2018 ICD-10-CM Diagnosis Code Q87.1

Congenital malformation syndromes predominantly associated with short stature

Applicable To
  • Aarskog syndrome
  • Cockayne syndrome
  • De Lange syndrome
  • Dubowitz syndrome
  • Noonan syndrome
  • Prader-Willi syndrome
  • Robinow-Silverman-Smith syndrome
  • Russell-Silver syndrome
  • Seckel syndrome
Type 1 Excludes
Type 1 Excludes Help
A type 1 excludes note is a pure excludes. It means "not coded here". A type 1 excludes note indicates that the code excluded should never be used at the same time as Q87.1. A type 1 excludes note is for used for when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Ellis-van Creveld syndrome (
    ICD-10-CM Diagnosis Code Q77.6

    Chondroectodermal dysplasia

      2016 2017 2018 Billable/Specific Code POA Exempt
    Applicable To
    • Ellis-van Creveld syndrome
    Q77.6
    )
  • Smith-Lemli-Opitz syndrome (
    ICD-10-CM Diagnosis Code E78.72

    Smith-Lemli-Opitz syndrome

      2016 2017 2018 Billable/Specific Code
    E78.72
    )
The following code(s) above Q87.1 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q87.1:
  • Q00-Q99
    2018 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal or fetal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q87
    ICD-10-CM Diagnosis Code Q87

    Other specified congenital malformation syndromes affecting multiple systems

      2016 2017 2018 Non-Billable/Non-Specific Code
    Use Additional
    • code(s) to identify all associated manifestations
    Other specified congenital malformation syndromes affecting multiple systems
Approximate Synonyms Clinical Information Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
ICD-10-CM Q87.1 is grouped within Diagnostic Related Group(s) (MS-DRG v35.0):

Convert Q87.1 to ICD-9-CM

Code History
Code annotations containing back-references to Q87.1:

Diagnosis Index entries containing back-references to Q87.1:

ICD-10-CM Codes Adjacent To Q87.1
Q85.1 Tuberous sclerosis
Q85.8 Other phakomatoses, not elsewhere classified
Q85.9 Phakomatosis, unspecified
Q86 Congenital malformation syndromes due to known exogenous causes, not elsewhere classified
Q86.0 Fetal alcohol syndrome (dysmorphic)
Q86.1 Fetal hydantoin syndrome
Q86.2 Dysmorphism due to warfarin
Q86.8 Other congenital malformation syndromes due to known exogenous causes
Q87 Other specified congenital malformation syndromes affecting multiple systems
Q87.0 Congenital malformation syndromes predominantly affecting facial appearance
Q87.1 Congenital malformation syndromes predominantly associated with short stature
Q87.2 Congenital malformation syndromes predominantly involving limbs
Q87.3 Congenital malformation syndromes involving early overgrowth
Q87.4 Marfan's syndrome
Q87.40 …… unspecified
Q87.41 Marfan's syndrome with cardiovascular manifestations
Q87.410 Marfan's syndrome with aortic dilation
Q87.418 Marfan's syndrome with other cardiovascular manifestations
Q87.42 …… with ocular manifestations
Q87.43 …… with skeletal manifestation
Q87.5 Other congenital malformation syndromes with other skeletal changes

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.