2021 ICD-10-CM Diagnosis Code Q04.6

Congenital cerebral cysts

    2016 2017 2018 2019 2020 2021 Billable/Specific Code POA Exempt
  • Q04.6 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2021 edition of ICD-10-CM Q04.6 became effective on October 1, 2020.
  • This is the American ICD-10-CM version of Q04.6 - other international versions of ICD-10 Q04.6 may differ.
Applicable To
  • Porencephaly
  • Schizencephaly
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q04.6. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • acquired porencephalic cyst (
    ICD-10-CM Diagnosis Code G93.0

    Cerebral cysts

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Arachnoid cyst
    • Porencephalic cyst, acquired
    Type 1 Excludes
    • acquired periventricular cysts of newborn (P91.1)
    • congenital cerebral cysts (Q04.6)
    G93.0
    )
The following code(s) above Q04.6 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q04.6:
  • Q00-Q99
    2021 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q04
    ICD-10-CM Diagnosis Code Q04

    Other congenital malformations of brain

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Other congenital malformations of brain
Approximate Synonyms
  • Cerebral cysts, congenital
  • Colloid cyst of third ventricle
  • Colloid cyst third ventricle of brain, congenital
  • Congenital choroid plexus cyst
  • Congenital porencephalic cyst
  • Congenital porencephaly
  • Congenital pseudoporencephaly
  • Multiple congenital cerebral cysts
  • Porencephaly, congenital
  • Pseudoporencephaly, congenital
  • Schizencephaly
Clinical Information
  • A rare developmental abnormality characterized by the presence of clefs in the cerebral hemispheres. The abnormality may involve one or both cerebral hemispheres. Signs and symptoms include developmental delays, mental retardation, paralysis, presence of a small head, and seizures.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q04.6 is considered exempt from POA reporting.
ICD-10-CM Q04.6 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
  • 091 Other disorders of nervous system with mcc
  • 092 Other disorders of nervous system with cc
  • 093 Other disorders of nervous system without cc/mcc
  • 791 Prematurity with major problems
  • 793 Full term neonate with major problems

Convert Q04.6 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
Code annotations containing back-references to Q04.6:
  • Type 1 Excludes: G93.0
    ICD-10-CM Diagnosis Code G93.0

    Cerebral cysts

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Arachnoid cyst
    • Porencephalic cyst, acquired
    Type 1 Excludes
    • acquired periventricular cysts of newborn (P91.1)
    • congenital cerebral cysts (Q04.6)

Diagnosis Index entries containing back-references to Q04.6:
  • Cyst (colloid) (mucous) (simple) (retention)
    • arachnoid, brain (acquired) G93.0
      ICD-10-CM Diagnosis Code G93.0

      Cerebral cysts

        2016 2017 2018 2019 2020 2021 Billable/Specific Code
      Applicable To
      • Arachnoid cyst
      • Porencephalic cyst, acquired
      Type 1 Excludes
      • acquired periventricular cysts of newborn (P91.1)
      • congenital cerebral cysts (Q04.6)
      • congenital Q04.6
    • brain (acquired) G93.0
      ICD-10-CM Diagnosis Code G93.0

      Cerebral cysts

        2016 2017 2018 2019 2020 2021 Billable/Specific Code
      Applicable To
      • Arachnoid cyst
      • Porencephalic cyst, acquired
      Type 1 Excludes
      • acquired periventricular cysts of newborn (P91.1)
      • congenital cerebral cysts (Q04.6)
      • congenital Q04.6
      • third ventricle Q04.6 (colloid)
    • choroid plexus G93.0
      ICD-10-CM Diagnosis Code G93.0

      Cerebral cysts

        2016 2017 2018 2019 2020 2021 Billable/Specific Code
      Applicable To
      • Arachnoid cyst
      • Porencephalic cyst, acquired
      Type 1 Excludes
      • acquired periventricular cysts of newborn (P91.1)
      • congenital cerebral cysts (Q04.6)
      • congenital Q04.6
    • porencephalic Q04.6
    • paraphysis, cerebri, congenital Q04.6
  • Degeneration, degenerative
    • brain (cortical) (progressive) G31.9
      ICD-10-CM Diagnosis Code G31.9

      Degenerative disease of nervous system, unspecified

        2016 2017 2018 2019 2020 2021 Billable/Specific Code
      • cystic G31.89
        ICD-10-CM Diagnosis Code G31.89

        Other specified degenerative diseases of nervous system

          2016 2017 2018 2019 2020 2021 Billable/Specific Code
        • congenital Q04.6
  • Porencephaly (congenital) (developmental) (true) Q04.6
  • Schizencephaly Q04.6

ICD-10-CM Codes Adjacent To Q04.6
Q03.1 Atresia of foramina of Magendie and Luschka
Q03.8 Other congenital hydrocephalus
Q03.9 Congenital hydrocephalus, unspecified
Q04 Other congenital malformations of brain
Q04.0 Congenital malformations of corpus callosum
Q04.1 Arhinencephaly
Q04.2 Holoprosencephaly
Q04.3 Other reduction deformities of brain
Q04.4 Septo-optic dysplasia of brain
Q04.5 Megalencephaly
Q04.6 Congenital cerebral cysts
Q04.8 Other specified congenital malformations of brain
Q04.9 Congenital malformation of brain, unspecified
Q05 Spina bifida
Q05.0 Cervical spina bifida with hydrocephalus
Q05.1 Thoracic spina bifida with hydrocephalus
Q05.2 Lumbar spina bifida with hydrocephalus
Q05.3 Sacral spina bifida with hydrocephalus
Q05.4 Unspecified spina bifida with hydrocephalus
Q05.5 Cervical spina bifida without hydrocephalus
Q05.6 Thoracic spina bifida without hydrocephalus

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.