ICD-10-CM Codes
Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities
Q50-Q56 Congenital malformations of genital organs
Q56- Indeterminate sex and pseudohermaphroditism
2021 ICD-10-CM Diagnosis Code Q56

2021 ICD-10-CM Diagnosis Code Q56

Indeterminate sex and pseudohermaphroditism

2016

2017

2018

2019

2020

2021

Non-Billable/Non-Specific Code

Q56 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
The 2021 edition of ICD-10-CM Q56 became effective on October 1, 2020.
This is the American ICD-10-CM version of Q56 - other international versions of ICD-10 Q56 may differ.

Type 1 Excludes

Type 1 Excludes Help

A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q56. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

46,XX true hermaphrodite (
ICD-10-CM Diagnosis Code Q99.1
46, XX true hermaphrodite
Applicable To
- 46, XX with streak gonads
- 46, XY with streak gonads
- Pure gonadal dysgenesis
Q99.1
)
androgen insensitivity syndrome (
ICD-10-CM Diagnosis Code E34.5
Androgen insensitivity syndrome
E34.5-
)
chimera 46,XX/46,XY true hermaphrodite (
ICD-10-CM Diagnosis Code Q99.0
Chimera 46, XX/46, XY
Applicable To
- Chimera 46, XX/46, XY true hermaphrodite
Q99.0
)
female pseudohermaphroditism with adrenocortical disorder (
ICD-10-CM Diagnosis Code E25
- E25 Adrenogenital disorders
  - E25.0 Congenital adrenogenital disorders associated...
  - E25.8 Other adrenogenital disorders
  - E25.9 Adrenogenital disorder, unspecified
E25.-
)
pseudohermaphroditism with specified chromosomal anomaly (
ICD-10-CM Diagnosis Code Q96
Turner's syndrome
Type 1 Excludes
- Noonan syndrome (Q87.19)
Q96
-
ICD-10-CM Diagnosis Code Q99
Other chromosome abnormalities, not elsewhere classified
Q99
)
pure gonadal dysgenesis (
ICD-10-CM Diagnosis Code Q99.1
46, XX true hermaphrodite
Applicable To
- 46, XX with streak gonads
- 46, XY with streak gonads
- Pure gonadal dysgenesis
Q99.1
)

The following code(s) above Q56 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to Q56:

Q00-Q99
2021 ICD-10-CM Range Q00-Q99
Congenital malformations, deformations and chromosomal abnormalities
Note
- Codes from this chapter are not for use on maternal records
Type 2 Excludes
- inborn errors of metabolism (E70-E88)
Congenital malformations, deformations and chromosomal abnormalities
Q50-Q56
2021 ICD-10-CM Range Q50-Q56
Congenital malformations of genital organs
Type 1 Excludes
- androgen insensitivity syndrome (E34.5-)
- syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)
Congenital malformations of genital organs

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change

Code annotations containing back-references to Q56:

Type 1 Excludes: E25

ICD-10-CM Diagnosis Code E25
Adrenogenital disorders
Includes
- adrenogenital syndromes, virilizing or feminizing, whether acquired or due to adrenal hyperplasia consequent on inborn enzyme defects in hormone synthesis
- Female adrenal pseudohermaphroditism
- Female heterosexual precocious pseudopuberty
- Male isosexual precocious pseudopuberty
- Male macrogenitosomia praecox
- Male sexual precocity with adrenal hyperplasia
- Male virilization (female)
Type 1 Excludes
- indeterminate sex and pseudohermaphroditism (Q56)
- chromosomal abnormalities (Q90-Q99)

ICD-10-CM Codes Adjacent To Q56

Q55.5 Congenital absence and aplasia of penis

Q55.6 Other congenital malformations of penis

Q55.61 Curvature of penis (lateral)

Q55.62 Hypoplasia of penis

Q55.63 Congenital torsion of penis

Q55.64 Hidden penis

Q55.69 Other congenital malformation of penis

Q55.7 Congenital vasocutaneous fistula

Q55.8 Other specified congenital malformations of male genital organs

Q55.9 Congenital malformation of male genital organ, unspecified

Q56 Indeterminate sex and pseudohermaphroditism

Q56.0 Hermaphroditism, not elsewhere classified

Q56.1 Male pseudohermaphroditism, not elsewhere classified

Q56.2 Female pseudohermaphroditism, not elsewhere classified

Q56.3 Pseudohermaphroditism, unspecified

Q56.4 Indeterminate sex, unspecified

Q60 Renal agenesis and other reduction defects of kidney

Q60.0 Renal agenesis, unilateral

Q60.1 Renal agenesis, bilateral

Q60.2 Renal agenesis, unspecified

Q60.3 Renal hypoplasia, unilateral

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2021 ICD-10-CM Diagnosis Code Q56

Indeterminate sex and pseudohermaphroditism

46, XX true hermaphrodite

Androgen insensitivity syndrome

Chimera 46, XX/46, XY

Turner's syndrome

Other chromosome abnormalities, not elsewhere classified

46, XX true hermaphrodite

Congenital malformations, deformations and chromosomal abnormalities

Congenital malformations of genital organs

Adrenogenital disorders