When the protrusion includes the meninges, the term encephalomeningocele is used.
  • Brain tissue herniation through a congenital or acquired defect in the skull. The majority of congenital encephaloceles occur in the occipital or frontal regions. Clinical features include a protuberant mass that may be pulsatile. The quantity and location of protruding neural tissue determines the type and degree of neurologic deficit. Visual defects, psychomotor developmental delay, and persistent motor deficits frequently occur.
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change
Code annotations containing back-references to Q01:
  • Type 1 Excludes: Q07.0
    , Q75
    ICD-10-CM Diagnosis Code Q07.0

    Arnold-Chiari syndrome

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Applicable To
    • Arnold-Chiari syndrome, type II
    Type 1 Excludes
    • Arnold-Chiari syndrome, type III (Q01.-)
    • Arnold-Chiari syndrome, type IV (Q04.8)
    ICD-10-CM Diagnosis Code Q75

    Other congenital malformations of skull and face bones

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • congenital malformation of face NOS (Q18.-)
    • congenital malformation syndromes classified to Q87.-
    • dentofacial anomalies [including malocclusion] (M26.-)
    • musculoskeletal deformities of head and face (Q67.0-Q67.4)
    • skull defects associated with congenital anomalies of brain such as:
    • anencephaly (Q00.0)
    • encephalocele (Q01.-)
    • hydrocephalus (Q03.-)
    • microcephaly (Q02)
ICD-10-CM Codes Adjacent To Q01
P96.8 Other specified conditions originating in the perinatal period
P96.81 Exposure to (parental) (environmental) tobacco smoke in the perinatal period
P96.82 Delayed separation of umbilical cord
P96.83 Meconium staining
P96.89 Other specified conditions originating in the perinatal period
P96.9 Condition originating in the perinatal period, unspecified
Q00 Anencephaly and similar malformations
Q00.0 Anencephaly
Q00.1 Craniorachischisis
Q00.2 Iniencephaly
Q01 Encephalocele
Q01.0 Frontal encephalocele
Q01.1 Nasofrontal encephalocele
Q01.2 Occipital encephalocele
Q01.8 Encephalocele of other sites
Q01.9 Encephalocele, unspecified
Q02 Microcephaly
Q03 Congenital hydrocephalus
Q03.0 Malformations of aqueduct of Sylvius
Q03.1 Atresia of foramina of Magendie and Luschka
Q03.8 Other congenital hydrocephalus

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.