2020 ICD-10-CM Diagnosis Code Q07.0

Arnold-Chiari syndrome

    2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
  • Q07.0 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2020 edition of ICD-10-CM Q07.0 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of Q07.0 - other international versions of ICD-10 Q07.0 may differ.
Applicable To
  • Arnold-Chiari syndrome, type II
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q07.0. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Arnold-Chiari syndrome, type III (
    ICD-10-CM Diagnosis Code Q01
    • Q01 Encephalocele
      • Q01.0 Frontal encephalocele
      • Q01.1 Nasofrontal encephalocele
      • Q01.2 Occipital encephalocele
      • Q01.8 Encephalocele of other sites
      • Q01.9 Encephalocele, unspecified
    Q01.-
    )
  • Arnold-Chiari syndrome, type IV (
    ICD-10-CM Diagnosis Code Q04.8

    Other specified congenital malformations of brain

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Arnold-Chiari syndrome, type IV
    • Macrogyria
    Q04.8
    )
The following code(s) above Q07.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q07.0:
  • Q00-Q99
    2020 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q07
    ICD-10-CM Diagnosis Code Q07

    Other congenital malformations of nervous system

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • congenital central alveolar hypoventilation syndrome (G47.35)
    • familial dysautonomia [Riley-Day] (G90.1)
    • neurofibromatosis (nonmalignant) (Q85.0-)
    Other congenital malformations of nervous system
Clinical Information
  • A group of congenital malformations involving the brainstem, cerebellum, upper spinal cord, and surrounding bony structures. Type ii is the most common, and features compression of the medulla and cerebellar tonsils into the upper cervical spinal canal and an associated meningomyelocele. Type i features similar, but less severe malformations and is without an associated meningomyelocele. Type iii has the features of type ii with an additional herniation of the entire cerebellum through the bony defect involving the foramen magnum, forming an encephalocele. Type iv is a form a cerebellar hypoplasia. Clinical manifestations of types i-iii include torticollis; opisthotonus; headache; vertigo; vocal cord paralysis; apnea; nystagmus, congenital; swallowing difficulties; and ataxia. (from menkes, textbook of child neurology, 5th ed, p261; davis, textbook of neuropathology, 2nd ed, pp236-46)
  • A rare genetic brain malformation characterized by displacement of the brain stem and cerebellum through the foramen magnum. It may result in hydrocephalus.
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to Q07.0:
  • Type 1 Excludes: Q03
    , Q05
    ICD-10-CM Diagnosis Code Q03

    Congenital hydrocephalus

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Includes
    • hydrocephalus in newborn
    Type 1 Excludes
    • Arnold-Chiari syndrome, type II (Q07.0-)
    • acquired hydrocephalus (G91.-)
    • hydrocephalus due to congenital toxoplasmosis (P37.1)
    • hydrocephalus with spina bifida (Q05.0-Q05.4)
    ICD-10-CM Diagnosis Code Q05

    Spina bifida

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Includes
    • hydromeningocele (spinal)
    • meningocele (spinal)
    • meningomyelocele
    • myelocele
    • myelomeningocele
    • rachischisis
    • spina bifida (aperta)(cystica)
    • syringomyelocele
    Type 1 Excludes
    • Arnold-Chiari syndrome, type II (Q07.0-)
    • spina bifida occulta (Q76.0)
    Use Additional
    • code for any associated paraplegia (paraparesis) (G82.2-)
ICD-10-CM Codes Adjacent To Q07.0
Q05.9 Spina bifida, unspecified
Q06 Other congenital malformations of spinal cord
Q06.0 Amyelia
Q06.1 Hypoplasia and dysplasia of spinal cord
Q06.2 Diastematomyelia
Q06.3 Other congenital cauda equina malformations
Q06.4 Hydromyelia
Q06.8 Other specified congenital malformations of spinal cord
Q06.9 Congenital malformation of spinal cord, unspecified
Q07 Other congenital malformations of nervous system
Q07.0 Arnold-Chiari syndrome
Q07.00 …… without spina bifida or hydrocephalus
Q07.01 …… with spina bifida
Q07.02 …… with hydrocephalus
Q07.03 …… with spina bifida and hydrocephalus
Q07.8 Other specified congenital malformations of nervous system
Q07.9 Congenital malformation of nervous system, unspecified
Q10 Congenital malformations of eyelid, lacrimal apparatus and orbit
Q10.0 Congenital ptosis
Q10.1 Congenital ectropion
Q10.2 Congenital entropion

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.