2020 ICD-10-CM Diagnosis Code Q81.0

Epidermolysis bullosa simplex

    2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
  • Q81.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM Q81.0 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of Q81.0 - other international versions of ICD-10 Q81.0 may differ.
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q81.0. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Cockayne's syndrome (
    ICD-10-CM Diagnosis Code Q87.19

    Other congenital malformation syndromes predominantly associated with short stature

      2020 - New Code Billable/Specific Code POA Exempt
    Applicable To
    • Aarskog syndrome
    • Cockayne syndrome
    • De Lange syndrome
    • Dubowitz syndrome
    • Noonan syndrome
    • Robinow-Silverman-Smith syndrome
    • Russell-Silver syndrome
    • Seckel syndrome
    Q87.19
    )
The following code(s) above Q81.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q81.0:
  • Q00-Q99
    2020 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
Clinical Information
  • A form of epidermolysis bullosa characterized by serous bullae that heal without scarring. Mutations in the genes that encode keratin-5 and keratin-14 have been associated with several subtypes of epidermolysis bullosa simplex.
  • A genetic skin disorder caused by mutations in the krt5 and krt14 genes. It is characterized by the formation of blisters and increased fragility of the skin.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q81.0 is considered exempt from POA reporting.
ICD-10-CM Q81.0 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 606 Minor skin disorders with mcc
  • 607 Minor skin disorders without mcc
  • 795 Normal newborn

Convert Q81.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to Q81.0:
  • Epidermolysis
    • bullosa (congenital) Q81.9
      ICD-10-CM Diagnosis Code Q81.9

      Epidermolysis bullosa, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • simplex Q81.0

ICD-10-CM Codes Adjacent To Q81.0
Q79.9 Congenital malformation of musculoskeletal system, unspecified
Q80 Congenital ichthyosis
Q80.0 Ichthyosis vulgaris
Q80.1 X-linked ichthyosis
Q80.2 Lamellar ichthyosis
Q80.3 Congenital bullous ichthyosiform erythroderma
Q80.4 Harlequin fetus
Q80.8 Other congenital ichthyosis
Q80.9 Congenital ichthyosis, unspecified
Q81 Epidermolysis bullosa
Q81.0 Epidermolysis bullosa simplex
Q81.1 Epidermolysis bullosa letalis
Q81.2 Epidermolysis bullosa dystrophica
Q81.8 Other epidermolysis bullosa
Q81.9 Epidermolysis bullosa, unspecified
Q82 Other congenital malformations of skin
Q82.0 Hereditary lymphedema
Q82.1 Xeroderma pigmentosum
Q82.2 Congenital cutaneous mastocytosis
Q82.3 Incontinentia pigmenti
Q82.4 Ectodermal dysplasia (anhidrotic)

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.