2020 ICD-10-CM Diagnosis Code Q21.3

Tetralogy of Fallot

    2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
  • Q21.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM Q21.3 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of Q21.3 - other international versions of ICD-10 Q21.3 may differ.
Applicable To
  • Ventricular septal defect with pulmonary stenosis or atresia, dextroposition of aorta and hypertrophy of right ventricle.
The following code(s) above Q21.3 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q21.3:
  • Q00-Q99
    2020 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q21
    ICD-10-CM Diagnosis Code Q21

    Congenital malformations of cardiac septa

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • acquired cardiac septal defect (I51.0)
    Congenital malformations of cardiac septa
Approximate Synonyms
  • Dextraposition of aorta in fallot's tetralogy
  • Dextroposition of aorta in tetralogy of fallot
  • Tetralogy of fallot with absent pulmonary valve
  • Tetralogy of fallot with pulmonary atresia
  • Tetralogy of fallot with pulmonary stenosis
  • Tetralogy of fallot with ventricular septal defect
  • Ventricular septal defect in fallot's tetralogy
Clinical Information
  • A combination of congenital heart defects consisting of four key features including ventricular septal defects; pulmonary stenosis; right ventricular hypertrophy; and a dextro-positioned aorta. In this condition, blood from both ventricles (oxygen-rich and oxygen-poor) is pumped into the body often causing cyanosis.
  • A congenital heart disorder characterized by the presence of the following four abnormalities: ventricular septal defect, pulmonary stenosis, overriding aorta, and right ventricular hypertrophy.
  • Combination of congenital cardiac defects consisting of pulmonary stenosis, interventricular septal defect, dextroposition of the aorta so that it overrides the interventricular septum and receives venous as well as arterial blood, and right ventricular hypertrophy.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q21.3 is considered exempt from POA reporting.
ICD-10-CM Q21.3 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 306 Cardiac congenital and valvular disorders with mcc
  • 307 Cardiac congenital and valvular disorders without mcc

Convert Q21.3 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to Q21.3:
  • Anomaly, anomalous (congenital) (unspecified type) Q89.9
    ICD-10-CM Diagnosis Code Q89.9

    Congenital malformation, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital anomaly NOS
    • Congenital deformity NOS
    • heart Q24.9
      ICD-10-CM Diagnosis Code Q24.9

      Congenital malformation of heart, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of heart
      • Congenital disease of heart
      • septum Q21.9
        ICD-10-CM Diagnosis Code Q21.9

        Congenital malformation of cardiac septum, unspecified

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Septal (heart) defect NOS
        • interventricular Q21.0
          ICD-10-CM Diagnosis Code Q21.0

          Ventricular septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Roger's disease
          • with pulmonary stenosis or atresia, dextraposition of aorta and hypertrophy of right ventricle Q21.3
        • ventricular Q21.0
          ICD-10-CM Diagnosis Code Q21.0

          Ventricular septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Roger's disease
          • with pulmonary stenosis or atresia, dextraposition of aorta and hypertrophy of right ventricle Q21.3
      • tetralogy of Fallot Q21.3
  • Defect, defective Q89.9
    ICD-10-CM Diagnosis Code Q89.9

    Congenital malformation, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital anomaly NOS
    • Congenital deformity NOS
    • interventricular septal Q21.0
      ICD-10-CM Diagnosis Code Q21.0

      Ventricular septal defect

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Roger's disease
      • with dextroposition of aorta, pulmonary stenosis and hypertrophy of right ventricle Q21.3
      • in tetralogy of Fallot Q21.3
    • ventricular septal Q21.0
      ICD-10-CM Diagnosis Code Q21.0

      Ventricular septal defect

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Roger's disease
      • in tetralogy of Fallot Q21.3
  • Dextraposition, aorta Q20.3
    ICD-10-CM Diagnosis Code Q20.3

    Discordant ventriculoarterial connection

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Dextrotransposition of aorta
    • Transposition of great vessels (complete)
    • in tetralogy of Fallot Q21.3
  • Fallot's
    • tetrad or tetralogy Q21.3
  • Hypertrophy, hypertrophic
  • Imperfect
    • closure (congenital)
      • septum
        • interventricular Q21.0
          ICD-10-CM Diagnosis Code Q21.0

          Ventricular septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Roger's disease
          • in tetralogy of Fallot Q21.3
        • ventricular Q21.0
          ICD-10-CM Diagnosis Code Q21.0

          Ventricular septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Roger's disease
          • with pulmonary stenosis or atresia, dextraposition of aorta, and hypertrophy of right ventricle Q21.3
          • in tetralogy of Fallot Q21.3
  • Stenosis, stenotic (cicatricial) - see also Stricture
    • pulmonary (artery) (congenital) Q25.6
      ICD-10-CM Diagnosis Code Q25.6

      Stenosis of pulmonary artery

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Supravalvular pulmonary stenosis
      • with ventricular septal defect, transposition of aorta, and hypertrophy of right ventricle Q21.3
      • in tetralogy of Fallot Q21.3
  • Syndrome - see also Disease
    • Fallot's Q21.3
  • Tetralogy of Fallot Q21.3

ICD-10-CM Codes Adjacent To Q21.3
Q20.3 Discordant ventriculoarterial connection
Q20.4 Double inlet ventricle
Q20.5 Discordant atrioventricular connection
Q20.6 Isomerism of atrial appendages
Q20.8 Other congenital malformations of cardiac chambers and connections
Q20.9 Congenital malformation of cardiac chambers and connections, unspecified
Q21 Congenital malformations of cardiac septa
Q21.0 Ventricular septal defect
Q21.1 Atrial septal defect
Q21.2 Atrioventricular septal defect
Q21.3 Tetralogy of Fallot
Q21.4 Aortopulmonary septal defect
Q21.8 Other congenital malformations of cardiac septa
Q21.9 Congenital malformation of cardiac septum, unspecified
Q22 Congenital malformations of pulmonary and tricuspid valves
Q22.0 Pulmonary valve atresia
Q22.1 Congenital pulmonary valve stenosis
Q22.2 Congenital pulmonary valve insufficiency
Q22.3 Other congenital malformations of pulmonary valve
Q22.4 Congenital tricuspid stenosis
Q22.5 Ebstein's anomaly

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.