ICD-10-CM Codes
Q00-Q99
Q80-Q89
Q82-
2023 ICD-10-CM Diagnosis Code Q82.2

2023 ICD-10-CM Diagnosis Code Q82.2

Congenital cutaneous mastocytosis

2016

2017

2018 - Revised Code

2019

2020

2021

2022

2023

Billable/Specific Code

POA Exempt

Q82.2 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2023 edition of ICD-10-CM Q82.2 became effective on October 1, 2022.
This is the American ICD-10-CM version of Q82.2 - other international versions of ICD-10 Q82.2 may differ.

Applicable To

Congenital diffuse cutaneous mastocytosis
Congenital maculopapular cutaneous mastocytosis
Congenital urticaria pigmentosa

Type 1 Excludes

Type 1 Excludes Help

A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q82.2. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

cutaneous mastocytosis NOS (
ICD-10-CM Diagnosis Code D47.01
Cutaneous mastocytosis
Applicable To
- Diffuse cutaneous mastocytosis
- Maculopapular cutaneous mastocytosis
- Solitary mastocytoma
- Telangiectasia macularis eruptiva perstans
- Urticaria pigmentosa
Type 1 Excludes
- congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
- congenital urticaria pigmentosa (Q82.2)
- extracutaneous mastocytoma (D47.09)
D47.01
)
diffuse cutaneous mastocytosis (with onset after newborn period) (
ICD-10-CM Diagnosis Code D47.01
Cutaneous mastocytosis
Applicable To
- Diffuse cutaneous mastocytosis
- Maculopapular cutaneous mastocytosis
- Solitary mastocytoma
- Telangiectasia macularis eruptiva perstans
- Urticaria pigmentosa
Type 1 Excludes
- congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
- congenital urticaria pigmentosa (Q82.2)
- extracutaneous mastocytoma (D47.09)
D47.01
)
malignant mastocytosis (
ICD-10-CM Diagnosis Code C96.2
Malignant mast cell neoplasm
Type 1 Excludes
- indolent mastocytosis (D47.02)
- mast cell leukemia (C94.30)
- mastocytosis (congenital) (cutaneous) (Q82.2)
C96.2-
)
systemic mastocytosis (
ICD-10-CM Diagnosis Code D47.02
Systemic mastocytosis
Applicable To
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia (C92.6-, C92.A-)
- chronic myelomonocytic leukemia (C93.1-)
- essential thrombocytosis (D47.3)
- hypereosinophilic syndrome (D72.1)
- myelodysplastic syndrome (D46.9)
- myeloproliferative syndrome (D47.1)
- non-Hodgkin lymphoma (C82-C85)
- plasma cell myeloma (C90.0-)
- polycythemia vera (D45)
Type 1 Excludes
- aggressive systemic mastocytosis (C96.21)
- mast cell leukemia (C94.3-)
D47.02
)
urticaria pigmentosa (non-congenital) (with onset after newborn period) (
ICD-10-CM Diagnosis Code D47.01
Cutaneous mastocytosis
Applicable To
- Diffuse cutaneous mastocytosis
- Maculopapular cutaneous mastocytosis
- Solitary mastocytoma
- Telangiectasia macularis eruptiva perstans
- Urticaria pigmentosa
Type 1 Excludes
- congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
- congenital urticaria pigmentosa (Q82.2)
- extracutaneous mastocytoma (D47.09)
D47.01
)

The following code(s) above Q82.2 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to Q82.2:

Q00-Q99
2023 ICD-10-CM Range Q00-Q99
Congenital malformations, deformations and chromosomal abnormalities
Note
- Codes from this chapter are not for use on maternal records
Type 2 Excludes
- inborn errors of metabolism (E70-E88)
Congenital malformations, deformations and chromosomal abnormalities
Q82
ICD-10-CM Diagnosis Code Q82
Other congenital malformations of skin
Type 1 Excludes
- acrodermatitis enteropathica (E83.2)
- congenital erythropoietic porphyria (E80.0)
- pilonidal cyst or sinus (L05.-)
- Sturge-Weber (-Dimitri) syndrome (Q85.89)
Other congenital malformations of skin

