2019 ICD-10-CM Diagnosis Code Q44.6

Cystic disease of liver

    2016 2017 2018 2019 Billable/Specific Code POA Exempt
  • Q44.6 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM Q44.6 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of Q44.6 - other international versions of ICD-10 Q44.6 may differ.
Applicable To
  • Fibrocystic disease of liver
The following code(s) above Q44.6 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q44.6:
  • Q00-Q99
    2019 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
Approximate Synonyms
  • Congenital cystic disease of liver
  • Cystic liver, congenital
Clinical Information
  • A usually asymptomatic hereditary disorder which is often associated with polycystic kidney disease. It is characterized by the presence of fluid-filled biliary cysts throughout the liver.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q44.6 is considered exempt from POA reporting.
ICD-10-CM Q44.6 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 441 Disorders of liver except malignancy, cirrhosis or alcoholic hepatitis with mcc
  • 442 Disorders of liver except malignancy, cirrhosis or alcoholic hepatitis with cc
  • 443 Disorders of liver except malignancy, cirrhosis or alcoholic hepatitis without cc/mcc

Convert Q44.6 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
Code annotations containing back-references to Q44.6:
  • Type 2 Excludes: K76
    ICD-10-CM Diagnosis Code K76

    Other diseases of liver

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • alcoholic liver disease (K70.-)
    • amyloid degeneration of liver (E85.-)
    • cystic disease of liver (congenital) (Q44.6)
    • hepatic vein thrombosis (I82.0)
    • hepatomegaly NOS (R16.0)
    • pigmentary cirrhosis (of liver) (E83.110)
    • portal vein thrombosis (I81)
    • toxic liver disease (K71.-)

Diagnosis Index entries containing back-references to Q44.6:
  • Cyst (colloid) (mucous) (simple) (retention)
    • congenital NEC Q89.8
      ICD-10-CM Diagnosis Code Q89.8

      Other specified congenital malformations

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Use Additional
      • code(s) to identify all associated manifestations
      • liver Q44.6
    • liver (idiopathic) (simple) K76.89
      ICD-10-CM Diagnosis Code K76.89

      Other specified diseases of liver

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Cyst (simple) of liver
      • Focal nodular hyperplasia of liver
      • Hepatoptosis
      • congenital Q44.6
  • Cystic - see also condition
    • liver, congenital Q44.6
  • Degeneration, degenerative
    • liver (diffuse) K76.89
      ICD-10-CM Diagnosis Code K76.89

      Other specified diseases of liver

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Cyst (simple) of liver
      • Focal nodular hyperplasia of liver
      • Hepatoptosis
      • cystic K76.89
        ICD-10-CM Diagnosis Code K76.89

        Other specified diseases of liver

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Cyst (simple) of liver
        • Focal nodular hyperplasia of liver
        • Hepatoptosis
        • congenital Q44.6
  • Disease, diseased - see also Syndrome
    • cystic
      • liver, congenital Q44.6
    • liver (chronic) (organic) K76.9
      ICD-10-CM Diagnosis Code K76.9

      Liver disease, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • cystic, congenital Q44.6
      • fibrocystic Q44.6 (congenital)
      • polycystic Q44.6 (congenital)
    • polycystic
      • liver or hepatic Q44.6
  • Fibrocystic
    • disease - see also Fibrosis, cystic
      • liver Q44.6
  • Polycystic (disease)
    • liver Q44.6

ICD-10-CM Codes Adjacent To Q44.6
Q43.7 Persistent cloaca
Q43.8 Other specified congenital malformations of intestine
Q43.9 Congenital malformation of intestine, unspecified
Q44 Congenital malformations of gallbladder, bile ducts and liver
Q44.0 Agenesis, aplasia and hypoplasia of gallbladder
Q44.1 Other congenital malformations of gallbladder
Q44.2 Atresia of bile ducts
Q44.3 Congenital stenosis and stricture of bile ducts
Q44.4 Choledochal cyst
Q44.5 Other congenital malformations of bile ducts
Q44.6 Cystic disease of liver
Q44.7 Other congenital malformations of liver
Q45 Other congenital malformations of digestive system
Q45.0 Agenesis, aplasia and hypoplasia of pancreas
Q45.1 Annular pancreas
Q45.2 Congenital pancreatic cyst
Q45.3 Other congenital malformations of pancreas and pancreatic duct
Q45.8 Other specified congenital malformations of digestive system
Q45.9 Congenital malformation of digestive system, unspecified
Q50 Congenital malformations of ovaries, fallopian tubes and broad ligaments
Q50.0 Congenital absence of ovary

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.