ICD-10-CM Codes
Q00-Q99
Q80-Q89
Q82-
2023 ICD-10-CM Diagnosis Code Q82.8

2023 ICD-10-CM Diagnosis Code Q82.8

Other specified congenital malformations of skin

2016

2017

2018

2019

2020

2021

2022

2023

Billable/Specific Code

POA Exempt

Q82.8 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
The 2023 edition of ICD-10-CM Q82.8 became effective on October 1, 2022.
This is the American ICD-10-CM version of Q82.8 - other international versions of ICD-10 Q82.8 may differ.

Applicable To

Abnormal palmar creases
Accessory skin tags
Benign familial pemphigus [Hailey-Hailey]
Congenital poikiloderma
Cutis laxa (hyperelastica)
Dermatoglyphic anomalies
Inherited keratosis palmaris et plantaris
Keratosis follicularis [Darier-White]

Type 1 Excludes

Type 1 Excludes Help

A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q82.8. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

Ehlers-Danlos syndromes (
ICD-10-CM Diagnosis Code Q79.6
Ehlers-Danlos syndromes
Q79.6-
)

The following code(s) above Q82.8 contain annotation back-references

Annotation Back-References

In this context, annotation back-references refer to codes that contain:

Applicable To annotations, or
Code Also annotations, or
Code First annotations, or
Excludes1 annotations, or
Excludes2 annotations, or
Includes annotations, or
Note annotations, or
Use Additional annotations

that may be applicable to Q82.8:

Q00-Q99
2023 ICD-10-CM Range Q00-Q99
Congenital malformations, deformations and chromosomal abnormalities
Note
- Codes from this chapter are not for use on maternal records
Type 2 Excludes
- inborn errors of metabolism (E70-E88)
Congenital malformations, deformations and chromosomal abnormalities
Q82
ICD-10-CM Diagnosis Code Q82
Other congenital malformations of skin
Type 1 Excludes
- acrodermatitis enteropathica (E83.2)
- congenital erythropoietic porphyria (E80.0)
- pilonidal cyst or sinus (L05.-)
- Sturge-Weber (-Dimitri) syndrome (Q85.89)
Other congenital malformations of skin

Approximate Synonyms

Abnormal dermatoglyphic pattern
Abnormal gluteal crease
Abnormal palmar creases
Accessory skin tag, congenital
Acrokeratosis verruciformis of hopf
Acrokeratosis verruciforms
Anomaly of skin pigment, congenital
Aplasia cutis
Aplasia cutis congenita
Bloom syndrome
Congenital accessory skin tag
Congenital keratoderma
Congenital keratosis follicularis
Congenital keratosis pilaris
Congenital pigmentary skin anomalies
Congenital scar
Congenital skin contracture
Dariers disease
Dermatoglyphic anomalies
Dyskeratosis congenita
Familial benign pemphigus
Goltz syndrome
Goltz-gorlin (dermal hypoplasia) syndrome
Hailey disease
Hereditary benign acanthosis nigricans
Howel evans syndrome
Howel-evans' syndrome
Keratoderma, congenital
Keratosis follicularis
Keratosis pilaris, congenital
Mongolian spot
Mongolian spot (blue/gray skin discoloration)
Pachydermoperiostosis syndrome
Porokeratosis
Porokeratosis (skin condition)
Porokeratosis of mibelli
Pseudoxanthoma elasticum
Sacral dimple
Scar, congenital
Touraine-solente-gole syndrome

Clinical Information

A congenital or acquired disorder affecting the elastic fibers of the skin. It is characterized by loss of elasticity resulting in loosening and folding of the skin.
A group of connective tissue diseases in which skin hangs in loose pendulous folds. It is believed to be associated with decreased elastic tissue formation as well as an abnormality in elastin formation. Cutis laxa is usually a genetic disease, but acquired cases have been reported. (from Dorland, 27th ed)
A rare inherited disorder that affects the skin and many other parts of the body, including the bones, eyes, nose, hair, nails, teeth, testes, and ovaries. People with rothmund-thomson syndrome have an increased risk of osteosarcoma (bone cancer).
An autosomal dominant disorder characterized by a history of multiple relapses and remissions of pemphigus lesions.
An autosomal dominantly inherited skin disorder characterized by recurrent eruptions of vesicles and bullae mainly on the neck, axillae, and groin. Mutations in the atp2c1 gene (encoding the secretory pathway ca2++/mn2++ atpase 1 (spca1)) cause this disease. It is clinically and histologically similar to darier disease - both have abnormal, unstable desmosomes between keratinocytes and defective calcium-transporting atpases. It is unrelated to pemphigus vulgaris though it closely resembles that disease.
An autosomal recessive inherited syndrome usually caused by mutations in the recql4 gene. It is characterized by poikilodermatous skin changes, sparse hair, cataracts, small stature, skeletal abnormalities, and an increased predisposition to cancer, particularly osteosarcoma.
An autosomal recessive syndrome occurring principally in females, characterized by the presence of reticulated, atrophic, hyperpigmented, telangiectatic cutaneous plaques, often accompanied by juvenile cataracts, saddle nose, congenital bone defects, disturbances in the growth of hair; nails; and teeth; and hypogonadism.
Group of connective tissue diseases in which skin hangs in loose pendulous folds; believed to be associated with decreased elastic tissue formation as well as an abnormality in elastin formation; usually a genetic disease, but acquired cases have been reported.

