Congenital malformations, deformations and chromosomal abnormalities
Congenital malformations of the nervous system
Spina bifida Q05- >
Use Additional Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q05. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
"Includes" further defines, or give examples of, the content of the code or category.
- hydromeningocele (spinal)
- meningocele (spinal)
- spina bifida (aperta)(cystica)
- Birth defect involving inadequate closure of the bony casement of the spinal cord, through which the spinal membranes, with or without spinal cord tissue, may protrude.
- Congenital defects of closure of one or more vertebral arches, which may be associated with malformations of the spinal cord, nerve roots, congenital fibrous bands, lipomas, and congenital cysts. These malformations range from mild (e.g., spina bifida occulta) to severe, including rachischisis where there is complete failure of neural tube and spinal cord fusion, resulting in exposure of the spinal cord at the surface. Spinal dysraphism includes all forms of spina bifida. The open form is called spina bifida cystica and the closed form is spina bifida occulta. (from Joynt, Clinical Neurology, 1992, ch55, p34)
- Congenital, or rarely acquired, herniation of meningeal and spinal cord tissue through a bony defect in the vertebral column. The majority of these defects occur in the lumbosacral region. Clinical features include paraplegia, loss of sensation in the lower body, and incontinence. This condition may be associated with the arnold-chiari malformation and hydrocephalus. (from Joynt, Clinical Neurology, 1992, ch55, pp35-6)
- Developmental anomaly characterized by defective closure of the bony encasement of the spinal cord, through which the cord and meninges may protrude.
- Hernial protrusion of the spinal cord and its meninges through a defect in the vertebral canal.
- Herniation of spinal cord tissue and meninges through a defect in a region of the vertebral column.
- Spina bifida is the most common disabling birth defect in the United States. It is a type of neural tube defect, which is a problem with the spinal cord or its coverings. It happens if the fetal spinal column doesn't close completely during the first month of pregnancy. There is usually nerve damage that causes at least some paralysis of the legs. Many people with spina bifida will need assistive devices such as braces, crutches or wheelchairs. They may have learning difficulties, urinary and bowel problems or hydrocephalus, a buildup of fluid in the brain. There is no cure. Treatments focus on the complications, and can include surgery, medicine and physiotherapy. Taking folic acid can reduce the risk of having a baby with spina bifida. It's in most multivitamins. Women who could become pregnant should take it daily.
- Q05 Spina bifida
- Q05.0 Cervical spina bifida with hydrocephalus
- Q05.1 Thoracic spina bifida with hydrocephalus
- Q05.2 Lumbar spina bifida with hydrocephalus
- Q05.3 Sacral spina bifida with hydrocephalus
- Q05.4 Unspecified spina bifida with hydrocephalus
- Q05.5 Cervical spina bifida without hydrocephalus
- Q05.6 Thoracic spina bifida without hydrocephalus
- Q05.7 Lumbar spina bifida without hydrocephalus
- Q05.8 Sacral spina bifida without hydrocephalus
- Q05.9 Spina bifida, unspecified