2021 ICD-10-CM Diagnosis Code Q82.2

Congenital cutaneous mastocytosis

    2016 2017 2018 - Revised Code 2019 2020 2021 Billable/Specific Code POA Exempt
  • Q82.2 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2021 edition of ICD-10-CM Q82.2 became effective on October 1, 2020.
  • This is the American ICD-10-CM version of Q82.2 - other international versions of ICD-10 Q82.2 may differ.
Applicable To
  • Congenital diffuse cutaneous mastocytosis
  • Congenital maculopapular cutaneous mastocytosis
  • Congenital urticaria pigmentosa
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q82.2. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • cutaneous mastocytosis NOS (
    ICD-10-CM Diagnosis Code D47.01

    Cutaneous mastocytosis

      2018 - New Code 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Diffuse cutaneous mastocytosis
    • Maculopapular cutaneous mastocytosis
    • Solitary mastocytoma
    • Telangiectasia macularis eruptiva perstans
    • Urticaria pigmentosa
    Type 1 Excludes
    • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
    • congenital urticaria pigmentosa (Q82.2)
    • extracutaneous mastocytoma (D47.09)
    D47.01
    )
  • diffuse cutaneous mastocytosis (with onset after newborn period) (
    ICD-10-CM Diagnosis Code D47.01

    Cutaneous mastocytosis

      2018 - New Code 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Diffuse cutaneous mastocytosis
    • Maculopapular cutaneous mastocytosis
    • Solitary mastocytoma
    • Telangiectasia macularis eruptiva perstans
    • Urticaria pigmentosa
    Type 1 Excludes
    • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
    • congenital urticaria pigmentosa (Q82.2)
    • extracutaneous mastocytoma (D47.09)
    D47.01
    )
  • malignant mastocytosis (
    ICD-10-CM Diagnosis Code C96.2

    Malignant mast cell neoplasm

      2016 2017 2018 - Converted to Parent Code 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • indolent mastocytosis (D47.02)
    • mast cell leukemia (C94.30)
    • mastocytosis (congenital) (cutaneous) (Q82.2)
    C96.2-
    )
  • systemic mastocytosis (
    ICD-10-CM Diagnosis Code D47.02

    Systemic mastocytosis

      2018 - New Code 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Indolent systemic mastocytosis
    • Isolated bone marrow mastocytosis
    • Smoldering systemic mastocytosis
    • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
    Code Also
    • , if applicable, any associated hematological non-mast cell lineage disease, such as:
    • acute myeloid leukemia (C92.6-, C92.A-)
    • chronic myelomonocytic leukemia (C93.1-)
    • essential thrombocytosis (D47.3)
    • hypereosinophilic syndrome (D72.1)
    • myelodysplastic syndrome (D46.9)
    • myeloproliferative syndrome (D47.1)
    • non-Hodgkin lymphoma (C82-C85)
    • plasma cell myeloma (C90.0-)
    • polycythemia vera (D45)
    Type 1 Excludes
    • aggressive systemic mastocytosis (C96.21)
    • mast cell leukemia (C94.3-)
    D47.02
    )
  • urticaria pigmentosa (non-congenital) (with onset after newborn period) (
    ICD-10-CM Diagnosis Code D47.01

    Cutaneous mastocytosis

      2018 - New Code 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Diffuse cutaneous mastocytosis
    • Maculopapular cutaneous mastocytosis
    • Solitary mastocytoma
    • Telangiectasia macularis eruptiva perstans
    • Urticaria pigmentosa
    Type 1 Excludes
    • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
    • congenital urticaria pigmentosa (Q82.2)
    • extracutaneous mastocytoma (D47.09)
    D47.01
    )
The following code(s) above Q82.2 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q82.2:
  • Q00-Q99
    2021 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q82
    ICD-10-CM Diagnosis Code Q82

    Other congenital malformations of skin

      2016 2017 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • acrodermatitis enteropathica (E83.2)
    • congenital erythropoietic porphyria (E80.0)
    • pilonidal cyst or sinus (L05.-)
    • Sturge-Weber (-Dimitri) syndrome (Q85.8)
    Other congenital malformations of skin
Approximate Synonyms
  • Urticaria pigmentosa
Clinical Information
  • A clonal myeloproliferative neoplasm characterized by the proliferation and accumulation of neoplastic mast cells in one or multiple organs or organ systems. It is a heterogeneous group of neoplasms, ranging from cutaneous proliferations which may regress spontaneously, to aggressive neoplasms associated with organ failure and short survival.
  • A heterogenous group of disorders characterized by the abnormal increase of mast cells in only the skin (mastocytosis, cutaneous), in extracutaneous tissues involving multiple organs (mastocytosis, systemic), or in solid tumors (mastocytoma).
  • Most common form of mastocytosis, characterized by multiple persistant small reddish brown hyperpigmented pruritic macules and papules.
  • Rare disease characterized by an abnormal increase in mast cells in the bone marrow, liver, spleen, lymph nodes, gastrointestinal tract, and skin.
  • The most common form of cutaneous mastocytosis (mastocytosis, cutaneous) that occurs primarily in children. It is characterized by the multiple small reddish-brown pigmented pruritic macules and papules.
  • The most frequent form of cutaneous mastocytosis. In children, the lesions tend to be papular, and are characterized by aggregates of elongated or spindle-shaped mast cells which fill the papillary dermis and extend into the reticular dermis. In adults, the lesions tend to have fewer mast cells compared to those in children. The lesions are located most commonly on the trunk, but they can be seen on the extremities, head and neck. (who, 2001)
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q82.2 is considered exempt from POA reporting.
ICD-10-CM Q82.2 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
  • 606 Minor skin disorders with mcc
  • 607 Minor skin disorders without mcc
  • 795 Normal newborn