Present On Admission

POA Help

"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.

Q82.8 is considered exempt from POA reporting.

ICD-10-CM Q82.8 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):

606 Minor skin disorders with mcc
607 Minor skin disorders without mcc
795 Normal newborn

Convert Q82.8 to ICD-9-CM

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change
2022 (effective 10/1/2021): No change
2023 (effective 10/1/2022): No change

Code annotations containing back-references to Q82.8:

Type 1 Excludes: E79
, L11.0
, L85.1

ICD-10-CM Diagnosis Code E79
Disorders of purine and pyrimidine metabolism
Type 1 Excludes
- Ataxia-telangiectasia (Q87.19)
- Bloom's syndrome (Q82.8)
- Cockayne's syndrome (Q87.19)
- calculus of kidney (N20.0)
- combined immunodeficiency disorders (D81.-)
- Fanconi's anemia (D61.09)
- gout (M1A.-, M10.-)
- orotaciduric anemia (D53.0)
- progeria (E34.8)
- Werner's syndrome (E34.8)
- xeroderma pigmentosum (Q82.1)
ICD-10-CM Diagnosis Code L11.0
Acquired keratosis follicularis
Type 1 Excludes
- keratosis follicularis (congenital) [Darier-White] (Q82.8)
ICD-10-CM Diagnosis Code L85.1
Acquired keratosis [keratoderma] palmaris et plantaris
Type 1 Excludes
- inherited keratosis palmaris et plantaris (Q82.8)

Diagnosis Index entries containing back-references to Q82.8:

Abnormal, abnormality, abnormalities - see also Anomaly
- palmar creases Q82.8
Acanthosis (acquired) (nigricans) L83
ICD-10-CM Diagnosis Code L83
Acanthosis nigricans
Applicable To
Confluent and reticulated papillomatosis
- benign Q82.8
- congenital Q82.8
Accessory (congenital)
- skin tags Q82.8
Angiomatosis Q82.8
Anomaly, anomalous (congenital) (unspecified type) Q89.9
ICD-10-CM Diagnosis Code Q89.9
Congenital malformation, unspecified
Applicable To
Congenital anomaly NOS
Congenital deformity NOS
- pigmentation L81.9
  ICD-10-CM Diagnosis Code L81.9
  Disorder of pigmentation, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - congenital Q82.8
- dermatoglyphic Q82.8
- simian crease Q82.8
Bloom Q82.8 (-Machacek)(-Torre)
Brugsch's syndrome Q82.8
Cutis - see also condition
- hyperelastica Q82.8
- verticis gyrata Q82.8
Darier (-White) disease (congenital) Q82.8
Dermatolysis (exfoliativa) (congenital) Q82.8
Dermatomegaly NEC Q82.8
Dyskeratosis L85.8
ICD-10-CM Diagnosis Code L85.8
Other specified epidermal thickening
Applicable To
Cutaneous horn
- congenital Q82.8
Dysplasia - see also Anomaly
- ectodermal (anhidrotic) (congenital) (hereditary) Q82.4
  ICD-10-CM Diagnosis Code Q82.4
  Ectodermal dysplasia (anhidrotic)
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Type 1 Excludes
  Ellis-van Creveld syndrome (Q77.6)
  - hydrotic Q82.8
Elastic skin Q82.8
Elastoma (juvenile) Q82.8
Gyrate scalp Q82.8
Hailey-Hailey disease Q82.8
Hyperkeratosis L85.9
- see also Keratosis
ICD-10-CM Diagnosis Code L85.9
Epidermal thickening, unspecified
- follicularis Q82.8
Hypoplasia, hypoplastic
- focal dermal Q82.8
- skin Q82.8
Ichthyosis (congenital) Q80.9
ICD-10-CM Diagnosis Code Q80.9
Congenital ichthyosis, unspecified
- palmaris and plantaris Q82.8
India rubber skin Q82.8
Keratoderma, keratodermia (congenital) (palmaris et plantaris) (symmetrical) Q82.8
Keratoma L57.0
ICD-10-CM Diagnosis Code L57.0
Actinic keratosis
Applicable To
Keratosis NOS
Senile keratosis
Solar keratosis
- palmaris and plantaris hereditarium Q82.8
Keratosis L57.0
ICD-10-CM Diagnosis Code L57.0
Actinic keratosis
Applicable To
Keratosis NOS
Senile keratosis
Solar keratosis
- follicularis Q82.8
  - congenita Q82.8
  - spinulosa Q82.8 (decalvans)
- palmaris et plantaris (inherited) (symmetrical) Q82.8
- vegetans Q82.8
Lax, laxity - see also Relaxation
- skin (acquired) L57.4
  ICD-10-CM Diagnosis Code L57.4
  Cutis laxa senilis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Elastosis senilis
  - congenital Q82.8
Lichen L28.0
ICD-10-CM Diagnosis Code L28.0
Lichen simplex chronicus
Applicable To
Circumscribed neurodermatitis
Lichen NOS
- pilaris Q82.8
- congenital Q82.8
Melanocytosis, neurocutaneous Q82.8
Mibelli's disease Q82.8 (porokeratosis)
Naegeli's
- disease Q82.8
Pachydermatocele Q82.8 (congenital)
Particolored infant Q82.8
Pemphigus L10.9
ICD-10-CM Diagnosis Code L10.9
Pemphigus, unspecified
- benign familial Q82.8 (chronic)
Pigmentation (abnormal) (anomaly) L81.9
ICD-10-CM Diagnosis Code L81.9
Disorder of pigmentation, unspecified
- lids, congenital Q82.8
- scrotum, congenital Q82.8
Poikiloderma L81.6
ICD-10-CM Diagnosis Code L81.6
Other disorders of diminished melanin formation
- congenital Q82.8
Porokeratosis Q82.8
Pseudoxanthoma elasticum Q82.8
Rothmund Q82.8 (-Thomson)
Siemens' syndrome Q82.8 (ectodermal dysplasia)
Syndrome - see also Disease
- telangiectasic-pigmentation-cataract Q82.8
Tag (hypertrophied skin) (infected) L91.8
ICD-10-CM Diagnosis Code L91.8
Other hypertrophic disorders of the skin
- skin L91.8
  ICD-10-CM Diagnosis Code L91.8
  Other hypertrophic disorders of the skin
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - accessory Q82.8 (congenital)
  - congenital Q82.8
Tylosis (acquired) L84
ICD-10-CM Diagnosis Code L84
Corns and callosities
Applicable To
Callus
Clavus
- palmaris et plantaris (congenital) (inherited) Q82.8

ICD-10-CM Codes Adjacent To Q82.8

Q81.8 Other epidermolysis bullosa

Q81.9 Epidermolysis bullosa, unspecified

Q82 Other congenital malformations of skin

Q82.0 Hereditary lymphedema

Q82.1 Xeroderma pigmentosum

Q82.2 Congenital cutaneous mastocytosis

Q82.3 Incontinentia pigmenti

Q82.4 Ectodermal dysplasia (anhidrotic)

Q82.5 Congenital non-neoplastic nevus

Q82.6 Congenital sacral dimple

Q82.8 Other specified congenital malformations of skin

Q82.9 Congenital malformation of skin, unspecified

Q83 Congenital malformations of breast

Q83.0 Congenital absence of breast with absent nipple

Q83.1 Accessory breast

Q83.2 Absent nipple

Q83.3 Accessory nipple

Q83.8 Other congenital malformations of breast

Q83.9 Congenital malformation of breast, unspecified

Q84 Other congenital malformations of integument

Q84.0 Congenital alopecia

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.

2023 ICD-10-CM Diagnosis Code Q82.8

Other specified congenital malformations of skin

Ehlers-Danlos syndromes

Congenital malformations, deformations and chromosomal abnormalities

Other congenital malformations of skin

Disorders of purine and pyrimidine metabolism

Acquired keratosis follicularis

Acquired keratosis [keratoderma] palmaris et plantaris

Acanthosis nigricans

Congenital malformation, unspecified

Disorder of pigmentation, unspecified

Other specified epidermal thickening

Ectodermal dysplasia (anhidrotic)

Epidermal thickening, unspecified

Congenital ichthyosis, unspecified

Actinic keratosis

Actinic keratosis

Cutis laxa senilis

Lichen simplex chronicus

Pemphigus, unspecified

Disorder of pigmentation, unspecified

Other disorders of diminished melanin formation

Other hypertrophic disorders of the skin

Other hypertrophic disorders of the skin

Corns and callosities