2021 ICD-10-CM Diagnosis Code Q89.8

Other specified congenital malformations

    2016 2017 2018 2019 2020 2021 Billable/Specific Code POA Exempt
  • Q89.8 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • The 2021 edition of ICD-10-CM Q89.8 became effective on October 1, 2020.
  • This is the American ICD-10-CM version of Q89.8 - other international versions of ICD-10 Q89.8 may differ.
Use Additional
Use Additional Help
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation. In most cases the manifestation codes will have in the code title, "in diseases classified elsewhere." Codes with this title are a component of the etiology/manifestation convention. The code title indicates that it is a manifestation code. "In diseases classified elsewhere" codes are never permitted to be used as first listed or principle diagnosis codes. They must be used in conjunction with an underlying condition code and they must be listed following the underlying condition.
  • code(s) to identify all associated manifestations
The following code(s) above Q89.8 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to Q89.8:
  • Q00-Q99
    2021 ICD-10-CM Range Q00-Q99

    Congenital malformations, deformations and chromosomal abnormalities

    Note
    • Codes from this chapter are not for use on maternal records
    Type 2 Excludes
    • inborn errors of metabolism (E70-E88)
    Congenital malformations, deformations and chromosomal abnormalities
Approximate Synonyms
  • Acardiac monster
  • Acardiac syndrome
  • Caudal dysplasia sequence
  • Charge association
  • Kabuki make-up syndrome
  • Kabuki syndrome
  • Stickler syndrome
  • Williams syndrome
Present On Admission
POA Help
"Present On Admission" is defined as present at the time the order for inpatient admission occurs — conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered POA.
  • Q89.8 is considered exempt from POA reporting.
ICD-10-CM Q89.8 is grouped within Diagnostic Related Group(s) (MS-DRG v38.0):
  • 564 Other musculoskeletal system and connective tissue diagnoses with mcc
  • 565 Other musculoskeletal system and connective tissue diagnoses with cc
  • 566 Other musculoskeletal system and connective tissue diagnoses without cc/mcc

Convert Q89.8 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change

Diagnosis Index entries containing back-references to Q89.8:
  • Absence (of) (organ or part) (complete or partial)
  • Acardia, acardius Q89.8
  • Acardiacus amorphus Q89.8
  • Accessory (congenital)
  • Acephalobrachia monster Q89.8
  • Acephalochirus monster Q89.8
  • Acephalogaster Q89.8
  • Acephalostomus monster Q89.8
  • Acephalothorax Q89.8
  • Anomaly, anomalous (congenital) (unspecified type) Q89.9
    ICD-10-CM Diagnosis Code Q89.9

    Congenital malformation, unspecified

      2016 2017 2018 2019 2020 2021 Billable/Specific Code POA Exempt
    Applicable To
    • Congenital anomaly NOS
    • Congenital deformity NOS
    • specified organ or site NEC Q89.8
  • Atresia, atretic
    • organ or site NEC Q89.8
  • CHARGE association Q89.8
  • Cyst (colloid) (mucous) (simple) (retention)
  • Disease, diseased - see also Syndrome
    • Kok Q89.8
    • Startle Q89.8
  • Goldberg syndrome Q89.8
  • Hyperekplexia Q89.8
  • Hyperexplexia Q89.8
  • Malformation (congenital) - see also Anomaly
    • specified NEC Q89.8
  • Myofibromatosis D48.1
    ICD-10-CM Diagnosis Code D48.1

    Neoplasm of uncertain behavior of connective and other soft tissue

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    Applicable To
    • Neoplasm of uncertain behavior of connective tissue of ear
    • Neoplasm of uncertain behavior of connective tissue of eyelid
    • Stromal tumors of uncertain behavior of digestive system
    Type 1 Excludes
    • neoplasm of uncertain behavior of articular cartilage (D48.0)
    • neoplasm of uncertain behavior of cartilage of larynx (D38.0)
    • neoplasm of uncertain behavior of cartilage of nose (D38.5)
    • neoplasm of uncertain behavior of connective tissue of breast (D48.6-)
    • infantile Q89.8
  • Nephrosis, nephrotic (Epstein's) (syndrome) (congenital) N04.9
    ICD-10-CM Diagnosis Code N04.9

    Nephrotic syndrome with unspecified morphologic changes

      2016 2017 2018 2019 2020 2021 Billable/Specific Code
    • Finnish type Q89.8 (congenital)
  • Syndrome - see also Disease
    • Borjeson Forssman Lehmann Q89.8
    • CHARGE Q89.8
    • Coffin-Lowry Q89.8
    • Goldberg Q89.8
    • Kabuki Q89.8
    • Stickler Q89.8
    • stiff baby Q89.8
  • Teratencephalus Q89.8

ICD-10-CM Codes Adjacent To Q89.8
Q87.89 Other specified congenital malformation syndromes, not elsewhere classified
Q89 Other congenital malformations, not elsewhere classified
Q89.0 Congenital absence and malformations of spleen
Q89.01 Asplenia (congenital)
Q89.09 Congenital malformations of spleen
Q89.1 Congenital malformations of adrenal gland
Q89.2 Congenital malformations of other endocrine glands
Q89.3 Situs inversus
Q89.4 Conjoined twins
Q89.7 Multiple congenital malformations, not elsewhere classified
Q89.8 Other specified congenital malformations
Q89.9 Congenital malformation, unspecified
Q90 Down syndrome
Q90.0 Trisomy 21, nonmosaicism (meiotic nondisjunction)
Q90.1 Trisomy 21, mosaicism (mitotic nondisjunction)
Q90.2 Trisomy 21, translocation
Q90.9 Down syndrome, unspecified
Q91 Trisomy 18 and Trisomy 13
Q91.0 Trisomy 18, nonmosaicism (meiotic nondisjunction)
Q91.1 Trisomy 18, mosaicism (mitotic nondisjunction)
Q91.2 Trisomy 18, translocation

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.