1. ICD-10-CM Codes
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2. Q00-Q99
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3. Q00-Q07
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4. Q04-
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5. 2023 ICD-10-CM Diagnosis Code Q04.3

2023 ICD-10-CM Diagnosis Code Q04.3

Other reduction deformities of brain

2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

• Q04.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
• The 2023 edition of ICD-10-CM Q04.3 became effective on October 1, 2022.
• This is the American ICD-10-CM version of Q04.3 - other international versions of ICD-10 Q04.3 may differ.

• Congenital hypoplasia of part of brain
• Hydranencephaly
• Hypoplasia of part of brain, congenital
• Joubert syndrome
• Lissencephaly
• Microgyria
• Reduction deformities of brain
• Reduction deformity of brain, congenital

• A "smooth brain" malformation of the cerebral cortex resulting from abnormal location of developing neurons during corticogenesis. It is characterized by an absence of normal convoluted indentations on the surface of the brain (agyria), or fewer and shallower indentations (pachygryia). There is a reduced number of cortical layers, typically 4 instead of 6, resulting in a thickened cortex, and reduced cerebral white matter that is a reversal of the normal ratio of cerebral white matter to cortex.
• A congenital abnormality characterized by the presence of abnormally small convolutions in the brain. It results in mental retardation.
• A congenital condition where the greater portions of the cerebral hemispheres and corpus striatum are replaced by csf and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (menkes, textbook of child neurology, 5th ed, p307)
• A rare congenital brain disorder in which the cerebral hemispheres are absent and replaced by sacs that contain cerebrospinal fluid. Signs and symptoms include irritability, increased muscle tone, seizures, and hydrocephalus. The prognosis is poor.

• Q04.3 is considered exempt from POA reporting.

• 091 Other disorders of nervous system with mcc
• 092 Other disorders of nervous system with cc
• 093 Other disorders of nervous system without cc/mcc
• 791 Prematurity with major problems
• 793 Full term neonate with major problems

Convert Q04.3 to ICD-9-CM

• 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
• 2017 (effective 10/1/2016): No change
• 2018 (effective 10/1/2017): No change
• 2019 (effective 10/1/2018): No change
• 2020 (effective 10/1/2019): No change
• 2021 (effective 10/1/2020): No change
• 2022 (effective 10/1/2021): No change
• 2023 (effective 10/1/2022): No change

• Absence (of) (organ or part) (complete or partial)
  • brain Q00.0
    ICD-10-CM Diagnosis Code Q00.0

    Anencephaly

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Acephaly
    • Acrania
    • Amyelencephaly
    • Hemianencephaly
    • Hemicephaly
    • part of Q04.3
  • cerebellum Q04.3 (vermis)
• Agenesis
  • brain Q00.0
    ICD-10-CM Diagnosis Code Q00.0

    Anencephaly

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Acephaly
    • Acrania
    • Amyelencephaly
    • Hemianencephaly
    • Hemicephaly
    • part of Q04.3
  • cerebellum Q04.3
  • vermis of cerebellum Q04.3
• Agyria Q04.3
• Aplasia - see also Agenesis
  • brain Q00.0
    ICD-10-CM Diagnosis Code Q00.0

    Anencephaly

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Acephaly
    • Acrania
    • Amyelencephaly
    • Hemianencephaly
    • Hemicephaly
    • part of Q04.3
  • cerebellum Q04.3
• Deformity Q89.9
  ICD-10-CM Diagnosis Code Q89.9

  Congenital malformation, unspecified

  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

  Applicable To

  • Congenital anomaly NOS
  • Congenital deformity NOS
  • brain (congenital) Q04.9
    ICD-10-CM Diagnosis Code Q04.9

    Congenital malformation of brain, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital anomaly NOS of brain
    • Congenital deformity NOS of brain
    • Congenital disease or lesion NOS of brain
    • Multiple anomalies NOS of brain, congenital
    • reduction Q04.3
  • reduction (extremity) (limb) Q73.8
    - see also condition and site
    ICD-10-CM Diagnosis Code Q73.8

    Other reduction defects of unspecified limb(s)

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Longitudinal reduction deformity of unspecified limb(s)
    • Ectromelia of limb NOS
    • Hemimelia of limb NOS
    • Reduction defect of limb NOS
    • brain Q04.3
• Hydrancephaly, hydranencephaly Q04.3
• Hypoplasia, hypoplastic
  • brain Q02
    ICD-10-CM Diagnosis Code Q02

    Microcephaly

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Code First

    • , if applicable, congenital Zika virus disease

    Includes

    • hydromicrocephaly
    • micrencephalon

    Type 1 Excludes

    • Meckel-Gruber syndrome (Q61.9)
    • gyri Q04.3
    • part of Q04.3
  • cerebellum Q04.3
• Lissencephalia, lissencephaly Q04.3
• Microgyria Q04.3 (congenital)
• Nondevelopment
  • brain Q02
    ICD-10-CM Diagnosis Code Q02

    Microcephaly

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Code First

    • , if applicable, congenital Zika virus disease

    Includes

    • hydromicrocephaly
    • micrencephalon

    Type 1 Excludes

    • Meckel-Gruber syndrome (Q61.9)
    • part of Q04.3
• Pachygyria Q04.3

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.