Other congenital malformations of skull and face bones Q75-

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Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q75. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • congenital malformation of face NOS (
    ICD-10-CM Diagnosis Code Q18
    • Q18 Other congenital malformations of face and ne...
      • Q18.0 Sinus, fistula and cyst of branchial cleft
      • Q18.1 Preauricular sinus and cyst
      • Q18.2 Other branchial cleft malformations
      • Q18.3 Webbing of neck
      • Q18.4 Macrostomia
      • Q18.5 Microstomia
      • Q18.6 Macrocheilia
      • Q18.7 Microcheilia
      • Q18.8 Other specified congenital malformations of f...
      • Q18.9 Congenital malformation of face and neck, uns...
  • congenital malformation syndromes classified to
    ICD-10-CM Diagnosis Code Q87
    • Q87 Other specified congenital malformation syndr...
      • Q87.0 Congenital malformation syndromes predominant...
      • Q87.1 Congenital malformation syndromes predominant...
        • Q87.11 Prader-Willi syndrome
        • Q87.19 Other congenital malformation syndromes predo...
      • Q87.2 Congenital malformation syndromes predominant...
      • Q87.3 Congenital malformation syndromes involving e...
      • Q87.4 Marfan's syndrome
        • Q87.40 …… unspecified
        • Q87.41 Marfan's syndrome with cardiovascular manifes...
          • Q87.410 Marfan's syndrome with aortic dilation
          • Q87.418 Marfan's syndrome with other cardiovascular m...
        • Q87.42 …… with ocular manifestations
        • Q87.43 Marfan's syndrome with skeletal manifestation...
      • Q87.5 Other congenital malformation syndromes with ...
      • Q87.8 Other specified congenital malformation syndr...
        • Q87.81 Alport syndrome
        • Q87.82 Arterial tortuosity syndrome
        • Q87.89 Other specified congenital malformation syndr...
  • dentofacial anomalies [including malocclusion] (
    ICD-10-CM Diagnosis Code M26
    • M26 Dentofacial anomalies [including malocclusion...
      • M26.0 Major anomalies of jaw size
        • M26.00 Unspecified anomaly of jaw size
        • M26.01 Maxillary hyperplasia
        • M26.02 Maxillary hypoplasia
        • M26.03 Mandibular hyperplasia
        • M26.04 Mandibular hypoplasia
        • M26.05 Macrogenia
        • M26.06 Microgenia
        • M26.07 Excessive tuberosity of jaw
        • M26.09 Other specified anomalies of jaw size
      • M26.1 Anomalies of jaw-cranial base relationship
        • M26.10 Unspecified anomaly of jaw-cranial base relat...
        • M26.11 Maxillary asymmetry
        • M26.12 Other jaw asymmetry
        • M26.19 Other specified anomalies of jaw-cranial base...
      • M26.2 Anomalies of dental arch relationship
        • M26.20 Unspecified anomaly of dental arch relationsh...
        • M26.21 Malocclusion, Angle's class
        • M26.22 Open occlusal relationship
          • M26.220 Open anterior occlusal relationship
          • M26.221 Open posterior occlusal relationship
        • M26.23 Excessive horizontal overlap
        • M26.24 Reverse articulation
        • M26.25 Anomalies of interarch distance
        • M26.29 Other anomalies of dental arch relationship
      • M26.3 Anomalies of tooth position of fully erupted ...
        • M26.30 Unspecified anomaly of tooth position of full...
        • M26.31 Crowding of fully erupted teeth
        • M26.32 Excessive spacing of fully erupted teeth
        • M26.33 Horizontal displacement of fully erupted toot...
        • M26.34 Vertical displacement of fully erupted tooth ...
        • M26.35 Rotation of fully erupted tooth or teeth
        • M26.36 Insufficient interocclusal distance of fully ...
        • M26.37 Excessive interocclusal distance of fully eru...
        • M26.39 Other anomalies of tooth position of fully er...
      • M26.4 Malocclusion, unspecified
      • M26.5 Dentofacial functional abnormalities
        • M26.50 Dentofacial functional abnormalities, unspeci...
        • M26.51 Abnormal jaw closure
        • M26.52 Limited mandibular range of motion
        • M26.53 Deviation in opening and closing of the mandi...
        • M26.54 Insufficient anterior guidance
        • M26.55 Centric occlusion maximum intercuspation disc...
        • M26.56 Non-working side interference
        • M26.57 Lack of posterior occlusal support
        • M26.59 Other dentofacial functional abnormalities
      • M26.6 Temporomandibular joint disorders
        • M26.60 Temporomandibular joint disorder, unspecified...
          • M26.601 Right temporomandibular joint disorder, unspe...
          • M26.602 Left temporomandibular joint disorder, unspec...
          • M26.603 Bilateral temporomandibular joint disorder, u...
          • M26.609 Unspecified temporomandibular joint disorder,...
        • M26.61 Adhesions and ankylosis of temporomandibular ...
          • M26.611 Adhesions and ankylosis of right temporomandi...
          • M26.612 Adhesions and ankylosis of left temporomandib...
          • M26.613 Adhesions and ankylosis of bilateral temporom...
          • M26.619 Adhesions and ankylosis of temporomandibular ...
        • M26.62 Arthralgia of temporomandibular joint
          • M26.621 Arthralgia of right temporomandibular joint
          • M26.622 Arthralgia of left temporomandibular joint
          • M26.623 Arthralgia of bilateral temporomandibular joi...
          • M26.629 Arthralgia of temporomandibular joint, unspec...
        • M26.63 Articular disc disorder of temporomandibular ...
          • M26.631 Articular disc disorder of right temporomandi...
          • M26.632 Articular disc disorder of left temporomandib...
          • M26.633 Articular disc disorder of bilateral temporom...
          • M26.639 Articular disc disorder of temporomandibular ...
        • M26.64 Arthritis of temporomandibular joint
          • M26.641 Arthritis of right temporomandibular joint
          • M26.642 Arthritis of left temporomandibular joint
          • M26.643 Arthritis of bilateral temporomandibular join...
          • M26.649 Arthritis of unspecified temporomandibular jo...
        • M26.65 Arthropathy of temporomandibular joint
          • M26.651 Arthropathy of right temporomandibular joint
          • M26.652 Arthropathy of left temporomandibular joint
          • M26.653 Arthropathy of bilateral temporomandibular jo...
          • M26.659 Arthropathy of unspecified temporomandibular ...
        • M26.69 Other specified disorders of temporomandibula...
      • M26.7 Dental alveolar anomalies
        • M26.70 Unspecified alveolar anomaly
        • M26.71 Alveolar maxillary hyperplasia
        • M26.72 Alveolar mandibular hyperplasia
        • M26.73 Alveolar maxillary hypoplasia
        • M26.74 Alveolar mandibular hypoplasia
        • M26.79 Other specified alveolar anomalies
      • M26.8 Other dentofacial anomalies
        • M26.81 Anterior soft tissue impingement
        • M26.82 Posterior soft tissue impingement
        • M26.89 Other dentofacial anomalies
      • M26.9 Dentofacial anomaly, unspecified
  • musculoskeletal deformities of head and face (
    ICD-10-CM Diagnosis Code Q67.0

