ICD-10-CM Codes
Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities
Q65-Q79 Congenital malformations and deformations of the musculoskeletal system
Q76- Congenital malformations of spine and bony thorax
2022 ICD-10-CM Diagnosis Code Q76.1

2022 ICD-10-CM Diagnosis Code Q76.1

Klippel-Feil syndrome

2016

2017

2018

2019

2020

2021

2022

Billable/Specific Code

POA Exempt

Q76.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2022 edition of ICD-10-CM Q76.1 became effective on October 1, 2021.
This is the American ICD-10-CM version of Q76.1 - other international versions of ICD-10 Q76.1 may differ.

Applicable To

Cervical fusion syndrome

The following code(s) above Q76.1 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to Q76.1:

Q00-Q99
2022 ICD-10-CM Range Q00-Q99
Congenital malformations, deformations and chromosomal abnormalities
Note
- Codes from this chapter are not for use on maternal records
Type 2 Excludes
- inborn errors of metabolism (E70-E88)
Congenital malformations, deformations and chromosomal abnormalities
Q76
ICD-10-CM Diagnosis Code Q76
Congenital malformations of spine and bony thorax
Type 1 Excludes
- congenital musculoskeletal deformities of spine and chest (Q67.5-Q67.8)
Congenital malformations of spine and bony thorax

Approximate Synonyms

Klippel feil sequence
Thoracolumbar kissing spine

Clinical Information

A condition characterized by shortness of the neck resulting from reduction in the number of vertebrae or the fusion of multiple hemivertebrae into one osseous mass. The hairline is low and the motion of the neck is limited. (Dorland, 27th ed)
A rare congenital syndrome characterized by the fusion of the vertebrae in the cervical spine. Patients present with a short neck and restricted mobility of the upper spine. Other signs and symptoms include scoliosis, spina bifida, cleft palate, and rib malformations.

Present On Admission

POA Help

"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.

Q76.1 is considered exempt from POA reporting.

ICD-10-CM Q76.1 is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):

564 Other musculoskeletal system and connective tissue diagnoses with mcc
565 Other musculoskeletal system and connective tissue diagnoses with cc
566 Other musculoskeletal system and connective tissue diagnoses without cc/mcc

Convert Q76.1 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change
2022 (effective 10/1/2021): No change

Code annotations containing back-references to Q76.1:

Type 1 Excludes: M43

ICD-10-CM Diagnosis Code M43
Other deforming dorsopathies
Type 1 Excludes
- congenital spondylolysis and spondylolisthesis (Q76.2)
- hemivertebra (Q76.3-Q76.4)
- Klippel-Feil syndrome (Q76.1)
- lumbarization and sacralization (Q76.4)
- platyspondylisis (Q76.4)
- spina bifida occulta (Q76.0)
- spinal curvature in osteoporosis (M80.-)
- spinal curvature in Paget's disease of bone [osteitis deformans] (M88.-)

Diagnosis Index entries containing back-references to Q76.1:

Anomaly, anomalous (congenital) (unspecified type) Q89.9
ICD-10-CM Diagnosis Code Q89.9
Congenital malformation, unspecified
Applicable To
Congenital anomaly NOS
Congenital deformity NOS
- Klippel-Feil Q76.1 (brevicollis)
Cervical - see also condition
- fusion syndrome Q76.1
Deformity Q89.9
ICD-10-CM Diagnosis Code Q89.9
Congenital malformation, unspecified
Applicable To
Congenital anomaly NOS
Congenital deformity NOS
- Klippel-Feil Q76.1 (brevicollis)
Disease, diseased - see also Syndrome
- Klippel-Feil Q76.1 (brevicollis)
Feil-Klippel syndrome Q76.1 (brevicollis)
Klippel-Feil deficiency, disease, or syndrome Q76.1 (brevicollis)
Syndrome - see also Disease
- cervical (root) M53.1
  ICD-10-CM Diagnosis Code M53.1
  Cervicobrachial syndrome
  2016 2017 2018 2019 2020 2021 2022 Billable/Specific Code
  Type 2 Excludes
  cervical disc disorder (M50.-)
  thoracic outlet syndrome (G54.0)
  - fusion Q76.1
- Feil-Klippel Q76.1 (brevicollis)
- Klippel-Feil Q76.1 (brevicollis)

ICD-10-CM Codes Adjacent To Q76.1

Q75.0 Craniosynostosis

Q75.1 Craniofacial dysostosis

Q75.2 Hypertelorism

Q75.3 Macrocephaly

Q75.4 Mandibulofacial dysostosis

Q75.5 Oculomandibular dysostosis

Q75.8 Other specified congenital malformations of skull and face bones

Q75.9 Congenital malformation of skull and face bones, unspecified

Q76 Congenital malformations of spine and bony thorax

Q76.0 Spina bifida occulta

Q76.1 Klippel-Feil syndrome

Q76.2 Congenital spondylolisthesis

Q76.3 Congenital scoliosis due to congenital bony malformation

Q76.4 Other congenital malformations of spine, not associated with scoliosis

Q76.41 Congenital kyphosis

Q76.411 …… occipito-atlanto-axial region

Q76.412 …… cervical region

Q76.413 …… cervicothoracic region

Q76.414 …… thoracic region

Q76.415 …… thoracolumbar region

Q76.419 …… unspecified region

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2022 ICD-10-CM Diagnosis Code Q76.1

Klippel-Feil syndrome

Congenital malformations, deformations and chromosomal abnormalities

Congenital malformations of spine and bony thorax

Other deforming dorsopathies

Congenital malformation, unspecified

Congenital malformation, unspecified

Cervicobrachial syndrome