2020 ICD-10-CM Diagnosis Code Q04.3

Other reduction deformities of brain

    2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
  • Q04.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM Q04.3 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of Q04.3 - other international versions of ICD-10 Q04.3 may differ.
Applicable To
  • Absence of part of brain
  • Agenesis of part of brain
  • Agyria
  • Aplasia of part of brain
  • Hydranencephaly
  • Hypoplasia of part of brain
  • Lissencephaly
  • Microgyria
  • Pachygyria
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q04.3. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • congenital malformations of corpus callosum (
    ICD-10-CM Diagnosis Code Q04.0

    Congenital malformations of corpus callosum

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Agenesis of corpus callosum
    Q04.0
    )
The following code(s) above Q04.3 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q04.3:
  • Q00-Q99
    2020 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q04
    ICD-10-CM Diagnosis Code Q04

    Other congenital malformations of brain

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Other congenital malformations of brain
Approximate Synonyms
  • Congenital hypoplasia of part of brain
  • Hydranencephaly
  • Hypoplasia of part of brain, congenital
  • Joubert syndrome
  • Lissencephaly
  • Microgyria
  • Reduction deformities of brain
  • Reduction deformity of brain, congenital
Clinical Information
  • A "smooth brain" malformation of the cerebral cortex resulting from abnormal location of developing neurons during corticogenesis. It is characterized by an absence of normal convoluted indentations on the surface of the brain (agyria), or fewer and shallower indentations (pachygryia). There is a reduced number of cortical layers, typically 4 instead of 6, resulting in a thickened cortex, and reduced cerebral white matter that is a reversal of the normal ratio of cerebral white matter to cortex.
  • A congenital abnormality characterized by the presence of abnormally small convolutions in the brain. It results in mental retardation.
  • A congenital condition where the greater portions of the cerebral hemispheres and corpus striatum are replaced by csf and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (menkes, textbook of child neurology, 5th ed, p307)
  • A rare congenital brain disorder in which the cerebral hemispheres are absent and replaced by sacs that contain cerebrospinal fluid. Signs and symptoms include irritability, increased muscle tone, seizures, and hydrocephalus. The prognosis is poor.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q04.3 is considered exempt from POA reporting.
ICD-10-CM Q04.3 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 091 Other disorders of nervous system with mcc
  • 092 Other disorders of nervous system with cc
  • 093 Other disorders of nervous system without cc/mcc
  • 791 Prematurity with major problems
  • 793 Full term neonate with major problems

Convert Q04.3 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to Q04.3:
  • Absence (of) (organ or part) (complete or partial)
    • brain Q00.0
      ICD-10-CM Diagnosis Code Q00.0

      Anencephaly

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Acephaly
      • Acrania
      • Amyelencephaly
      • Hemianencephaly
      • Hemicephaly
      • part of Q04.3
    • cerebellum Q04.3 (vermis)
  • Agenesis
    • brain Q00.0
      ICD-10-CM Diagnosis Code Q00.0

      Anencephaly

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Acephaly
      • Acrania
      • Amyelencephaly
      • Hemianencephaly
      • Hemicephaly
      • part of Q04.3
    • cerebellum Q04.3
    • vermis of cerebellum Q04.3
  • Agyria Q04.3
  • Aplasia - see also Agenesis
    • brain Q00.0
      ICD-10-CM Diagnosis Code Q00.0

      Anencephaly

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Acephaly
      • Acrania
      • Amyelencephaly
      • Hemianencephaly
      • Hemicephaly
      • part of Q04.3
    • cerebellum Q04.3
  • Deformity Q89.9
    ICD-10-CM Diagnosis Code Q89.9

    Congenital malformation, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital anomaly NOS
    • Congenital deformity NOS
    • brain (congenital) Q04.9
      ICD-10-CM Diagnosis Code Q04.9

      Congenital malformation of brain, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly NOS of brain
      • Congenital deformity NOS of brain
      • Congenital disease or lesion NOS of brain
      • Multiple anomalies NOS of brain, congenital
      • reduction Q04.3
    • reduction (extremity) (limb) Q73.8
      - see also condition and site
      ICD-10-CM Diagnosis Code Q73.8

      Other reduction defects of unspecified limb(s)

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Longitudinal reduction deformity of unspecified limb(s)
      • Ectromelia of limb NOS
      • Hemimelia of limb NOS
      • Reduction defect of limb NOS
      • brain Q04.3
  • Hydrancephaly, hydranencephaly Q04.3
  • Hypoplasia, hypoplastic
    • brain Q02
      ICD-10-CM Diagnosis Code Q02

      Microcephaly

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Code First
      • , if applicable, congenital Zika virus disease
      Includes
      • hydromicrocephaly
      • micrencephalon
      Type 1 Excludes
      • Meckel-Gruber syndrome (Q61.9)
      • gyri Q04.3
      • part of Q04.3
    • cerebellum Q04.3
  • Lissencephalia, lissencephaly Q04.3
  • Microgyria Q04.3 (congenital)
  • Nondevelopment
    • brain Q02
      ICD-10-CM Diagnosis Code Q02

      Microcephaly

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Code First
      • , if applicable, congenital Zika virus disease
      Includes
      • hydromicrocephaly
      • micrencephalon
      Type 1 Excludes
      • Meckel-Gruber syndrome (Q61.9)
      • part of Q04.3
  • Pachygyria Q04.3

ICD-10-CM Codes Adjacent To Q04.3
Q02 Microcephaly
Q03 Congenital hydrocephalus
Q03.0 Malformations of aqueduct of Sylvius
Q03.1 Atresia of foramina of Magendie and Luschka
Q03.8 Other congenital hydrocephalus
Q03.9 Congenital hydrocephalus, unspecified
Q04 Other congenital malformations of brain
Q04.0 Congenital malformations of corpus callosum
Q04.1 Arhinencephaly
Q04.2 Holoprosencephaly
Q04.3 Other reduction deformities of brain
Q04.4 Septo-optic dysplasia of brain
Q04.5 Megalencephaly
Q04.6 Congenital cerebral cysts
Q04.8 Other specified congenital malformations of brain
Q04.9 Congenital malformation of brain, unspecified
Q05 Spina bifida
Q05.0 Cervical spina bifida with hydrocephalus
Q05.1 Thoracic spina bifida with hydrocephalus
Q05.2 Lumbar spina bifida with hydrocephalus
Q05.3 Sacral spina bifida with hydrocephalus

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.