2023 ICD-10-CM Diagnosis Code Q85.89

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Other phakomatoses, not elsewhere classified

    2023 - New Code Billable/Specific Code POA Exempt
  • Q85.89 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • ICD-10-CM Q85.89 is a new 2023 ICD-10-CM code that became effective on October 1, 2022.
  • This is the American ICD-10-CM version of Q85.89 - other international versions of ICD-10 Q85.89 may differ.
Applicable To
  • Peutz-Jeghers syndrome
  • Sturge-Weber(-Dimitri) syndrome
The following code(s) above Q85.89 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q85.89:
  • Q00-Q99
    2023 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q85
    ICD-10-CM Diagnosis Code Q85

    Phakomatoses, not elsewhere classified

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • ataxia telangiectasia [Louis-Bar] (G11.3)
    • familial dysautonomia [Riley-Day] (G90.1)
    Phakomatoses, not elsewhere classified
  • Q85.8
    ICD-10-CM Diagnosis Code Q85.8

    Other phakomatoses, not elsewhere classified

      2016 2017 2018 2019 2020 2021 2022 2023 - Converted to Parent Code Non-Billable/Non-Specific Code
    Type 1 Excludes
    • Meckel-Gruber syndrome (Q61.9)
    Other phakomatoses, not elsewhere classified
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q85.89 is considered exempt from POA reporting.
ICD-10-CM Q85.89 is grouped within Diagnostic Related Group(s) (MS-DRG v40.0):
  • 826 Myeloproliferative disorders or poorly differentiated neoplasms with major o.r. Procedures with mcc
  • 827 Myeloproliferative disorders or poorly differentiated neoplasms with major o.r. Procedures with cc
  • 828 Myeloproliferative disorders or poorly differentiated neoplasms with major o.r. Procedures without cc/mcc
  • 829 Myeloproliferative disorders or poorly differentiated neoplasms with other procedures with cc/mcc
  • 830 Myeloproliferative disorders or poorly differentiated neoplasms with other procedures without cc/mcc
  • 843 Other myeloproliferative disorders or poorly differentiated neoplastic diagnoses with mcc
  • 844 Other myeloproliferative disorders or poorly differentiated neoplastic diagnoses with cc
  • 845 Other myeloproliferative disorders or poorly differentiated neoplastic diagnoses without cc/mcc
Code History
  • 2023 (effective 10/1/2022): New code
Code annotations containing back-references to Q85.89:
  • Type 1 Excludes: Q82
    , L81
    ICD-10-CM Diagnosis Code Q82

    Other congenital malformations of skin

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • acrodermatitis enteropathica (E83.2)
    • congenital erythropoietic porphyria (E80.0)
    • pilonidal cyst or sinus (L05.-)
    • Sturge-Weber (-Dimitri) syndrome (Q85.89)
    ICD-10-CM Diagnosis Code L81

    Other disorders of pigmentation

      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Type 2 Excludes
    • nevus - see Alphabetical Index

Diagnosis Index entries containing back-references to Q85.89:
  • Angiomatosis Q82.8
    ICD-10-CM Diagnosis Code Q82.8

    Other specified congenital malformations of skin

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    • Abnormal palmar creases
    • Accessory skin tags
    • Benign familial pemphigus [Hailey-Hailey]
    • Congenital poikiloderma
    • Cutis laxa (hyperelastica)
    • Dermatoglyphic anomalies
    • Inherited keratosis palmaris et plantaris
    • Keratosis follicularis [Darier-White]
    Type 1 Excludes
    • Ehlers-Danlos syndromes (Q79.6-)
    • encephalotrigeminal Q85.89
  • Dimitri-Sturge-Weber disease Q85.89
  • Kraft-Weber-Dimitri disease Q85.89
  • Peutz-Jeghers disease or syndrome Q85.89
  • Phakomatosis Q85.9
    - see also specific eponymous syndromes
    ICD-10-CM Diagnosis Code Q85.9

    Phakomatosis, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    • Hamartosis NOS
    • specified NEC Q85.89
  • Sturge Q85.89 (-Weber) (-Dimitri) (-Kalischer)
  • Syndrome - see also Disease
    • Peutz-Jeghers Q85.89
    • Sturge-Weber Q85.89 (-Dimitri)

ICD-10-CM Codes Adjacent To Q85.89
Q85.00 Neurofibromatosis, unspecified
Q85.01 Neurofibromatosis, type 1
Q85.02 Neurofibromatosis, type 2
Q85.03 Schwannomatosis
Q85.09 Other neurofibromatosis
Q85.1 Tuberous sclerosis
Q85.8 Other phakomatoses, not elsewhere classified
Q85.81 PTEN tumor syndrome
Q85.82 Other Cowden syndrome
Q85.83 Von Hippel-Lindau syndrome
Q85.89 Other phakomatoses, not elsewhere classified
Q85.9 Phakomatosis, unspecified
Q86 Congenital malformation syndromes due to known exogenous causes, not elsewhere classified
Q86.0 Fetal alcohol syndrome (dysmorphic)
Q86.1 Fetal hydantoin syndrome
Q86.2 Dysmorphism due to warfarin
Q86.8 Other congenital malformation syndromes due to known exogenous causes
Q87 Other specified congenital malformation syndromes affecting multiple systems
Q87.0 Congenital malformation syndromes predominantly affecting facial appearance
Q87.1 Congenital malformation syndromes predominantly associated with short stature
Q87.11 Prader-Willi syndrome

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.