2021 ICD-10-CM Diagnosis Code Q82.0

Hereditary lymphedema

    2016 2017 2018 2019 2020 2021 Billable/Specific Code POA Exempt
  • Q82.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2021 edition of ICD-10-CM Q82.0 became effective on October 1, 2020.
  • This is the American ICD-10-CM version of Q82.0 - other international versions of ICD-10 Q82.0 may differ.
The following code(s) above Q82.0 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q82.0:
  • Q00-Q99
    2021 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q82
    ICD-10-CM Diagnosis Code Q82

    Other congenital malformations of skin

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • acrodermatitis enteropathica (E83.2)
    • congenital erythropoietic porphyria (E80.0)
    • pilonidal cyst or sinus (L05.-)
    • Sturge-Weber (-Dimitri) syndrome (Q85.8)
    Other congenital malformations of skin
Approximate Synonyms
  • Hereditary edema of leg
  • Hereditary edema of legs
  • Hereditary lymphedema type i
  • Meige syndrome
  • Primary congenital lymphedema
Clinical Information
  • A congenital condition that results in swelling in the arms or legs, and can occur during adolescence or adulthood. Loss of motion and pain may also accompany the swelling. Protein-rich lymphatic fluid accumulates in tissues, engorging and enlarging vessels and often causing visible swelling, tenderness, and pain. Left untreated, the affected tissues may continue to swell, and can become hardened or fibrotic and susceptible to infection.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q82.0 is considered exempt from POA reporting.
ICD-10-CM Q82.0 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
  • 606 Minor skin disorders with mcc
  • 607 Minor skin disorders without mcc

Convert Q82.0 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
Code annotations containing back-references to Q82.0:
  • Type 1 Excludes: I89
    , R60
    ICD-10-CM Diagnosis Code I89

    Other noninfective disorders of lymphatic vessels and lymph nodes

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • chylocele, tunica vaginalis (nonfilarial) NOS (N50.89)
    • enlarged lymph nodes NOS (R59.-)
    • filarial chylocele (B74.-)
    • hereditary lymphedema (Q82.0)
    ICD-10-CM Diagnosis Code R60

    Edema, not elsewhere classified

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes

Diagnosis Index entries containing back-references to Q82.0:
  • Disease, diseased - see also Syndrome
    • Meige's Q82.0 (chronic hereditary edema)
    • Milroy's Q82.0 (chronic hereditary edema)
    • Nonne-Milroy-Meige Q82.0 (chronic hereditary edema)
  • Edema, edematous (infectious) (pitting) (toxic) R60.9
    ICD-10-CM Diagnosis Code R60.9

    Edema, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Fluid retention NOS
    • legs R60.0
      ICD-10-CM Diagnosis Code R60.0

      Localized edema

        2016 2017 2018 2019 2020 2021 Billable/Specific Code
      • hereditary Q82.0
    • chronic hereditary Q82.0
    • familial, hereditary Q82.0
    • hereditary Q82.0
    • Milroy's Q82.0
  • Elephantiasis (nonfilarial) I89.0
    ICD-10-CM Diagnosis Code I89.0

    Lymphedema, not elsewhere classified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Elephantiasis (nonfilarial) NOS
    • Lymphangiectasis
    • Obliteration, lymphatic vessel
    • Praecox lymphedema
    • Secondary lymphedema
    Type 1 Excludes
    • postmastectomy lymphedema (I97.2)
    • congenital Q82.0 (any site) (hereditary)
  • Lymphedema (acquired) - see also Elephantiasis
    • congenital Q82.0
    • hereditary Q82.0 (chronic) (idiopathic)
  • Meige-Milroy disease Q82.0 (chronic hereditary edema)
  • Meige's syndrome Q82.0
  • Milroy's disease Q82.0 (chronic hereditary edema)
  • Nonne-Milroy syndrome Q82.0
  • Pseudoelephantiasis neuroarthritica Q82.0
  • Syndrome - see also Disease
    • Nonne-Milroy-Meige Q82.0
  • Trophedema Q82.0 (congenital) (hereditary)
  • Tropholymphedema Q82.0

ICD-10-CM Codes Adjacent To Q82.0
Q80.4 Harlequin fetus
Q80.8 Other congenital ichthyosis
Q80.9 Congenital ichthyosis, unspecified
Q81 Epidermolysis bullosa
Q81.0 Epidermolysis bullosa simplex
Q81.1 Epidermolysis bullosa letalis
Q81.2 Epidermolysis bullosa dystrophica
Q81.8 Other epidermolysis bullosa
Q81.9 Epidermolysis bullosa, unspecified
Q82 Other congenital malformations of skin
Q82.0 Hereditary lymphedema
Q82.1 Xeroderma pigmentosum
Q82.2 Congenital cutaneous mastocytosis
Q82.3 Incontinentia pigmenti
Q82.4 Ectodermal dysplasia (anhidrotic)
Q82.5 Congenital non-neoplastic nevus
Q82.6 Congenital sacral dimple
Q82.8 Other specified congenital malformations of skin
Q82.9 Congenital malformation of skin, unspecified
Q83 Congenital malformations of breast
Q83.0 Congenital absence of breast with absent nipple

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.