2020 ICD-10-CM Diagnosis Code Q61.1

Polycystic kidney, infantile type

    2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
  • Q61.1 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2020 edition of ICD-10-CM Q61.1 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of Q61.1 - other international versions of ICD-10 Q61.1 may differ.
Applicable To
  • Polycystic kidney, autosomal recessive
The following code(s) above Q61.1 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q61.1:
  • Q00-Q99
    2020 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q61
    ICD-10-CM Diagnosis Code Q61

    Cystic kidney disease

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • acquired cyst of kidney (N28.1)
    • Potter's syndrome (Q60.6)
    Cystic kidney disease
Clinical Information
  • A genetic disorder with autosomal recessive inheritance, characterized by multiple cysts in both kidneys and associated liver lesions. Serious manifestations are usually present at birth with high perinatal mortality.
  • Polycystic kidney disease inherited in an autosomal recessive pattern. Patients present with progressive renal failure early in life. The autosomal recessive trait is associated with abnormalities of chromosome 6.
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
ICD-10-CM Codes Adjacent To Q61.1
Q60.2 Renal agenesis, unspecified
Q60.3 Renal hypoplasia, unilateral
Q60.4 Renal hypoplasia, bilateral
Q60.5 Renal hypoplasia, unspecified
Q60.6 Potter's syndrome
Q61 Cystic kidney disease
Q61.0 Congenital renal cyst
Q61.00 …… unspecified
Q61.01 Congenital single renal cyst
Q61.02 Congenital multiple renal cysts
Q61.1 Polycystic kidney, infantile type
Q61.11 Cystic dilatation of collecting ducts
Q61.19 Other polycystic kidney, infantile type
Q61.2 Polycystic kidney, adult type
Q61.3 Polycystic kidney, unspecified
Q61.4 Renal dysplasia
Q61.5 Medullary cystic kidney
Q61.8 Other cystic kidney diseases
Q61.9 Cystic kidney disease, unspecified
Q62 Congenital obstructive defects of renal pelvis and congenital malformations of ureter
Q62.0 Congenital hydronephrosis

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.