    Congenital facial asymmetry

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    ICD-10-CM Diagnosis Code Q67.4

    Other congenital deformities of skull, face and jaw

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital depressions in skull
    • Congenital hemifacial atrophy or hypertrophy
    • Deviation of nasal septum, congenital
    • Squashed or bent nose, congenital
    Type 1 Excludes
    • dentofacial anomalies [including malocclusion] (M26.-)
    • syphilitic saddle nose (A50.5)
  • skull defects associated with congenital anomalies of brain such as:
  • anencephaly (
    ICD-10-CM Diagnosis Code Q00.0


      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    • Acephaly
    • Acrania
    • Amyelencephaly
    • Hemianencephaly
    • Hemicephaly
  • encephalocele (
    ICD-10-CM Diagnosis Code Q01
    • Q01 Encephalocele
      • Q01.0 Frontal encephalocele
      • Q01.1 Nasofrontal encephalocele
      • Q01.2 Occipital encephalocele
      • Q01.8 Encephalocele of other sites
      • Q01.9 Encephalocele, unspecified
  • hydrocephalus (
    ICD-10-CM Diagnosis Code Q03
    • Q03 Congenital hydrocephalus
      • Q03.0 Malformations of aqueduct of Sylvius
      • Q03.1 Atresia of foramina of Magendie and Luschka
      • Q03.8 Other congenital hydrocephalus
      • Q03.9 Congenital hydrocephalus, unspecified
  • microcephaly (
    ICD-10-CM Diagnosis Code Q02


      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Code First
    • , if applicable, congenital Zika virus disease
    • hydromicrocephaly
    • micrencephalon
    Type 1 Excludes
    • Meckel-Gruber syndrome (Q61.9)
  • Q75 Other congenital malformations of skull and face bones
    • Q75.0 Craniosynostosis
    • Q75.1 Craniofacial dysostosis
    • Q75.2 Hypertelorism
    • Q75.3 Macrocephaly
    • Q75.4 Mandibulofacial dysostosis
    • Q75.5 Oculomandibular dysostosis
    • Q75.8 Other specified congenital malformations of skull and face bones
    • Q75.9 Congenital malformation of skull and face bones, unspecified