2023 ICD-10-CM Diagnosis Code Q26.8

Other congenital malformations of great veins

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • Q26.8 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2023 edition of ICD-10-CM Q26.8 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of Q26.8 - other international versions of ICD-10 Q26.8 may differ.
Applicable To
  • Absence of vena cava (inferior) (superior)
  • Azygos continuation of inferior vena cava
  • Persistent left posterior cardinal vein
  • Scimitar syndrome
The following code(s) above Q26.8 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q26.8:
  • Q00-Q99
    2023 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
Approximate Synonyms
  • Atresia of superior vena cava, congenital (at birth)
  • Congenital (at birth) absence of inferior vena cava
  • Congenital absence of inferior vena cava
  • Congenital absence of inferior vena cava (at birth)
  • Congenital atresia of superior vena cava
  • Congenital pulmonary vein stenosis (at birth)
  • Congenital stenosis of pulmonary veins
  • Congenital superior vena cava atresia (at birth)
  • Pulmonary vein stenosis, congenital (present at birth)
  • Scimitar syndrome
Clinical Information
  • A rare congenital cardiopulmonary defect characterized by abnormal right-sided pulmonary venous drainage and right lung malformations.
  • A rare congenital heart disorder in which all four pulmonary veins are not connected to the left atrium and drain into the systemic veins or the right atrium instead. Infants present with cyanosis, lethargy, tachypnea, respiratory infections, and poor growth.
  • An anomalous pulmonary venous return in which the right pulmonary vein is not connected to the left atrium but to the inferior vena cava. Scimitar syndrome is named for the crescent- or turkish sword-like shadow in the chest radiography and is often associated with hypoplasia of the right lung and right pulmonary artery, and dextroposition of the heart.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q26.8 is considered exempt from POA reporting.
ICD-10-CM Q26.8 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):
  • 306 Cardiac congenital and valvular disorders with mcc
  • 307 Cardiac congenital and valvular disorders without mcc

Convert Q26.8 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change

Diagnosis Index entries containing back-references to Q26.8:
  • Absence (of) (organ or part) (complete or partial)
    • vein (peripheral) Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix
      Type 1 Excludes
      • arteriovenous malformation (Q27.3-)
      • great Q26.8
    • superior vena cava, congenital Q26.8
    • vena cava Q26.8 (inferior) (superior)
  • Agenesis
    • vein(s) (peripheral) Q27.9
      ICD-10-CM Diagnosis Code Q27.9

      Congenital malformation of peripheral vascular system, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      • Anomaly of artery or vein NOS
      • great NEC Q26.8
    • vena cava Q26.8 (inferior) (superior)
  • Anomaly, anomalous (congenital) (unspecified type) Q89.9
    ICD-10-CM Diagnosis Code Q89.9

    Congenital malformation, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital anomaly NOS
    • Congenital deformity NOS
    • vein(s) (peripheral) Q27.9
      ICD-10-CM Diagnosis Code Q27.9

      Congenital malformation of peripheral vascular system, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      • Anomaly of artery or vein NOS
      • great Q26.9
        ICD-10-CM Diagnosis Code Q26.9

        Congenital malformation of great vein, unspecified

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly of vena cava (inferior) (superior) NOS
        • specified NEC Q26.8
    • venous return Q26.8
  • Atresia, atretic
    • vein NEC Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix
      Type 1 Excludes
      • arteriovenous malformation (Q27.3-)
      • great Q26.8
    • vena cava Q26.8 (inferior) (superior)
  • Azygos
    • continuation inferior vena cava Q26.8
  • Hypoplasia, hypoplastic
    • vein(s) (peripheral) Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix
      Type 1 Excludes
      • arteriovenous malformation (Q27.3-)
      • great Q26.8
    • vena cava Q26.8 (inferior) (superior)
  • Malformation (congenital) - see also Anomaly
    • great
      • vein Q26.9
        ICD-10-CM Diagnosis Code Q26.9

        Congenital malformation of great vein, unspecified

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly of vena cava (inferior) (superior) NOS
        • specified type NEC Q26.8
  • Malposition
    • congenital
      • vein(s) (peripheral) Q27.8
        ICD-10-CM Diagnosis Code Q27.8

        Other specified congenital malformations of peripheral vascular system

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        • Absence of peripheral vascular system
        • Atresia of peripheral vascular system
        • Congenital aneurysm (peripheral)
        • Congenital stricture, artery
        • Congenital varix
        Type 1 Excludes
        • arteriovenous malformation (Q27.3-)
        • great Q26.8
      • vena cava Q26.8 (inferior) (superior)
  • Persistence, persistent (congenital)
    • left
      • posterior cardinal vein Q26.8
    • sinus
      • venosus with imperfect incorporation in right auricle Q26.8
  • Scimitar syndrome Q26.8
  • Syndrome - see also Disease
    • scimitar Q26.8

ICD-10-CM Codes Adjacent To Q26.8
Q25.8 Other congenital malformations of other great arteries
Q25.9 Congenital malformation of great arteries, unspecified
Q26 Congenital malformations of great veins
Q26.0 Congenital stenosis of vena cava
Q26.1 Persistent left superior vena cava
Q26.2 Total anomalous pulmonary venous connection
Q26.3 Partial anomalous pulmonary venous connection
Q26.4 Anomalous pulmonary venous connection, unspecified
Q26.5 Anomalous portal venous connection
Q26.6 Portal vein-hepatic artery fistula
Q26.8 Other congenital malformations of great veins
Q26.9 Congenital malformation of great vein, unspecified
Q27 Other congenital malformations of peripheral vascular system
Q27.0 Congenital absence and hypoplasia of umbilical artery
Q27.1 Congenital renal artery stenosis
Q27.2 Other congenital malformations of renal artery
Q27.3 Arteriovenous malformation (peripheral)
Q27.30 Arteriovenous malformation, site unspecified
Q27.31 Arteriovenous malformation of vessel of upper limb
Q27.32 Arteriovenous malformation of vessel of lower limb
Q27.33 Arteriovenous malformation of digestive system vessel

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.