2021 ICD-10-CM Diagnosis Code Q75

Other congenital malformations of skull and face bones

    2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
  • Q75 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
  • The 2021 edition of ICD-10-CM Q75 became effective on October 1, 2020.
  • This is the American ICD-10-CM version of Q75 - other international versions of ICD-10 Q75 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q75. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • congenital malformation of face NOS (
    ICD-10-CM Diagnosis Code Q18
    • Q18 Other congenital malformations of face and ne...
      • Q18.0 Sinus, fistula and cyst of branchial cleft
      • Q18.1 Preauricular sinus and cyst
      • Q18.2 Other branchial cleft malformations
      • Q18.3 Webbing of neck
      • Q18.4 Macrostomia
      • Q18.5 Microstomia
      • Q18.6 Macrocheilia
      • Q18.7 Microcheilia
      • Q18.8 Other specified congenital malformations of f...
      • Q18.9 Congenital malformation of face and neck, uns...
  • congenital malformation syndromes classified to
    ICD-10-CM Diagnosis Code Q87
    • Q87 Other specified congenital malformation syndr...
      • Q87.0 Congenital malformation syndromes predominant...
      • Q87.1 Congenital malformation syndromes predominant...
        • Q87.11 Prader-Willi syndrome
        • Q87.19 Other congenital malformation syndromes predo...
      • Q87.2 Congenital malformation syndromes predominant...
      • Q87.3 Congenital malformation syndromes involving e...
      • Q87.4 Marfan's syndrome
        • Q87.40 …… unspecified
        • Q87.41 Marfan's syndrome with cardiovascular manifes...
          • Q87.410 Marfan's syndrome with aortic dilation
          • Q87.418 Marfan's syndrome with other cardiovascular m...
        • Q87.42 …… with ocular manifestations
        • Q87.43 Marfan's syndrome with skeletal manifestation...
      • Q87.5 Other congenital malformation syndromes with ...
      • Q87.8 Other specified congenital malformation syndr...
        • Q87.81 Alport syndrome
        • Q87.82 Arterial tortuosity syndrome
        • Q87.89 Other specified congenital malformation syndr...
  • dentofacial anomalies [including malocclusion] (
    ICD-10-CM Diagnosis Code M26
    • M26 Dentofacial anomalies [including malocclusion...
      • M26.0 Major anomalies of jaw size
        • M26.00 Unspecified anomaly of jaw size
        • M26.01 Maxillary hyperplasia
        • M26.02 Maxillary hypoplasia
        • M26.03 Mandibular hyperplasia
        • M26.04 Mandibular hypoplasia
        • M26.05 Macrogenia
        • M26.06 Microgenia
        • M26.07 Excessive tuberosity of jaw
        • M26.09 Other specified anomalies of jaw size
      • M26.1 Anomalies of jaw-cranial base relationship
        • M26.10 Unspecified anomaly of jaw-cranial base relat...
        • M26.11 Maxillary asymmetry
        • M26.12 Other jaw asymmetry
        • M26.19 Other specified anomalies of jaw-cranial base...
      • M26.2 Anomalies of dental arch relationship
        • M26.20 Unspecified anomaly of dental arch relationsh...
        • M26.21 Malocclusion, Angle's class
        • M26.22 Open occlusal relationship
          • M26.220 Open anterior occlusal relationship
          • M26.221 Open posterior occlusal relationship
        • M26.23 Excessive horizontal overlap
        • M26.24 Reverse articulation
        • M26.25 Anomalies of interarch distance
        • M26.29 Other anomalies of dental arch relationship
      • M26.3 Anomalies of tooth position of fully erupted ...
        • M26.30 Unspecified anomaly of tooth position of full...
        • M26.31 Crowding of fully erupted teeth
        • M26.32 Excessive spacing of fully erupted teeth
        • M26.33 Horizontal displacement of fully erupted toot...
        • M26.34 Vertical displacement of fully erupted tooth ...
        • M26.35 Rotation of fully erupted tooth or teeth
        • M26.36 Insufficient interocclusal distance of fully ...
        • M26.37 Excessive interocclusal distance of fully eru...
        • M26.39 Other anomalies of tooth position of fully er...
      • M26.4 Malocclusion, unspecified
      • M26.5 Dentofacial functional abnormalities
        • M26.50 Dentofacial functional abnormalities, unspeci...
        • M26.51 Abnormal jaw closure
        • M26.52 Limited mandibular range of motion
        • M26.53 Deviation in opening and closing of the mandi...
        • M26.54 Insufficient anterior guidance
        • M26.55 Centric occlusion maximum intercuspation disc...
        • M26.56 Non-working side interference
        • M26.57 Lack of posterior occlusal support
        • M26.59 Other dentofacial functional abnormalities
      • M26.6 Temporomandibular joint disorders
        • M26.60 Temporomandibular joint disorder, unspecified...
          • M26.601 Right temporomandibular joint disorder, unspe...
          • M26.602 Left temporomandibular joint disorder, unspec...
          • M26.603 Bilateral temporomandibular joint disorder, u...
          • M26.609 Unspecified temporomandibular joint disorder,...
        • M26.61 Adhesions and ankylosis of temporomandibular ...
          • M26.611 Adhesions and ankylosis of right temporomandi...
          • M26.612 Adhesions and ankylosis of left temporomandib...
          • M26.613 Adhesions and ankylosis of bilateral temporom...
          • M26.619 Adhesions and ankylosis of temporomandibular ...
        • M26.62 Arthralgia of temporomandibular joint
          • M26.621 Arthralgia of right temporomandibular joint
          • M26.622 Arthralgia of left temporomandibular joint
          • M26.623 Arthralgia of bilateral temporomandibular joi...
          • M26.629 Arthralgia of temporomandibular joint, unspec...
        • M26.63 Articular disc disorder of temporomandibular ...
          • M26.631 Articular disc disorder of right temporomandi...
          • M26.632 Articular disc disorder of left temporomandib...
          • M26.633 Articular disc disorder of bilateral temporom...
          • M26.639 Articular disc disorder of temporomandibular ...
        • M26.64 Arthritis of temporomandibular joint
          • M26.641 Arthritis of right temporomandibular joint
          • M26.642 Arthritis of left temporomandibular joint
          • M26.643 Arthritis of bilateral temporomandibular join...
          • M26.649 Arthritis of unspecified temporomandibular jo...
        • M26.65 Arthropathy of temporomandibular joint
          • M26.651 Arthropathy of right temporomandibular joint
          • M26.652 Arthropathy of left temporomandibular joint
          • M26.653 Arthropathy of bilateral temporomandibular jo...
          • M26.659 Arthropathy of unspecified temporomandibular ...
        • M26.69 Other specified disorders of temporomandibula...
      • M26.7 Dental alveolar anomalies
        • M26.70 Unspecified alveolar anomaly
        • M26.71 Alveolar maxillary hyperplasia
        • M26.72 Alveolar mandibular hyperplasia
        • M26.73 Alveolar maxillary hypoplasia
        • M26.74 Alveolar mandibular hypoplasia
        • M26.79 Other specified alveolar anomalies
      • M26.8 Other dentofacial anomalies
        • M26.81 Anterior soft tissue impingement
        • M26.82 Posterior soft tissue impingement
        • M26.89 Other dentofacial anomalies
      • M26.9 Dentofacial anomaly, unspecified
  • musculoskeletal deformities of head and face (
    ICD-10-CM Diagnosis Code Q67.0

