ICD-10-CM Codes
Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities
Q00-Q07 Congenital malformations of the nervous system
Q02- Microcephaly
2022 ICD-10-CM Diagnosis Code Q02

2022 ICD-10-CM Diagnosis Code Q02

Microcephaly

2016

2017

2018

2019

2020

2021

2022

Billable/Specific Code

POA Exempt

Q02 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2022 edition of ICD-10-CM Q02 became effective on October 1, 2021.
This is the American ICD-10-CM version of Q02 - other international versions of ICD-10 Q02 may differ.

Code First

Code First Help

Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.

, if applicable, congenital Zika virus disease

Type 1 Excludes

Type 1 Excludes Help

A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q02. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

Meckel-Gruber syndrome (
ICD-10-CM Diagnosis Code Q61.9
Cystic kidney disease, unspecified
Applicable To
- Meckel-Gruber syndrome
Q61.9
)

Includes

Includes Help

"Includes" further defines, or give examples of, the content of the code or category.

hydromicrocephaly
micrencephalon

The following code(s) above Q02 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to Q02:

Q00-Q99
2022 ICD-10-CM Range Q00-Q99
Congenital malformations, deformations and chromosomal abnormalities
Note
- Codes from this chapter are not for use on maternal records
Type 2 Excludes
- inborn errors of metabolism (E70-E88)
Congenital malformations, deformations and chromosomal abnormalities

Approximate Synonyms

Congenital brain hypoplasia
Congenital hypoplasia of brain
Hydromicrocephaly
Microcephalus
Primary microcephaly

Clinical Information

A congenital abnormality in which the cerebrum is underdeveloped, the fontanels close prematurely, and, as a result, the head is small. (desk reference for neuroscience, 2nd ed.)
A congenital or acquired developmental disorder in which the circumference of the head is smaller than normal for the person's age and sex. It is the result of brain developmental delay.
Abnormal smallness of the brain.
Smallness of the head produced by incomplete development of the brain, often associated with below normal mental and cognitive development.

Present On Admission

POA Help

"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.

Q02 is considered exempt from POA reporting.

ICD-10-CM Q02 is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):

091 Other disorders of nervous system with mcc
092 Other disorders of nervous system with cc
093 Other disorders of nervous system without cc/mcc
791 Prematurity with major problems
793 Full term neonate with major problems

Convert Q02 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change
2022 (effective 10/1/2021): No change

Code annotations containing back-references to Q02:

Type 1 Excludes: Q75

ICD-10-CM Diagnosis Code Q75
Other congenital malformations of skull and face bones
Type 1 Excludes
- congenital malformation of face NOS (Q18.-)
- congenital malformation syndromes classified to Q87.-
- dentofacial anomalies [including malocclusion] (M26.-)
- musculoskeletal deformities of head and face (Q67.0-Q67.4)
- skull defects associated with congenital anomalies of brain such as:
- anencephaly (Q00.0)
- encephalocele (Q01.-)
- hydrocephalus (Q03.-)
- microcephaly (Q02)

Diagnosis Index entries containing back-references to Q02:

