2023 ICD-10-CM Diagnosis Code Q13.81

Rieger's anomaly

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • Q13.81 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2023 edition of ICD-10-CM Q13.81 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of Q13.81 - other international versions of ICD-10 Q13.81 may differ.
Use Additional
Use Additional Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • code for associated glaucoma (
    ICD-10-CM Diagnosis Code H42

    Glaucoma in diseases classified elsewhere

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Manifestation Code
    Code First
    Type 1 Excludes
    • glaucoma (in) onchocerciasis (B73.02)
    • glaucoma (in) syphilis (A52.71)
    • glaucoma (in) tuberculous (A18.59)
    H42
    )
The following code(s) above Q13.81 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q13.81:
  • Q00-Q99
    2023 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q10-Q18
    2023 ICD-10-CM Range Q10-Q18

    Congenital malformations of eye, ear, face and neck

    Type 2 Excludes
    • cleft lip and cleft palate (Q35-Q37)
    • congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4)
    • congenital malformation of larynx (Q31.-)
    • congenital malformation of lip NEC (Q38.0)
    • congenital malformation of nose (Q30.-)
    • congenital malformation of parathyroid gland (Q89.2)
    • congenital malformation of thyroid gland (Q89.2)
    Congenital malformations of eye, ear, face and neck
Approximate Synonyms
  • Reigers anomaly
  • Reigers anomaly (eye condition)
  • Rieger eye malformation sequence
Clinical Information
  • Malformations of the anterior chamber of the eye and teeth with abnormalities involving the craniofacial structures, myotonic dystrophy, umbilical anomalies, and other variable defects. Psychomotor retardation occurs in some cases.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q13.81 is considered exempt from POA reporting.
ICD-10-CM Q13.81 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):
  • 124 Other disorders of the eye with mcc
  • 125 Other disorders of the eye without mcc

Convert Q13.81 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change
Code annotations containing back-references to Q13.81:
  • Code First: H42
    ICD-10-CM Diagnosis Code H42

    Glaucoma in diseases classified elsewhere

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Manifestation Code
    Code First
    Type 1 Excludes
    • glaucoma (in) onchocerciasis (B73.02)
    • glaucoma (in) syphilis (A52.71)
    • glaucoma (in) tuberculous (A18.59)

Diagnosis Index entries containing back-references to Q13.81:
  • Anomaly, anomalous (congenital) (unspecified type) Q89.9
    ICD-10-CM Diagnosis Code Q89.9

    Congenital malformation, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital anomaly NOS
    • Congenital deformity NOS
    • Rieger's Q13.81
  • Glaucoma H40.9
    ICD-10-CM Diagnosis Code H40.9

    Unspecified glaucoma

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • in (due to)
      • Rieger's anomaly Q13.81
  • Rieger's anomaly or syndrome Q13.81

ICD-10-CM Codes Adjacent To Q13.81
Q12.8 Other congenital lens malformations
Q12.9 Congenital lens malformation, unspecified
Q13 Congenital malformations of anterior segment of eye
Q13.0 Coloboma of iris
Q13.1 Absence of iris
Q13.2 Other congenital malformations of iris
Q13.3 Congenital corneal opacity
Q13.4 Other congenital corneal malformations
Q13.5 Blue sclera
Q13.8 Other congenital malformations of anterior segment of eye
Q13.81 Rieger's anomaly
Q13.89 Other congenital malformations of anterior segment of eye
Q13.9 Congenital malformation of anterior segment of eye, unspecified
Q14 Congenital malformations of posterior segment of eye
Q14.0 Congenital malformation of vitreous humor
Q14.1 Congenital malformation of retina
Q14.2 Congenital malformation of optic disc
Q14.3 Congenital malformation of choroid
Q14.8 Other congenital malformations of posterior segment of eye
Q14.9 Congenital malformation of posterior segment of eye, unspecified
Q15 Other congenital malformations of eye

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.