2020 ICD-10-CM Diagnosis Code Q87.89

Other specified congenital malformation syndromes, not elsewhere classified

    2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
  • Q87.89 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • Short description: Oth congenital malformation syndromes, NEC
  • The 2020 edition of ICD-10-CM Q87.89 became effective on October 1, 2019.
  • This is the American ICD-10-CM version of Q87.89 - other international versions of ICD-10 Q87.89 may differ.
Applicable To
  • Laurence-Moon (-Bardet)-Biedl syndrome
The following code(s) above Q87.89 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q87.89:
  • Q00-Q99
    2020 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
  • Q87
    ICD-10-CM Diagnosis Code Q87

    Other specified congenital malformation syndromes affecting multiple systems

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Use Additional
    • code(s) to identify all associated manifestations
    Other specified congenital malformation syndromes affecting multiple systems
  • Q87.8
    ICD-10-CM Diagnosis Code Q87.8

    Other specified congenital malformation syndromes, not elsewhere classified

      2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    Type 1 Excludes
    Other specified congenital malformation syndromes, not elsewhere classified
Approximate Synonyms
  • Bannayan riley ruvalcaba syndrome
  • Bannayan syndrome
  • Bardet biedl syndrome
  • Basal cell nevus syndrome
  • Congenital hemihypertrophy
  • Gorlin syndrome
  • Leopard syndrome
  • Loeys dietz syndrome
  • Mcdonough syndrome
  • Moynahan's syndrome
Clinical Information
  • A syndrome characterized mainly by obesity, pigmentary retinopathy, polydactyly, mental retardation, hypogonadism, and renal failure in fatal cases. Two forms have been identified: bardet-biedl syndrome 1 (bbs1) has no linkage to chromosome 16 bardet-biedl syndrome 2 (bbs2) is mapped to markers on chromosome 16. Laurence-moon-biedl syndrome and laurence-moon-biedl-bardet syndrome are no longer considered as valid terms in that patients of laurence and moon had paraplegia but no polydactyly and obesity which are the key elements of the bardet-biedl the syndrome. Laurence-moon syndrome is a separate entity.
  • An autosomal recessive disorder characterized by retinitis pigmentosa; polydactyly; obesity; mental retardation; hypogenitalism; renal dysplasia; and short stature. This syndrome has been distinguished as a separate entity from laurence-moon syndrome. (from j med genet 1997 feb;34(2):92-8)
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q87.89 is considered exempt from POA reporting.
ICD-10-CM Q87.89 is grouped within Diagnostic Related Group(s) (MS-DRG v37.0):
  • 564 Other musculoskeletal system and connective tissue diagnoses with mcc
  • 565 Other musculoskeletal system and connective tissue diagnoses with cc
  • 566 Other musculoskeletal system and connective tissue diagnoses without cc/mcc

Convert Q87.89 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change

Diagnosis Index entries containing back-references to Q87.89:
  • Biedl-Bardet syndrome Q87.89
  • Birt-Hogg-Dube syndrome Q87.89
  • Cantrell's syndrome Q87.89
  • Cerebro-hepato-renal syndrome Q87.89
  • Laurence-Moon Q87.89 (-Bardet)
  • Syndrome - see also Disease
    • congenital
      • affecting multiple systems NEC Q87.89
      • muscular hypertrophy-cerebral Q87.89
    • popliteal
      • web Q87.89
    • basal cell nevus Q87.89
    • Birt-Hogg-Dube syndrome Q87.89
    • cardiofaciocutaneous Q87.89
    • Glass Q87.89
    • Gorlin's Q87.89
    • SATB2-associated Q87.89
  • Web, webbed (congenital)
    • popliteal syndrome Q87.89

ICD-10-CM Codes Adjacent To Q87.89
Q87.40 …… unspecified
Q87.41 Marfan's syndrome with cardiovascular manifestations
Q87.410 Marfan's syndrome with aortic dilation
Q87.418 Marfan's syndrome with other cardiovascular manifestations
Q87.42 …… with ocular manifestations
Q87.43 …… with skeletal manifestation
Q87.5 Other congenital malformation syndromes with other skeletal changes
Q87.8 Other specified congenital malformation syndromes, not elsewhere classified
Q87.81 Alport syndrome
Q87.82 Arterial tortuosity syndrome
Q87.89 Other specified congenital malformation syndromes, not elsewhere classified
Q89 Other congenital malformations, not elsewhere classified
Q89.0 Congenital absence and malformations of spleen
Q89.01 Asplenia (congenital)
Q89.09 Congenital malformations of spleen
Q89.1 Congenital malformations of adrenal gland
Q89.2 Congenital malformations of other endocrine glands
Q89.3 Situs inversus
Q89.4 Conjoined twins
Q89.7 Multiple congenital malformations, not elsewhere classified
Q89.8 Other specified congenital malformations

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.