2020 ICD-10-CM Diagnosis Code Q87.81

Alport syndrome

    2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
  • Q87.81 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2020 edition of ICD-10-CM Q87.81 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of Q87.81 - other international versions of ICD-10 Q87.81 may differ.
Use Additional
Use Additional Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • code to identify stage of chronic kidney disease (
    ICD-10-CM Diagnosis Code N18.1

    Chronic kidney disease, stage 1

      2016 2017 2018 2019 2020 Billable/Specific Code
    N18.1-
    ICD-10-CM Diagnosis Code N18.6

    End stage renal disease

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Chronic kidney disease requiring chronic dialysis
    Use Additional
    • code to identify dialysis status (Z99.2)
    N18.6
    )
The following code(s) above Q87.81 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q87.81:
  • Q00-Q99
    2020 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q87
    ICD-10-CM Diagnosis Code Q87

    Other specified congenital malformation syndromes affecting multiple systems

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Use Additional
    • code(s) to identify all associated manifestations
    Other specified congenital malformation syndromes affecting multiple systems
  • Q87.8
    ICD-10-CM Diagnosis Code Q87.8

    Other specified congenital malformation syndromes, not elsewhere classified

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Other specified congenital malformation syndromes, not elsewhere classified
Approximate Synonyms
  • Alports syndrome
  • Hereditary nephritis
Clinical Information
  • A genetic syndrome usually inherited as an x-link trait. It is caused by abnormalities in the col4a5 gene. It affects males more often than females and is characterized by hematuria, progressive renal insufficiency, hearing loss, and ocular abnormalities.
  • A genetically heterogenous disorder characterized by kidney abnormalities with hematuria and proteinuria, sensorineural hearing loss, and eye abnormalities. Two main genetically distinct forms are recognized: an x-linked dominant form (mim 301050) with additional features including mental retardation, dysmorphic facies with midfacial hypoplasia, elliptocytosis and smooth muscle tumors; and an autosomal recessive form (omim 203780). Variants of alport syndrome without mental retardation include: alport syndrome with leukocyte inclusions and macrothrombocytopenia (transmitted as an autosomal dominant trait) synonyms: fechtner syndrome (named after a patient) sebastian platelet syndrome (named after a patient) macrothrombocytopathy-deafness-nephritis-leukocyte inclusions syndrome (omim 153640) alport syndrome with macrothrombocytopenia (transmitted as an autosomal dominant trait) synonyms: epstein syndrome hereditary macrothrombocytopathia-nephritis-deafness syndrome macrothrombocytopathy-nephritis-deafness syndrome thrombocytopenia-macrothrombocytopathia-nephritis-defames syndrome (omim 153650) hereditary nephropathy-deafness syndrome (transmitted as an autosomal dominant trait) synonym: hereditary nephropathy-sensorineural hearing loss syndrome (omim 104200) alport syndrome with abnormal collagen of basement membrane (transmitted as an x-linked trait) (omim 303630)
  • Hereditary disorder characterized by progressive sensorineural hearing loss, progressive pyelonephritis or glomerulonephritis, and, occasionally, ocular defects; transmitted as an autosomal dominant or x-linked trait.
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q87.81 is considered exempt from POA reporting.
ICD-10-CM Q87.81 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 564 Other musculoskeletal system and connective tissue diagnoses with mcc
  • 565 Other musculoskeletal system and connective tissue diagnoses with cc
  • 566 Other musculoskeletal system and connective tissue diagnoses without cc/mcc

Convert Q87.81 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
Code annotations containing back-references to Q87.81:
  • Type 2 Excludes: N07
    ICD-10-CM Diagnosis Code N07

    Hereditary nephropathy, not elsewhere classified

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 2 Excludes
    • Alport's syndrome (Q87.81-)
    • hereditary amyloid nephropathy (E85.-)
    • nail patella syndrome (Q87.2)
    • non-neuropathic heredofamilial amyloidosis (E85.-)

Diagnosis Index entries containing back-references to Q87.81:

ICD-10-CM Codes Adjacent To Q87.81
Q87.3 Congenital malformation syndromes involving early overgrowth
Q87.4 Marfan's syndrome
Q87.40 …… unspecified
Q87.41 Marfan's syndrome with cardiovascular manifestations
Q87.410 Marfan's syndrome with aortic dilation
Q87.418 Marfan's syndrome with other cardiovascular manifestations
Q87.42 …… with ocular manifestations
Q87.43 …… with skeletal manifestation
Q87.5 Other congenital malformation syndromes with other skeletal changes
Q87.8 Other specified congenital malformation syndromes, not elsewhere classified
Q87.81 Alport syndrome
Q87.82 Arterial tortuosity syndrome
Q87.89 Other specified congenital malformation syndromes, not elsewhere classified
Q89 Other congenital malformations, not elsewhere classified
Q89.0 Congenital absence and malformations of spleen
Q89.01 Asplenia (congenital)
Q89.09 Congenital malformations of spleen
Q89.1 Congenital malformations of adrenal gland
Q89.2 Congenital malformations of other endocrine glands
Q89.3 Situs inversus
Q89.4 Conjoined twins

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.