Approximate Synonyms

Urticaria pigmentosa

Clinical Information

A clonal myeloproliferative neoplasm characterized by the proliferation and accumulation of neoplastic mast cells in one or multiple organs or organ systems. It is a heterogeneous group of neoplasms, ranging from cutaneous proliferations which may regress spontaneously, to aggressive neoplasms associated with organ failure and short survival.
A heterogenous group of disorders characterized by the abnormal increase of mast cells in only the skin (mastocytosis, cutaneous), in extracutaneous tissues involving multiple organs (mastocytosis, systemic), or in solid tumors (mastocytoma).
Most common form of mastocytosis, characterized by multiple persistant small reddish brown hyperpigmented pruritic macules and papules.
Rare disease characterized by an abnormal increase in mast cells in the bone marrow, liver, spleen, lymph nodes, gastrointestinal tract, and skin.
The most common form of cutaneous mastocytosis (mastocytosis, cutaneous) that occurs primarily in children. It is characterized by the multiple small reddish-brown pigmented pruritic macules and papules.
The most frequent form of cutaneous mastocytosis. In children, the lesions tend to be papular, and are characterized by aggregates of elongated or spindle-shaped mast cells which fill the papillary dermis and extend into the reticular dermis. In adults, the lesions tend to have fewer mast cells compared to those in children. The lesions are located most commonly on the trunk, but they can be seen on the extremities, head and neck. (who, 2001)

Present On Admission

POA Help

"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.

Q82.2 is considered exempt from POA reporting.

ICD-10-CM Q82.2 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):

606 Minor skin disorders with mcc
607 Minor skin disorders without mcc
795 Normal newborn

Convert Q82.2 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): Revised code
- New description: Congenital cutaneous mastocytosis
- 2017 description: Mastocytosis
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change
2022 (effective 10/1/2021): No change
2023 (effective 10/1/2022): No change

Code annotations containing back-references to Q82.2:

Type 1 Excludes: D47.0
, D47.01
, D47.01
, D89.4
, C96.2

ICD-10-CM Diagnosis Code D47.0
Mast cell neoplasms of uncertain behavior
Type 1 Excludes
- congenital cutaneous mastocytosis (Q82.2)
- histiocytic neoplasms of uncertain behavior (D47.Z9)
- malignant mast cell neoplasm (C96.2-)
ICD-10-CM Diagnosis Code D47.01
Cutaneous mastocytosis
Applicable To
- Diffuse cutaneous mastocytosis
- Maculopapular cutaneous mastocytosis
- Solitary mastocytoma
- Telangiectasia macularis eruptiva perstans
- Urticaria pigmentosa
Type 1 Excludes
- congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
- congenital urticaria pigmentosa (Q82.2)
- extracutaneous mastocytoma (D47.09)
ICD-10-CM Diagnosis Code D47.01
Cutaneous mastocytosis
Applicable To
- Diffuse cutaneous mastocytosis
- Maculopapular cutaneous mastocytosis
- Solitary mastocytoma
- Telangiectasia macularis eruptiva perstans
- Urticaria pigmentosa
Type 1 Excludes
- congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
- congenital urticaria pigmentosa (Q82.2)
- extracutaneous mastocytoma (D47.09)
ICD-10-CM Diagnosis Code D89.4
Mast cell activation syndrome and related disorders
Type 1 Excludes
- aggressive systemic mastocytosis (C96.21)
- congenital cutaneous mastocytosis (Q82.2)
- (non-congenital) cutaneous mastocytosis (D47.01)
- (indolent) systemic mastocytosis (D47.02)
- malignant mast cell neoplasm (C96.2-)
- malignant mastocytoma (C96.29)
- mast cell leukemia (C94.3-)
- mast cell sarcoma (C96.22)
- mastocytoma NOS (D47.09)
- other mast cell neoplasms of uncertain behavior (D47.09)
- systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)
ICD-10-CM Diagnosis Code C96.2
Malignant mast cell neoplasm
Type 1 Excludes
- indolent mastocytosis (D47.02)
- mast cell leukemia (C94.30)
- mastocytosis (congenital) (cutaneous) (Q82.2)

