2019 ICD-10-CM Diagnosis Code Q76.1

Klippel-Feil syndrome

    2016 2017 2018 2019 Billable/Specific Code POA Exempt
  • Q76.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM Q76.1 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of Q76.1 - other international versions of ICD-10 Q76.1 may differ.
Applicable To
  • Cervical fusion syndrome
The following code(s) above Q76.1 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q76.1:
  • Q00-Q99
    2019 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q76
    ICD-10-CM Diagnosis Code Q76

    Congenital malformations of spine and bony thorax

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • congenital musculoskeletal deformities of spine and chest (Q67.5-Q67.8)
    Congenital malformations of spine and bony thorax
Approximate Synonyms
  • Klippel feil sequence
  • Thoracolumbar kissing spine
Clinical Information
  • A condition characterized by shortness of the neck resulting from reduction in the number of vertebrae or the fusion of multiple hemivertebrae into one osseous mass. The hairline is low and the motion of the neck is limited. (Dorland, 27th ed)
  • A rare congenital syndrome characterized by the fusion of the vertebrae in the cervical spine. Patients present with a short neck and restricted mobility of the upper spine. Other signs and symptoms include scoliosis, spina bifida, cleft palate, and rib malformations.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q76.1 is considered exempt from POA reporting.
ICD-10-CM Q76.1 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 564 Other musculoskeletal system and connective tissue diagnoses with mcc
  • 565 Other musculoskeletal system and connective tissue diagnoses with cc
  • 566 Other musculoskeletal system and connective tissue diagnoses without cc/mcc

Convert Q76.1 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
Code annotations containing back-references to Q76.1:
  • Type 1 Excludes: M43
    ICD-10-CM Diagnosis Code M43

    Other deforming dorsopathies

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • congenital spondylolysis and spondylolisthesis (Q76.2)
    • hemivertebra (Q76.3-Q76.4)
    • Klippel-Feil syndrome (Q76.1)
    • lumbarization and sacralization (Q76.4)
    • platyspondylisis (Q76.4)
    • spina bifida occulta (Q76.0)
    • spinal curvature in osteoporosis (M80.-)
    • spinal curvature in Paget's disease of bone [osteitis deformans] (M88.-)

Diagnosis Index entries containing back-references to Q76.1:
  • Anomaly, anomalous (congenital) (unspecified type) Q89.9
    ICD-10-CM Diagnosis Code Q89.9

    Congenital malformation, unspecified

      2016 2017 2018 2019 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital anomaly NOS
    • Congenital deformity NOS
    • Klippel-Feil Q76.1 (brevicollis)
  • Cervical - see also condition
    • fusion syndrome Q76.1
  • Deformity Q89.9
    ICD-10-CM Diagnosis Code Q89.9

    Congenital malformation, unspecified

      2016 2017 2018 2019 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital anomaly NOS
    • Congenital deformity NOS
    • Klippel-Feil Q76.1 (brevicollis)
  • Disease, diseased - see also Syndrome
    • Klippel-Feil Q76.1 (brevicollis)
  • Feil-Klippel syndrome Q76.1 (brevicollis)
  • Klippel-Feil deficiency, disease, or syndrome Q76.1 (brevicollis)
  • Syndrome - see also Disease
    • cervical (root) M53.1
      ICD-10-CM Diagnosis Code M53.1

      Cervicobrachial syndrome

        2016 2017 2018 2019 Billable/Specific Code
      Type 2 Excludes
      • cervical disc disorder (M50.-)
      • thoracic outlet syndrome (G54.0)
      • fusion Q76.1
    • Feil-Klippel Q76.1 (brevicollis)
    • Klippel-Feil Q76.1 (brevicollis)

ICD-10-CM Codes Adjacent To Q76.1
Q75.0 Craniosynostosis
Q75.1 Craniofacial dysostosis
Q75.2 Hypertelorism
Q75.3 Macrocephaly
Q75.4 Mandibulofacial dysostosis
Q75.5 Oculomandibular dysostosis
Q75.8 Other specified congenital malformations of skull and face bones
Q75.9 Congenital malformation of skull and face bones, unspecified
Q76 Congenital malformations of spine and bony thorax
Q76.0 Spina bifida occulta
Q76.1 Klippel-Feil syndrome
Q76.2 Congenital spondylolisthesis
Q76.3 Congenital scoliosis due to congenital bony malformation
Q76.4 Other congenital malformations of spine, not associated with scoliosis
Q76.41 Congenital kyphosis
Q76.411 …… occipito-atlanto-axial region
Q76.412 …… cervical region
Q76.413 …… cervicothoracic region
Q76.414 …… thoracic region
Q76.415 …… thoracolumbar region
Q76.419 …… unspecified region

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.