2019 ICD-10-CM Diagnosis Code Q40.0

Congenital hypertrophic pyloric stenosis

    2016 2017 2018 2019 Billable/Specific Code POA Exempt
  • Q40.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM Q40.0 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of Q40.0 - other international versions of ICD-10 Q40.0 may differ.
Applicable To
  • Congenital or infantile constriction
  • Congenital or infantile hypertrophy
  • Congenital or infantile spasm
  • Congenital or infantile stenosis
  • Congenital or infantile stricture
The following code(s) above Q40.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q40.0:
  • Q00-Q99
    2019 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
Approximate Synonyms
  • Hypertrophic pyloric stenosis, congenital
Clinical Information
  • An abnormality characterized by thickening of the muscle in the wall of the pylorus. It results in the narrowing of the pyloric channel. The overlying mucosa may appear hypertrophic as well. Clinical signs and symptoms appear early in life and include projectile vomiting and dehydration.
  • Narrowing of the pyloric canal due to hypertrophy of the surrounding circular muscle. It is usually seen in infants or young children.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q40.0 is considered exempt from POA reporting.
ICD-10-CM Q40.0 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 393 Other digestive system diagnoses with mcc
  • 394 Other digestive system diagnoses with cc
  • 395 Other digestive system diagnoses without cc/mcc

Convert Q40.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
Code annotations containing back-references to Q40.0:
  • Type 1 Excludes: K31.1
    , K31.3
    ICD-10-CM Diagnosis Code K31.1

    Adult hypertrophic pyloric stenosis

      2016 2017 2018 2019 Billable/Specific Code Adult Dx (15-124 years)
    Applicable To
    • Pyloric stenosis NOS
    Type 1 Excludes
    • congenital or infantile pyloric stenosis (Q40.0)
    ICD-10-CM Diagnosis Code K31.3

    Pylorospasm, not elsewhere classified

      2016 2017 2018 2019 Billable/Specific Code
    Type 1 Excludes
    • congenital or infantile pylorospasm (Q40.0)
    • neurotic pylorospasm (F45.8)
    • psychogenic pylorospasm (F45.8)

Diagnosis Index entries containing back-references to Q40.0:
  • Achalasia (cardia) (esophagus) K22.0
    ICD-10-CM Diagnosis Code K22.0

    Achalasia of cardia

      2016 2017 2018 2019 Billable/Specific Code
    Applicable To
    • Achalasia NOS
    • Cardiospasm
    Type 1 Excludes
    • congenital cardiospasm (Q39.5)
    • pylorus Q40.0
  • Constriction - see also Stricture
    • pylorus (adult hypertrophic) K31.1
      ICD-10-CM Diagnosis Code K31.1

      Adult hypertrophic pyloric stenosis

        2016 2017 2018 2019 Billable/Specific Code Adult Dx (15-124 years)
      Applicable To
      • Pyloric stenosis NOS
      Type 1 Excludes
      • congenital or infantile pyloric stenosis (Q40.0)
      • congenital or infantile Q40.0
      • newborn Q40.0
  • Hypertrophy, hypertrophic
    • pylorus (adult) (muscle) (sphincter) K31.1
      ICD-10-CM Diagnosis Code K31.1

      Adult hypertrophic pyloric stenosis

        2016 2017 2018 2019 Billable/Specific Code Adult Dx (15-124 years)
      Applicable To
      • Pyloric stenosis NOS
      Type 1 Excludes
      • congenital or infantile pyloric stenosis (Q40.0)
      • congenital or infantile Q40.0
  • Obstruction, obstructed, obstructive
    • pylorus
      • congenital or infantile Q40.0
  • Pylorospasm (reflex) K31.3
    ICD-10-CM Diagnosis Code K31.3

    Pylorospasm, not elsewhere classified

      2016 2017 2018 2019 Billable/Specific Code
    Type 1 Excludes
    • congenital or infantile pylorospasm (Q40.0)
    • neurotic pylorospasm (F45.8)
    • psychogenic pylorospasm (F45.8)
    • congenital or infantile Q40.0
    • newborn Q40.0
  • Spasm(s) R25.2
    - see also condition
    ICD-10-CM Diagnosis Code R25.2

    Cramp and spasm

      2016 2017 2018 2019 Billable/Specific Code
    Type 2 Excludes
    • pylorus NEC K31.3
      ICD-10-CM Diagnosis Code K31.3

      Pylorospasm, not elsewhere classified

        2016 2017 2018 2019 Billable/Specific Code
      Type 1 Excludes
      • congenital or infantile pylorospasm (Q40.0)
      • neurotic pylorospasm (F45.8)
      • psychogenic pylorospasm (F45.8)
      • congenital or infantile Q40.0
  • Stenosis, stenotic (cicatricial) - see also Stricture
    • pylorus (hypertrophic) (acquired) K31.1
      ICD-10-CM Diagnosis Code K31.1

      Adult hypertrophic pyloric stenosis

        2016 2017 2018 2019 Billable/Specific Code Adult Dx (15-124 years)
      Applicable To
      • Pyloric stenosis NOS
      Type 1 Excludes
      • congenital or infantile pyloric stenosis (Q40.0)
      • congenital Q40.0
      • infantile Q40.0
  • Stricture - see also Stenosis
    • pylorus (hypertrophic) K31.1
      ICD-10-CM Diagnosis Code K31.1

      Adult hypertrophic pyloric stenosis

        2016 2017 2018 2019 Billable/Specific Code Adult Dx (15-124 years)
      Applicable To
      • Pyloric stenosis NOS
      Type 1 Excludes
      • congenital or infantile pyloric stenosis (Q40.0)
      • congenital Q40.0
      • infantile Q40.0

ICD-10-CM Codes Adjacent To Q40.0
Q39.0 Atresia of esophagus without fistula
Q39.1 Atresia of esophagus with tracheo-esophageal fistula
Q39.2 Congenital tracheo-esophageal fistula without atresia
Q39.3 Congenital stenosis and stricture of esophagus
Q39.4 Esophageal web
Q39.5 Congenital dilatation of esophagus
Q39.6 Congenital diverticulum of esophagus
Q39.8 Other congenital malformations of esophagus
Q39.9 Congenital malformation of esophagus, unspecified
Q40 Other congenital malformations of upper alimentary tract
Q40.0 Congenital hypertrophic pyloric stenosis
Q40.1 Congenital hiatus hernia
Q40.2 Other specified congenital malformations of stomach
Q40.3 Congenital malformation of stomach, unspecified
Q40.8 Other specified congenital malformations of upper alimentary tract
Q40.9 Congenital malformation of upper alimentary tract, unspecified
Q41 Congenital absence, atresia and stenosis of small intestine
Q41.0 Congenital absence, atresia and stenosis of duodenum
Q41.1 Congenital absence, atresia and stenosis of jejunum
Q41.2 Congenital absence, atresia and stenosis of ileum
Q41.8 Congenital absence, atresia and stenosis of other specified parts of small intestine

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.