Diagnosis Index entries containing back-references to Q82.2:

Mastocytosis D47.09
ICD-10-CM Diagnosis Code D47.09
Other mast cell neoplasms of uncertain behavior
Applicable To
Extracutaneous mastocytoma
Mast cell tumor NOS
Mastocytoma NOS
Mastocytosis NOS
- cutaneous (diffuse) (maculopapular) D47.01
  ICD-10-CM Diagnosis Code D47.01
  Cutaneous mastocytosis
  2018 - New Code 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Diffuse cutaneous mastocytosis
  Maculopapular cutaneous mastocytosis
  Solitary mastocytoma
  Telangiectasia macularis eruptiva perstans
  Urticaria pigmentosa
  Type 1 Excludes
  congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
  congenital urticaria pigmentosa (Q82.2)
  extracutaneous mastocytoma (D47.09)
  - congenital Q82.2
  - of neonatal onset Q82.2
  - of newborn onset Q82.2
Urticaria L50.9
ICD-10-CM Diagnosis Code L50.9
Urticaria, unspecified
- pigmentosa D47.01
  ICD-10-CM Diagnosis Code D47.01
  Cutaneous mastocytosis
  2018 - New Code 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Diffuse cutaneous mastocytosis
  Maculopapular cutaneous mastocytosis
  Solitary mastocytoma
  Telangiectasia macularis eruptiva perstans
  Urticaria pigmentosa
  Type 1 Excludes
  congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
  congenital urticaria pigmentosa (Q82.2)
  extracutaneous mastocytoma (D47.09)
  - congenital Q82.2
  - of neonatal onset Q82.2
  - of newborn onset Q82.2

ICD-10-CM Codes Adjacent To Q82.2

Q80.9 Congenital ichthyosis, unspecified

Q81 Epidermolysis bullosa

Q81.0 Epidermolysis bullosa simplex

Q81.1 Epidermolysis bullosa letalis

Q81.2 Epidermolysis bullosa dystrophica

Q81.8 Other epidermolysis bullosa

Q81.9 Epidermolysis bullosa, unspecified

Q82 Other congenital malformations of skin

Q82.0 Hereditary lymphedema

Q82.1 Xeroderma pigmentosum

Q82.2 Congenital cutaneous mastocytosis

Q82.3 Incontinentia pigmenti

Q82.4 Ectodermal dysplasia (anhidrotic)

Q82.5 Congenital non-neoplastic nevus

Q82.6 Congenital sacral dimple

Q82.8 Other specified congenital malformations of skin

Q82.9 Congenital malformation of skin, unspecified

Q83 Congenital malformations of breast

Q83.0 Congenital absence of breast with absent nipple

Q83.1 Accessory breast

Q83.2 Absent nipple

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2023 ICD-10-CM Diagnosis Code Q82.2

Congenital cutaneous mastocytosis

Cutaneous mastocytosis

Cutaneous mastocytosis

Malignant mast cell neoplasm

Systemic mastocytosis

Cutaneous mastocytosis

Congenital malformations, deformations and chromosomal abnormalities

Other congenital malformations of skin

Mast cell neoplasms of uncertain behavior

Cutaneous mastocytosis

Cutaneous mastocytosis

Mast cell activation syndrome and related disorders

Malignant mast cell neoplasm

Other mast cell neoplasms of uncertain behavior

Cutaneous mastocytosis

Urticaria, unspecified

Cutaneous mastocytosis