2020 ICD-10-CM Diagnosis Code Q77.6

Chondroectodermal dysplasia

    2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
  • Q77.6 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM Q77.6 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of Q77.6 - other international versions of ICD-10 Q77.6 may differ.
Applicable To
  • Ellis-van Creveld syndrome
The following code(s) above Q77.6 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q77.6:
  • Q00-Q99
    2020 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q77
    ICD-10-CM Diagnosis Code Q77

    Osteochondrodysplasia with defects of growth of tubular bones and spine

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Type 2 Excludes
    • congenital myotonic chondrodystrophy (G71.13)
    Osteochondrodysplasia with defects of growth of tubular bones and spine
Clinical Information
  • A rare autosomal recessive syndrome caused by mutations in the evc gene. It is characterized by dwarfism, small chest, ectodermal dysplasia, and postaxial polydactyly. There is an increased frequency of congenital heart malformations.
  • Chondrodysplasia of long bones affecting mainly the distal ends of extremities and resulting in short-limb dwarfism, hexadactyly of the fingers and less frequently the toes; ectodermal dysplasia with nail and hair abnormalities, and congenital heart defects. Associated abnormalities may include cryptorchidism, epispadias, talipes equinovalgus, and dandy-walker syndrome (absence of cerebellar vermis, hydrocephalus, and posterior fossa cyst continuous with the fourth ventricle). Some patients are retarded. The largest pedigree was observed in old order amish in lancaster county, pennsylvania and some cases were reported in australian aborigines.
  • Dwarfism occurring in association with defective development of skin, hair, and teeth, polydactyly, and defect of the cardiac septum. (Dorland, 27th ed)
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q77.6 is considered exempt from POA reporting.
ICD-10-CM Q77.6 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 564 Other musculoskeletal system and connective tissue diagnoses with mcc
  • 565 Other musculoskeletal system and connective tissue diagnoses with cc
  • 566 Other musculoskeletal system and connective tissue diagnoses without cc/mcc

Convert Q77.6 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to Q77.6:
  • Type 1 Excludes: Q87.1
    , Q82.4
    ICD-10-CM Diagnosis Code Q87.1

    Congenital malformation syndromes predominantly associated with short stature

      2016 2017 2018 2019 2020 - Converted to Parent Code Non-Billable/Non-Specific Code
    Type 1 Excludes
    • Ellis-van Creveld syndrome (Q77.6)
    • Smith-Lemli-Opitz syndrome (E78.72)
    ICD-10-CM Diagnosis Code Q82.4

    Ectodermal dysplasia (anhidrotic)

      2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    Type 1 Excludes
    • Ellis-van Creveld syndrome (Q77.6)

Diagnosis Index entries containing back-references to Q77.6:
  • Chondroectodermal dysplasia Q77.6
  • Disease, diseased - see also Syndrome
    • Ellis-van Creveld Q77.6 (chondroectodermal dysplasia)
  • Dysplasia - see also Anomaly
    • chondroectodermal Q77.6
  • Ellis-van Creveld syndrome Q77.6 (chondroectodermal dysplasia)
  • Syndrome - see also Disease
    • chondroectodermal dysplasia Q77.6
    • Ellis-van Creveld Q77.6

ICD-10-CM Codes Adjacent To Q77.6
Q76.7 Congenital malformation of sternum
Q76.8 Other congenital malformations of bony thorax
Q76.9 Congenital malformation of bony thorax, unspecified
Q77 Osteochondrodysplasia with defects of growth of tubular bones and spine
Q77.0 Achondrogenesis
Q77.1 Thanatophoric short stature
Q77.2 Short rib syndrome
Q77.3 Chondrodysplasia punctata
Q77.4 Achondroplasia
Q77.5 Diastrophic dysplasia
Q77.6 Chondroectodermal dysplasia
Q77.7 Spondyloepiphyseal dysplasia
Q77.8 Other osteochondrodysplasia with defects of growth of tubular bones and spine
Q77.9 Osteochondrodysplasia with defects of growth of tubular bones and spine, unspecified
Q78 Other osteochondrodysplasias
Q78.0 Osteogenesis imperfecta
Q78.1 Polyostotic fibrous dysplasia
Q78.2 Osteopetrosis
Q78.3 Progressive diaphyseal dysplasia
Q78.4 Enchondromatosis
Q78.5 Metaphyseal dysplasia

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.