2023 ICD-10-CM Diagnosis Code Q80.1

X-linked ichthyosis

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • Q80.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2023 edition of ICD-10-CM Q80.1 became effective on October 1, 2022.
  • This is the American ICD-10-CM version of Q80.1 - other international versions of ICD-10 Q80.1 may differ.
The following code(s) above Q80.1 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q80.1:
  • Q00-Q99
    2023 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q80
    ICD-10-CM Diagnosis Code Q80

    Congenital ichthyosis

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Congenital ichthyosis
Approximate Synonyms
  • Placental sulfatase deficiency
Clinical Information
  • Chronic form of ichthyosis that is inherited as a sex-linked recessive trait carried on the x-chromosome and transmitted to the male offspring. It is characterized by severe scaling, especially on the extremities, and is associated with steroid sulfatase deficiency.
  • Sex linked inherited disease characterized by excessive scaling
  • The second most common form of ichthyosis. It is an x-linked inherited disorder with mild skin manifestations. The skin changes appear at birth and include keratinization and scaling.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q80.1 is considered exempt from POA reporting.
ICD-10-CM Q80.1 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):
  • 606 Minor skin disorders with mcc
  • 607 Minor skin disorders without mcc

Convert Q80.1 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change

Diagnosis Index entries containing back-references to Q80.1:
  • Ichthyosis (congenital) Q80.9
    ICD-10-CM Diagnosis Code Q80.9

    Congenital ichthyosis, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    • X-linked Q80.1

ICD-10-CM Codes Adjacent To Q80.1
Q79.6 Ehlers-Danlos syndromes
Q79.60 Ehlers-Danlos syndrome, unspecified
Q79.61 Classical Ehlers-Danlos syndrome
Q79.62 Hypermobile Ehlers-Danlos syndrome
Q79.63 Vascular Ehlers-Danlos syndrome
Q79.69 Other Ehlers-Danlos syndromes
Q79.8 Other congenital malformations of musculoskeletal system
Q79.9 Congenital malformation of musculoskeletal system, unspecified
Q80 Congenital ichthyosis
Q80.0 Ichthyosis vulgaris
Q80.1 X-linked ichthyosis
Q80.2 Lamellar ichthyosis
Q80.3 Congenital bullous ichthyosiform erythroderma
Q80.4 Harlequin fetus
Q80.8 Other congenital ichthyosis
Q80.9 Congenital ichthyosis, unspecified
Q81 Epidermolysis bullosa
Q81.0 Epidermolysis bullosa simplex
Q81.1 Epidermolysis bullosa letalis
Q81.2 Epidermolysis bullosa dystrophica
Q81.8 Other epidermolysis bullosa

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.