ICD-10-CM Codes
Q00-Q99
Q80-Q89
Other specified congenital malformation syndromes affecting multiple systems Q87

Other specified congenital malformation syndromes affecting multiple systems Q87-

Use Additional

Use Additional Help

Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.

code(s) to identify all associated manifestations

Codes

Q87 Other specified congenital malformation syndromes affecting multiple systems
- Q87.0 Congenital malformation syndromes predominantly affecting facial appearance
- Q87.1 Congenital malformation syndromes predominantly associated with short stature
  - Q87.11 Prader-Willi syndrome
  - Q87.19 Other congenital malformation syndromes predominantly associated with short stature
- Q87.2 Congenital malformation syndromes predominantly involving limbs
- Q87.3 Congenital malformation syndromes involving early overgrowth
- Q87.4 Marfan's syndrome
  - Q87.40 …… unspecified
  - Q87.41 Marfan's syndrome with cardiovascular manifestations
    - Q87.410 Marfan's syndrome with aortic dilation
    - Q87.418 Marfan's syndrome with other cardiovascular manifestations
  - Q87.42 …… with ocular manifestations
  - Q87.43 …… with skeletal manifestation
- Q87.5 Other congenital malformation syndromes with other skeletal changes
- Q87.8 Other specified congenital malformation syndromes, not elsewhere classified
  - Q87.81 Alport syndrome
  - Q87.82 Arterial tortuosity syndrome
  - Q87.89 Other specified congenital malformation syndromes, not elsewhere classified