Convert Q82.2 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): Revised code
    • New description: Congenital cutaneous mastocytosis
    • 2017 description: Mastocytosis
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
Code annotations containing back-references to Q82.2:
  • Type 1 Excludes: C96.2
    , D47.0
    , D47.01
    , D47.01
    , D89.4
    ICD-10-CM Diagnosis Code C96.2

    Malignant mast cell neoplasm

      2016 2017 2018 - Converted to Parent Code 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • indolent mastocytosis (D47.02)
    • mast cell leukemia (C94.30)
    • mastocytosis (congenital) (cutaneous) (Q82.2)
    ICD-10-CM Diagnosis Code D47.0

    Mast cell neoplasms of uncertain behavior

      2016 2017 2018 - Converted to Parent Code 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • congenital cutaneous mastocytosis (Q82.2)
    • histiocytic neoplasms of uncertain behavior (D47.Z9)
    • malignant mast cell neoplasm (C96.2-)
    ICD-10-CM Diagnosis Code D47.01

    Cutaneous mastocytosis

      2018 - New Code 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Diffuse cutaneous mastocytosis
    • Maculopapular cutaneous mastocytosis
    • Solitary mastocytoma
    • Telangiectasia macularis eruptiva perstans
    • Urticaria pigmentosa
    Type 1 Excludes
    • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
    • congenital urticaria pigmentosa (Q82.2)
    • extracutaneous mastocytoma (D47.09)
    ICD-10-CM Diagnosis Code D47.01

    Cutaneous mastocytosis

      2018 - New Code 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Diffuse cutaneous mastocytosis
    • Maculopapular cutaneous mastocytosis
    • Solitary mastocytoma
    • Telangiectasia macularis eruptiva perstans
    • Urticaria pigmentosa
    Type 1 Excludes
    • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
    • congenital urticaria pigmentosa (Q82.2)
    • extracutaneous mastocytoma (D47.09)
    ICD-10-CM Diagnosis Code D89.4

    Mast cell activation syndrome and related disorders

      2017 - New Code 2018 2019 2020 2021 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • aggressive systemic mastocytosis (C96.21)
    • congenital cutaneous mastocytosis (Q82.2)
    • (non-congenital) cutaneous mastocytosis (D47.01)
    • (indolent) systemic mastocytosis (D47.02)
    • malignant mast cell neoplasm (C96.2-)
    • malignant mastocytoma (C96.29)
    • mast cell leukemia (C94.3-)
    • mast cell sarcoma (C96.22)
    • mastocytoma NOS (D47.09)
    • other mast cell neoplasms of uncertain behavior (D47.09)
    • systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)

Diagnosis Index entries containing back-references to Q82.2:
  • Mastocytosis D47.09
    ICD-10-CM Diagnosis Code D47.09

    Other mast cell neoplasms of uncertain behavior

      2018 - New Code 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Extracutaneous mastocytoma
    • Mast cell tumor NOS
    • Mastocytoma NOS
    • Mastocytosis NOS
    • cutaneous (diffuse) (maculopapular) D47.01
      ICD-10-CM Diagnosis Code D47.01

      Cutaneous mastocytosis

        2018 - New Code 2019 2020 2021 Billable/Specific Code
      Applicable To
      • Diffuse cutaneous mastocytosis
      • Maculopapular cutaneous mastocytosis
      • Solitary mastocytoma
      • Telangiectasia macularis eruptiva perstans
      • Urticaria pigmentosa
      Type 1 Excludes
      • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
      • congenital urticaria pigmentosa (Q82.2)
      • extracutaneous mastocytoma (D47.09)
      • congenital Q82.2
      • of neonatal onset Q82.2
      • of newborn onset Q82.2
  • Urticaria L50.9
    ICD-10-CM Diagnosis Code L50.9

    Urticaria, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    • pigmentosa D47.01
      ICD-10-CM Diagnosis Code D47.01

      Cutaneous mastocytosis

        2018 - New Code 2019 2020 2021 Billable/Specific Code
      Applicable To
      • Diffuse cutaneous mastocytosis
      • Maculopapular cutaneous mastocytosis
      • Solitary mastocytoma
      • Telangiectasia macularis eruptiva perstans
      • Urticaria pigmentosa
      Type 1 Excludes
      • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
      • congenital urticaria pigmentosa (Q82.2)
      • extracutaneous mastocytoma (D47.09)
      • congenital Q82.2
      • of neonatal onset Q82.2
      • of newborn onset Q82.2

ICD-10-CM Codes Adjacent To Q82.2
Q80.9 Congenital ichthyosis, unspecified
Q81 Epidermolysis bullosa
Q81.0 Epidermolysis bullosa simplex
Q81.1 Epidermolysis bullosa letalis
Q81.2 Epidermolysis bullosa dystrophica
Q81.8 Other epidermolysis bullosa
Q81.9 Epidermolysis bullosa, unspecified
Q82 Other congenital malformations of skin
Q82.0 Hereditary lymphedema
Q82.1 Xeroderma pigmentosum
Q82.2 Congenital cutaneous mastocytosis
Q82.3 Incontinentia pigmenti
Q82.4 Ectodermal dysplasia (anhidrotic)
Q82.5 Congenital non-neoplastic nevus
Q82.6 Congenital sacral dimple
Q82.8 Other specified congenital malformations of skin
Q82.9 Congenital malformation of skin, unspecified
Q83 Congenital malformations of breast
Q83.0 Congenital absence of breast with absent nipple
Q83.1 Accessory breast
Q83.2 Absent nipple

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.