2020 ICD-10-CM Diagnosis Code Q56

Indeterminate sex and pseudohermaphroditism

    2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
  • Q56 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2020 edition of ICD-10-CM Q56 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of Q56 - other international versions of ICD-10 Q56 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q56. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • 46,XX true hermaphrodite (
    ICD-10-CM Diagnosis Code Q99.1

    46, XX true hermaphrodite

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • 46, XX with streak gonads
    • 46, XY with streak gonads
    • Pure gonadal dysgenesis
    Q99.1
    )
  • androgen insensitivity syndrome (
    ICD-10-CM Diagnosis Code E34.5

    Androgen insensitivity syndrome

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    E34.5-
    )
  • chimera 46,XX/46,XY true hermaphrodite (
    ICD-10-CM Diagnosis Code Q99.0

    Chimera 46, XX/46, XY

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • Chimera 46, XX/46, XY true hermaphrodite
    Q99.0
    )
  • female pseudohermaphroditism with adrenocortical disorder (
    ICD-10-CM Diagnosis Code E25
    • E25 Adrenogenital disorders
      • E25.0 Congenital adrenogenital disorders associated...
      • E25.8 Other adrenogenital disorders
      • E25.9 Adrenogenital disorder, unspecified
    E25.-
    )
  • pseudohermaphroditism with specified chromosomal anomaly (
    ICD-10-CM Diagnosis Code Q96

    Turner's syndrome

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Q96
    -
    ICD-10-CM Diagnosis Code Q99

    Other chromosome abnormalities, not elsewhere classified

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Q99
    )
  • pure gonadal dysgenesis (
    ICD-10-CM Diagnosis Code Q99.1

    46, XX true hermaphrodite

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Applicable To
    • 46, XX with streak gonads
    • 46, XY with streak gonads
    • Pure gonadal dysgenesis
    Q99.1
    )
The following code(s) above Q56 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q56:
  • Q00-Q99
    2020 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q50-Q56
    2020 ICD-10-CM Range Q50-Q56

    Congenital malformations of genital organs

    Type 1 Excludes
    • androgen insensitivity syndrome (E34.5-)
    • syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)
    Congenital malformations of genital organs
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to Q56:
  • Type 1 Excludes: E25
    ICD-10-CM Diagnosis Code E25

    Adrenogenital disorders

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Includes
    • adrenogenital syndromes, virilizing or feminizing, whether acquired or due to adrenal hyperplasia consequent on inborn enzyme defects in hormone synthesis
    • Female adrenal pseudohermaphroditism
    • Female heterosexual precocious pseudopuberty
    • Male isosexual precocious pseudopuberty
    • Male macrogenitosomia praecox
    • Male sexual precocity with adrenal hyperplasia
    • Male virilization (female)
    Type 1 Excludes
    • indeterminate sex and pseudohermaphroditism (Q56)
    • chromosomal abnormalities (Q90-Q99)
ICD-10-CM Codes Adjacent To Q56
Q55.5 Congenital absence and aplasia of penis
Q55.6 Other congenital malformations of penis
Q55.61 Curvature of penis (lateral)
Q55.62 Hypoplasia of penis
Q55.63 Congenital torsion of penis
Q55.64 Hidden penis
Q55.69 Other congenital malformation of penis
Q55.7 Congenital vasocutaneous fistula
Q55.8 Other specified congenital malformations of male genital organs
Q55.9 Congenital malformation of male genital organ, unspecified
Q56 Indeterminate sex and pseudohermaphroditism
Q56.0 Hermaphroditism, not elsewhere classified
Q56.1 Male pseudohermaphroditism, not elsewhere classified
Q56.2 Female pseudohermaphroditism, not elsewhere classified
Q56.3 Pseudohermaphroditism, unspecified
Q56.4 Indeterminate sex, unspecified
Q60 Renal agenesis and other reduction defects of kidney
Q60.0 Renal agenesis, unilateral
Q60.1 Renal agenesis, bilateral
Q60.2 Renal agenesis, unspecified
Q60.3 Renal hypoplasia, unilateral

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.