2020 ICD-10-CM Diagnosis Code Q23.4

Hypoplastic left heart syndrome

    2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
  • Q23.4 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM Q23.4 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of Q23.4 - other international versions of ICD-10 Q23.4 may differ.
The following code(s) above Q23.4 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q23.4:
  • Q00-Q99
    2020 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
Clinical Information
  • A condition caused by underdevelopment of the whole left half of the heart. It is characterized by hypoplasia of the left cardiac chambers (heart atrium; heart ventricle), the aorta, the aortic valve, and the mitral valve. Severe symptoms appear in early infancy when ductus arteriosus closes.
  • A rare congenital cardiovascular disorder characterized by severe underdevelopment of the left side of the heart. Signs and symptoms include tachypnea, cyanosis, dyspnea, and lethargy.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q23.4 is considered exempt from POA reporting.
ICD-10-CM Q23.4 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 306 Cardiac congenital and valvular disorders with mcc
  • 307 Cardiac congenital and valvular disorders without mcc

Convert Q23.4 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to Q23.4:
  • Type 1 Excludes: Q23.0
    , Q25.4
    ICD-10-CM Diagnosis Code Q23.0

    Congenital stenosis of aortic valve

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital aortic atresia
    • Congenital aortic stenosis NOS
    Type 1 Excludes
    • congenital stenosis of aortic valve in hypoplastic left heart syndrome (Q23.4)
    • congenital subaortic stenosis (Q24.4)
    • supravalvular aortic stenosis (congenital) (Q25.3)
    ICD-10-CM Diagnosis Code Q25.4

    Other congenital malformations of aorta

      2016 2017 - Converted to Parent Code 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • hypoplasia of aorta in hypoplastic left heart syndrome (Q23.4)

Diagnosis Index entries containing back-references to Q23.4:
  • Atresia, atretic
    • aortic (orifice) (valve) Q23.0
      ICD-10-CM Diagnosis Code Q23.0

      Congenital stenosis of aortic valve

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital aortic atresia
      • Congenital aortic stenosis NOS
      Type 1 Excludes
      • congenital stenosis of aortic valve in hypoplastic left heart syndrome (Q23.4)
      • congenital subaortic stenosis (Q24.4)
      • supravalvular aortic stenosis (congenital) (Q25.3)
      • congenital with hypoplasia of ascending aorta and defective development of left ventricle Q23.4 (with mitral stenosis)
      • in hypoplastic left heart syndrome Q23.4
    • mitral valve Q23.2
      ICD-10-CM Diagnosis Code Q23.2

      Congenital mitral stenosis

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital mitral atresia
      • in hypoplastic left heart syndrome Q23.4
  • Development
    • defective, congenital - see also Anomaly, by site
      • left ventricle Q24.8
        ICD-10-CM Diagnosis Code Q24.8

        Other specified congenital malformations of heart

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital diverticulum of left ventricle
        • Congenital malformation of myocardium
        • Congenital malformation of pericardium
        • Malposition of heart
        • Uhl's disease
        • in hypoplastic left heart syndrome Q23.4
  • Hypoplasia, hypoplastic
    • aorta, aortic Q25.42
      ICD-10-CM Diagnosis Code Q25.42

      Hypoplasia of aorta

        2017 - New Code 2018 2019 2020 Billable/Specific Code POA Exempt
      • valve Q23.1
        ICD-10-CM Diagnosis Code Q23.1

        Congenital insufficiency of aortic valve

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Bicuspid aortic valve
        • Congenital aortic insufficiency
        • in hypoplastic left heart syndrome Q23.4
      • ascending, in hypoplastic left heart syndrome Q23.4
    • left heart syndrome Q23.4
  • Syndrome - see also Disease
    • hypoplastic left-heart Q23.4

ICD-10-CM Codes Adjacent To Q23.4
Q22.4 Congenital tricuspid stenosis
Q22.5 Ebstein's anomaly
Q22.6 Hypoplastic right heart syndrome
Q22.8 Other congenital malformations of tricuspid valve
Q22.9 Congenital malformation of tricuspid valve, unspecified
Q23 Congenital malformations of aortic and mitral valves
Q23.0 Congenital stenosis of aortic valve
Q23.1 Congenital insufficiency of aortic valve
Q23.2 Congenital mitral stenosis
Q23.3 Congenital mitral insufficiency
Q23.4 Hypoplastic left heart syndrome
Q23.8 Other congenital malformations of aortic and mitral valves
Q23.9 Congenital malformation of aortic and mitral valves, unspecified
Q24 Other congenital malformations of heart
Q24.0 Dextrocardia
Q24.1 Levocardia
Q24.2 Cor triatriatum
Q24.3 Pulmonary infundibular stenosis
Q24.4 Congenital subaortic stenosis
Q24.5 Malformation of coronary vessels
Q24.6 Congenital heart block

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.