Absence (of) (organ or part) (complete or partial)
- skull bone (congenital) Q75.8
  ICD-10-CM Diagnosis Code Q75.8
  Other specified congenital malformations of skull and face bones
  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code POA Exempt
  Applicable To
  Absence of skull bone, congenital
  Congenital deformity of forehead
  Platybasia
  - with
    - microcephaly Q02
Agenesis
- skull (bone) Q75.8
  ICD-10-CM Diagnosis Code Q75.8
  Other specified congenital malformations of skull and face bones
  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code POA Exempt
  Applicable To
  Absence of skull bone, congenital
  Congenital deformity of forehead
  Platybasia
  - with
    - microcephaly Q02
Anomaly, anomalous (congenital) (unspecified type) Q89.9
ICD-10-CM Diagnosis Code Q89.9
Congenital malformation, unspecified
Applicable To
Congenital anomaly NOS
Congenital deformity NOS
- bone Q79.9
  ICD-10-CM Diagnosis Code Q79.9
  Congenital malformation of musculoskeletal system, unspecified
  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of musculoskeletal system NOS
  Congenital deformity of musculoskeletal system NOS
  - skull Q75.9
    ICD-10-CM Diagnosis Code Q75.9
    Congenital malformation of skull and face bones, unspecified
    2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly of face bones NOS
    Congenital anomaly of skull NOS
    - with
      - microcephaly Q02
- skull Q75.9
  ICD-10-CM Diagnosis Code Q75.9
  Congenital malformation of skull and face bones, unspecified
  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of face bones NOS
  Congenital anomaly of skull NOS
  - with
    - microcephaly Q02
Deformity Q89.9
ICD-10-CM Diagnosis Code Q89.9
Congenital malformation, unspecified
Applicable To
Congenital anomaly NOS
Congenital deformity NOS
- skull (acquired) M95.2
  ICD-10-CM Diagnosis Code M95.2
  Other acquired deformity of head
  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
  - congenital Q75.8
    ICD-10-CM Diagnosis Code Q75.8
    Other specified congenital malformations of skull and face bones
    2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code POA Exempt
    Applicable To
    Absence of skull bone, congenital
    Congenital deformity of forehead
    Platybasia
    - with
      - microcephaly Q02
Distortion(s) (congenital)
- skull bone(s) Q75.8
  ICD-10-CM Diagnosis Code Q75.8
  Other specified congenital malformations of skull and face bones
  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code POA Exempt
  Applicable To
  Absence of skull bone, congenital
  Congenital deformity of forehead
  Platybasia
  - with
    - microcephaly Q02
Hydromicrocephaly Q02
Hypoplasia, hypoplastic
- brain Q02
- skull (bone) Q75.8
  ICD-10-CM Diagnosis Code Q75.8
  Other specified congenital malformations of skull and face bones
  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code POA Exempt
  Applicable To
  Absence of skull bone, congenital
  Congenital deformity of forehead
  Platybasia
  - with
    - microcephaly Q02
- cephalic Q02
Idiot, idiocy (congenital) F73
ICD-10-CM Diagnosis Code F73
Profound intellectual disabilities
Applicable To
IQ level below 20-25
Profound mental subnormality
- microcephalic Q02
Imperfect
- closure (congenital)
  - skull Q75.0
    ICD-10-CM Diagnosis Code Q75.0
    Craniosynostosis
    2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code POA Exempt
    Applicable To
    Acrocephaly
    Imperfect fusion of skull
    Oxycephaly
    Trigonocephaly
    - with
      - microcephaly Q02
Micrencephalon, micrencephaly Q02
Microcephalus, microcephalic, microcephaly Q02
Microencephalon Q02
Nondevelopment
- brain Q02
Oligoencephalon Q02
Undeveloped, undevelopment - see also Hypoplasia
- brain Q02 (congenital)
- cerebral Q02 (congenital)

ICD-10-CM Codes Adjacent To Q02

Q00 Anencephaly and similar malformations

Q00.0 Anencephaly

Q00.1 Craniorachischisis

Q00.2 Iniencephaly

Q01 Encephalocele

Q01.0 Frontal encephalocele

Q01.1 Nasofrontal encephalocele

Q01.2 Occipital encephalocele

Q01.8 Encephalocele of other sites

Q01.9 Encephalocele, unspecified

Q02 Microcephaly

Q03 Congenital hydrocephalus

Q03.0 Malformations of aqueduct of Sylvius

Q03.1 Atresia of foramina of Magendie and Luschka

Q03.8 Other congenital hydrocephalus

Q03.9 Congenital hydrocephalus, unspecified

Q04 Other congenital malformations of brain

Q04.0 Congenital malformations of corpus callosum

Q04.1 Arhinencephaly

Q04.2 Holoprosencephaly

Q04.3 Other reduction deformities of brain

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2022 ICD-10-CM Diagnosis Code Q02

Microcephaly

Cystic kidney disease, unspecified

Congenital malformations, deformations and chromosomal abnormalities

Other congenital malformations of skull and face bones

Other specified congenital malformations of skull and face bones

Other specified congenital malformations of skull and face bones

Congenital malformation, unspecified

Congenital malformation of musculoskeletal system, unspecified

Congenital malformation of skull and face bones, unspecified

Congenital malformation of skull and face bones, unspecified

Congenital malformation, unspecified

Other acquired deformity of head

Other specified congenital malformations of skull and face bones

Other specified congenital malformations of skull and face bones

Other specified congenital malformations of skull and face bones

Profound intellectual disabilities

Craniosynostosis