    Congenital facial asymmetry

      2016 2017 2018 2019 2020 2021 Billable/Specific Code POA Exempt
    ICD-10-CM Diagnosis Code Q67.4

    Other congenital deformities of skull, face and jaw

      2016 2017 2018 2019 2020 2021 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital depressions in skull
    • Congenital hemifacial atrophy or hypertrophy
    • Deviation of nasal septum, congenital
    • Squashed or bent nose, congenital
    Type 1 Excludes
    • dentofacial anomalies [including malocclusion] (M26.-)
    • syphilitic saddle nose (A50.5)
  • skull defects associated with congenital anomalies of brain such as:
  • anencephaly (
    ICD-10-CM Diagnosis Code Q00.0


      2016 2017 2018 2019 2020 2021 Billable/Specific Code POA Exempt
    Applicable To
    • Acephaly
    • Acrania
    • Amyelencephaly
    • Hemianencephaly
    • Hemicephaly
  • encephalocele (
    ICD-10-CM Diagnosis Code Q01
    • Q01 Encephalocele
      • Q01.0 Frontal encephalocele
      • Q01.1 Nasofrontal encephalocele
      • Q01.2 Occipital encephalocele
      • Q01.8 Encephalocele of other sites
      • Q01.9 Encephalocele, unspecified
  • hydrocephalus (
    ICD-10-CM Diagnosis Code Q03
    • Q03 Congenital hydrocephalus
      • Q03.0 Malformations of aqueduct of Sylvius
      • Q03.1 Atresia of foramina of Magendie and Luschka
      • Q03.8 Other congenital hydrocephalus
      • Q03.9 Congenital hydrocephalus, unspecified
  • microcephaly (
    ICD-10-CM Diagnosis Code Q02


      2016 2017 2018 2019 2020 2021 Billable/Specific Code POA Exempt
    Code First
    • , if applicable, congenital Zika virus disease
    • hydromicrocephaly
    • micrencephalon
    Type 1 Excludes
    • Meckel-Gruber syndrome (Q61.9)
The following code(s) above Q75 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q75:
  • Q00-Q99
    2021 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
Code annotations containing back-references to Q75:
  • Type 1 Excludes: Q18
    ICD-10-CM Diagnosis Code Q18

    Other congenital malformations of face and neck

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • cleft lip and cleft palate (Q35-Q37)
    • conditions classified to Q67.0-Q67.4
    • congenital malformations of skull and face bones (Q75.-)
    • cyclopia (Q87.0)
    • dentofacial anomalies [including malocclusion] (M26.-)
    • malformation syndromes affecting facial appearance (Q87.0)
    • persistent thyroglossal duct (Q89.2)
ICD-10-CM Codes Adjacent To Q75
Q73.0 Congenital absence of unspecified limb(s)
Q73.1 Phocomelia, unspecified limb(s)
Q73.8 Other reduction defects of unspecified limb(s)
Q74 Other congenital malformations of limb(s)
Q74.0 Other congenital malformations of upper limb(s), including shoulder girdle
Q74.1 Congenital malformation of knee
Q74.2 Other congenital malformations of lower limb(s), including pelvic girdle
Q74.3 Arthrogryposis multiplex congenita
Q74.8 Other specified congenital malformations of limb(s)
Q74.9 Unspecified congenital malformation of limb(s)
Q75 Other congenital malformations of skull and face bones
Q75.0 Craniosynostosis
Q75.1 Craniofacial dysostosis
Q75.2 Hypertelorism
Q75.3 Macrocephaly
Q75.4 Mandibulofacial dysostosis
Q75.5 Oculomandibular dysostosis
Q75.8 Other specified congenital malformations of skull and face bones
Q75.9 Congenital malformation of skull and face bones, unspecified
Q76 Congenital malformations of spine and bony thorax
Q76.0 Spina bifida occulta

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.