2019 ICD-10-CM Diagnosis Code Q82.3

Incontinentia pigmenti

    2016 2017 2018 2019 Billable/Specific Code POA Exempt
  • Q82.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2019 edition of ICD-10-CM Q82.3 became effective on October 1, 2018.
  • This is the American ICD-10-CM version of Q82.3 - other international versions of ICD-10 Q82.3 may differ.
The following code(s) above Q82.3 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q82.3:
  • Q00-Q99
    2019 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q82
    ICD-10-CM Diagnosis Code Q82

    Other congenital malformations of skin

      2016 2017 2018 2019 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • acrodermatitis enteropathica (E83.2)
    • congenital erythropoietic porphyria (E80.0)
    • pilonidal cyst or sinus (L05.-)
    • Sturge-Weber (-Dimitri) syndrome (Q85.8)
    Other congenital malformations of skin
Approximate Synonyms
  • Incontinentia pigmenti syndrome
Clinical Information
  • A genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. Hyperpigmentation is bizarre and irregular. Sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.
  • A rare disorder caused by mutations in the ikbkg gene. It is characterized by skin abnormalities, alopecia, dystrophic nails, and abnormal tooth shape. The skin changes evolve from an initial blistering rash, to wart-like lesions, and eventually to hypopigmentation.
  • A skin pigmentation disorder with malformations of the eyes, teeth, bones, nails, heart, central nervous system, and hair. Mental deficiency is usually associated. The syndrome is divided into two forms: incontinentia pigmenti type i and type ii which lethal in males.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q82.3 is considered exempt from POA reporting.
ICD-10-CM Q82.3 is grouped within Diagnostic Related Group(s) (MS-DRG v36.0):
  • 606 Minor skin disorders with mcc
  • 607 Minor skin disorders without mcc
  • 795 Normal newborn

Convert Q82.3 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change

Diagnosis Index entries containing back-references to Q82.3:
  • Bloch-Sulzberger disease or syndrome Q82.3
  • Incontinentia pigmenti Q82.3

ICD-10-CM Codes Adjacent To Q82.3
Q81 Epidermolysis bullosa
Q81.0 Epidermolysis bullosa simplex
Q81.1 Epidermolysis bullosa letalis
Q81.2 Epidermolysis bullosa dystrophica
Q81.8 Other epidermolysis bullosa
Q81.9 Epidermolysis bullosa, unspecified
Q82 Other congenital malformations of skin
Q82.0 Hereditary lymphedema
Q82.1 Xeroderma pigmentosum
Q82.2 Congenital cutaneous mastocytosis
Q82.3 Incontinentia pigmenti
Q82.4 Ectodermal dysplasia (anhidrotic)
Q82.5 Congenital non-neoplastic nevus
Q82.6 Congenital sacral dimple
Q82.8 Other specified congenital malformations of skin
Q82.9 Congenital malformation of skin, unspecified
Q83 Congenital malformations of breast
Q83.0 Congenital absence of breast with absent nipple
Q83.1 Accessory breast
Q83.2 Absent nipple
Q83.3 Accessory nipple

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.