2020 ICD-10-CM Diagnosis Code Q33.0

Congenital cystic lung

    2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
  • Q33.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM Q33.0 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of Q33.0 - other international versions of ICD-10 Q33.0 may differ.
Applicable To
  • Congenital cystic lung disease
  • Congenital honeycomb lung
  • Congenital polycystic lung disease
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q33.0. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • cystic fibrosis (
    ICD-10-CM Diagnosis Code E84.0

    Cystic fibrosis with pulmonary manifestations

      2016 2017 2018 2019 2020 Billable/Specific Code
    Use Additional
    • code to identify any infectious organism present, such as:
    • Pseudomonas (B96.5)
    E84.0
    )
  • cystic lung disease, acquired or unspecified (
    ICD-10-CM Diagnosis Code J98.4

    Other disorders of lung

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Calcification of lung
    • Cystic lung disease (acquired)
    • Lung disease NOS
    • Pulmolithiasis
    Type 1 Excludes
    • acute interstitial pneumonitis (J84.114)
    • pulmonary insufficiency following surgery (J95.1-J95.2)
    J98.4
    )
The following code(s) above Q33.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q33.0:
  • Q00-Q99
    2020 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
Approximate Synonyms
  • Bronchogenic cyst
  • Congenital cystic adenomatoid malformation of lung
  • Congenital honeycomb lung
  • Cystic adenomatoid malformation
  • Cystic lung, congenital
  • Single lung cyst
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q33.0 is considered exempt from POA reporting.
ICD-10-CM Q33.0 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 205 Other respiratory system diagnoses with mcc
  • 206 Other respiratory system diagnoses without mcc

Convert Q33.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to Q33.0:
  • Cyst (colloid) (mucous) (simple) (retention)
    • bronchogenic (mediastinal) (sequestration) J98.4
      ICD-10-CM Diagnosis Code J98.4

      Other disorders of lung

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Calcification of lung
      • Cystic lung disease (acquired)
      • Lung disease NOS
      • Pulmolithiasis
      Type 1 Excludes
      • acute interstitial pneumonitis (J84.114)
      • pulmonary insufficiency following surgery (J95.1-J95.2)
      • congenital Q33.0
    • congenital NEC Q89.8
      ICD-10-CM Diagnosis Code Q89.8

      Other specified congenital malformations

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Use Additional
      • code(s) to identify all associated manifestations
      • lung Q33.0
    • lung J98.4
      ICD-10-CM Diagnosis Code J98.4

      Other disorders of lung

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Calcification of lung
      • Cystic lung disease (acquired)
      • Lung disease NOS
      • Pulmolithiasis
      Type 1 Excludes
      • acute interstitial pneumonitis (J84.114)
      • pulmonary insufficiency following surgery (J95.1-J95.2)
      • congenital Q33.0
  • Cystic - see also condition
    • lung disease J98.4
      ICD-10-CM Diagnosis Code J98.4

      Other disorders of lung

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Calcification of lung
      • Cystic lung disease (acquired)
      • Lung disease NOS
      • Pulmolithiasis
      Type 1 Excludes
      • acute interstitial pneumonitis (J84.114)
      • pulmonary insufficiency following surgery (J95.1-J95.2)
      • congenital Q33.0
  • Disease, diseased - see also Syndrome
    • cystic
      • lung J98.4
        ICD-10-CM Diagnosis Code J98.4

        Other disorders of lung

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Calcification of lung
        • Cystic lung disease (acquired)
        • Lung disease NOS
        • Pulmolithiasis
        Type 1 Excludes
        • acute interstitial pneumonitis (J84.114)
        • pulmonary insufficiency following surgery (J95.1-J95.2)
        • congenital Q33.0
    • lung J98.4
      ICD-10-CM Diagnosis Code J98.4

      Other disorders of lung

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Calcification of lung
      • Cystic lung disease (acquired)
      • Lung disease NOS
      • Pulmolithiasis
      Type 1 Excludes
      • acute interstitial pneumonitis (J84.114)
      • pulmonary insufficiency following surgery (J95.1-J95.2)
      • cystic J98.4
        ICD-10-CM Diagnosis Code J98.4

        Other disorders of lung

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Calcification of lung
        • Cystic lung disease (acquired)
        • Lung disease NOS
        • Pulmolithiasis
        Type 1 Excludes
        • acute interstitial pneumonitis (J84.114)
        • pulmonary insufficiency following surgery (J95.1-J95.2)
        • congenital Q33.0
      • polycystic J98.4
        ICD-10-CM Diagnosis Code J98.4

        Other disorders of lung

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Calcification of lung
        • Cystic lung disease (acquired)
        • Lung disease NOS
        • Pulmolithiasis
        Type 1 Excludes
        • acute interstitial pneumonitis (J84.114)
        • pulmonary insufficiency following surgery (J95.1-J95.2)
        • congenital Q33.0
    • polycystic
      • lung or pulmonary J98.4
        ICD-10-CM Diagnosis Code J98.4

        Other disorders of lung

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Calcification of lung
        • Cystic lung disease (acquired)
        • Lung disease NOS
        • Pulmolithiasis
        Type 1 Excludes
        • acute interstitial pneumonitis (J84.114)
        • pulmonary insufficiency following surgery (J95.1-J95.2)
        • congenital Q33.0
  • Honeycomb lung J98.4
    ICD-10-CM Diagnosis Code J98.4

    Other disorders of lung

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Calcification of lung
    • Cystic lung disease (acquired)
    • Lung disease NOS
    • Pulmolithiasis
    Type 1 Excludes
    • acute interstitial pneumonitis (J84.114)
    • pulmonary insufficiency following surgery (J95.1-J95.2)
    • congenital Q33.0
  • Polycystic (disease)
    • lung J98.4
      ICD-10-CM Diagnosis Code J98.4

      Other disorders of lung

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Calcification of lung
      • Cystic lung disease (acquired)
      • Lung disease NOS
      • Pulmolithiasis
      Type 1 Excludes
      • acute interstitial pneumonitis (J84.114)
      • pulmonary insufficiency following surgery (J95.1-J95.2)
      • congenital Q33.0

ICD-10-CM Codes Adjacent To Q33.0
Q31.5 Congenital laryngomalacia
Q31.8 Other congenital malformations of larynx
Q31.9 Congenital malformation of larynx, unspecified
Q32 Congenital malformations of trachea and bronchus
Q32.0 Congenital tracheomalacia
Q32.1 Other congenital malformations of trachea
Q32.2 Congenital bronchomalacia
Q32.3 Congenital stenosis of bronchus
Q32.4 Other congenital malformations of bronchus
Q33 Congenital malformations of lung
Q33.0 Congenital cystic lung
Q33.1 Accessory lobe of lung
Q33.2 Sequestration of lung
Q33.3 Agenesis of lung
Q33.4 Congenital bronchiectasis
Q33.5 Ectopic tissue in lung
Q33.6 Congenital hypoplasia and dysplasia of lung
Q33.8 Other congenital malformations of lung
Q33.9 Congenital malformation of lung, unspecified
Q34 Other congenital malformations of respiratory system
Q34.0 Anomaly of pleura

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.