2020 ICD-10-CM Diagnosis Code Q04

Other congenital malformations of brain

    2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
  • Q04 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2020 edition of ICD-10-CM Q04 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of Q04 - other international versions of ICD-10 Q04 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q04. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • cyclopia (
    ICD-10-CM Diagnosis Code Q87.0

    Congenital malformation syndromes predominantly affecting facial appearance

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Acrocephalopolysyndactyly
    • Acrocephalosyndactyly [Apert]
    • Cryptophthalmos syndrome
    • Cyclopia
    • Goldenhar syndrome
    • Moebius syndrome
    • Oro-facial-digital syndrome
    • Robin syndrome
    • Whistling face
    Q87.0
    )
  • macrocephaly (
    ICD-10-CM Diagnosis Code Q75.3

    Macrocephaly

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Q75.3
    )
The following code(s) above Q04 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q04:
  • Q00-Q99
    2020 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
ICD-10-CM Codes Adjacent To Q04
Q01.1 Nasofrontal encephalocele
Q01.2 Occipital encephalocele
Q01.8 Encephalocele of other sites
Q01.9 Encephalocele, unspecified
Q02 Microcephaly
Q03 Congenital hydrocephalus
Q03.0 Malformations of aqueduct of Sylvius
Q03.1 Atresia of foramina of Magendie and Luschka
Q03.8 Other congenital hydrocephalus
Q03.9 Congenital hydrocephalus, unspecified
Q04 Other congenital malformations of brain
Q04.0 Congenital malformations of corpus callosum
Q04.1 Arhinencephaly
Q04.2 Holoprosencephaly
Q04.3 Other reduction deformities of brain
Q04.4 Septo-optic dysplasia of brain
Q04.5 Megalencephaly
Q04.6 Congenital cerebral cysts
Q04.8 Other specified congenital malformations of brain
Q04.9 Congenital malformation of brain, unspecified
Q05 Spina bifida

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.